Mea Kākau: Clyde Lopez
Lā O Ka Hana: 18 Iulai 2021
HōʻAno Hou I Ka Lā: 1 Iulai 2024
Anonim
Amniotic band syndrome !!
Wikiō: Amniotic band syndrome !!

ʻO ka hui pūʻulu Amniotic (ABS) kahi hui o nā hānau kīnā ʻole i manaʻo ʻia he hopena ke kaʻawale nā ​​kaula o ka ʻeke amniotic a hoʻopuni i nā ʻāpana o ka pēpē i loko o ka ʻōpū. Hiki i nā kīnā ke hoʻololi i ka maka, nā lima, nā wāwae, nā manamana lima, a me nā manamana wāwae.

Kuhi ʻia nā pēpē amniotic e ka hōʻino ʻia o kahi ʻāpana o ka placenta i kapa ʻia ʻo amnion (a i ʻole membrane amniotic). Hāpai ka placenta i ke koko i kahi pēpē e ulu mau ana i ka ʻōpū. Hiki i ka hōʻino i ka placenta ke pale i ka ulu maʻamau a me ka ulu ʻana.

Hiki paha i ka hōʻino i ka amnion ke hana i nā kaula like me ka fiber e hiki ke hei a hoʻopaʻa i nā ʻāpana o ka pēpē e ulu ana. Hoʻoemi kēia mau kaula i ka lako o ke koko i nā wahi a hana iā lākou e ulu kino.

Eia nō naʻe, hiki i kekahi mau hihia o ka deformity ABS ke kumu ʻia e ka hoʻoliʻiliʻi o ke koko me ka ʻole o nā hōʻailona o nā band a i ʻole ka hōʻino ʻana i ka amnion. Aia kekahi mau hihia kakaikahi i ʻike ʻia ma muli o nā kīnā genetika.

Hiki ke loli ākea ka paʻakikī o ka deformity, mai kahi niho liʻiliʻi i ka manamana lima a i ka manamana lima i kahi ʻāpana kino āpau e nalo ana a i ʻole hoʻomohala nui ʻia. Pākuʻi ʻia paha nā ʻōuli:


  • ʻO ke āpau kūpono ʻole i ke poʻo a i ʻole ke alo (inā hele i ke alo, ua kapa ʻia ia he mālamana)
  • All a hapa o ka manamana lima, manamananui, lima a me ka wāwae e nalo ana (congenital amputation)
  • Kīnā (cleft a puka paha) o ka ʻōpū a i ʻole ka paia o ka umauma (inā aia ka pā i kēlā mau wahi)
  • Paʻa paʻa a i ʻole indentation a puni ka lima, ka wāwae, ka manamana lima a i ʻole ka manamana wāwae

Hiki i ka mea mālama ola ke hōʻoia i kēia ʻano i ka wā o ke ultrasound prenatal, inā lawa lawa ia, a i ʻole i kahi hoʻokolohua kino hānau hou.

Hoʻololi ka lapaʻau ʻana. ʻO ka manawa pinepine, ʻaʻole koʻikoʻi ka deformity a ʻaʻohe pono e mālama. ʻO ke ʻoki kino ʻoiai pēpē i loko o ka ʻōpū e kōkua paha i ka hoʻomaikaʻi ʻana i nā hopena i kekahi mau hihia, akā ʻaʻole maopopo akā ʻo nā pēpē hea e pōmaikaʻi ai. Hoʻonui a hoʻoponopono paha kekahi mau hihia ma mua o ka hānau ʻana. I nā hihia koʻikoʻi hou aku, pono paha ke kahakaha nui e hana hou i nā mea āpau a i ʻole kekahi o ka ʻāpana o ke kino. ʻO kekahi mau hihia koʻikoʻi loa i hiki ʻole ke hoʻoponopono.

Pono e hoʻolālā i nā hoʻolālā no ka lawe pono ʻana a me ka hoʻokele ʻana i ka pilikia ma hope o ka hānau ʻana. Lawe ʻia ka pēpē i kahi kikowaena olakino i ʻike ka poʻe loea i ka mālama ʻana i nā pēpē me kēia ʻano.


Aia ka maikaʻi o ke pēpē i ka paʻakikī o ke ʻano. He akahai ka hapa nui o nā hihia a maikaʻi loa ka nānā ʻana no ka hana maʻamau. ʻO nā hihia ʻoi aku ka nui i mālama ʻia nā hopena.

Hiki i nā pilikia ke hoʻopili i ka nalowale piha a hapa paha o ka hana o kahi ʻāpana o ke kino. Hoʻopili nā pēpena congenital i nā ʻāpana nui o ke kino i nā pilikia he nui. ʻO kekahi mau hihia koʻikoʻi loa i hiki ʻole ke hoʻoponopono.

Maʻi ʻaʻa Amniotic band; Nā pūʻulu hoʻoliʻiliʻi amniotic; Constriction band Syndrome; ABS; Pākuʻi paia-kino; Mau apo paʻa; Pā kīnā o ke kino

ʻO Crum CP, Laury AR, Hirsch MS, CM wikiwiki, Peters WA. Nā pēpē amniotic. I: Crum CP, Laury AR, Hirsch MS, CM wikiwiki, Peters WA. nā ʻaoʻao ʻO Pathology a Gynecologic a me Obstetric. Piladelapia, PA: Elsevier; 2016: 776-777.

ʻO Jain JA, Fuchs KM. Ke kaʻina band Amniotic. I: Copel JA, DAlton ME, Feltovich H, et al, eds. Kiʻi Obstetric: Diagnosis Fetal a me ka mālama. ʻElua ed. Piladelapia, PA: Elsevier; 2018: chap 98.

ʻO Obican SG, ʻo Odibo AO. Hoʻoikaika fetal invasive. I: Resnik R, Lockwood CJ, Moore TR, Greene MF, Copel JA, Silver RM, eds. ʻO Medicine a Maternal-Fetal a Creasy a me Resnik: Nā Manaʻo a me ka Hoʻomeheu. 8th ed. Piladelapia, PA: Elsevier; 2019: chap 37.


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