Mea Kākau: Virginia Floyd
Lā O Ka Hana: 6 Aukake 2021
HōʻAno Hou I Ka Lā: 19 Kepakemapa 2024
Anonim
Johns Hopkins Medicine | Aplastic Anemia
Wikiō: Johns Hopkins Medicine | Aplastic Anemia

ʻO ke anemia anplastic kahi ʻano e lawa ʻole ai ka momona o ka iwi. ʻO ka iwi iwi ka mea palupalu, nā mea i waenakonu o nā iwi ke kuleana no ka hana ʻana i nā hunaola a me nā pā.

Loaʻa nā anemia Aplastic mai ka hōʻino ʻana i nā hunaola koko. ʻO nā hunaola nā hunaola ʻole i loko o ka iwi o ka iwi e hoʻāla i nā ʻano puʻuwai koko āpau (nā ʻulaʻula, nā aʻa koko keʻokeʻo, a me nā platelet). ʻO ka ʻeha i nā hunaola ke alakaʻi i ka hōʻemi o ka helu o kēia ʻano ʻili koko.

Hiki ke kumu ʻia ka anemia anplastic e:

  • Hoʻohana o kekahi mau lāʻau a i ʻole ke hōʻike ʻana i nā kemika ʻino (e like me chloramphenicol, benzene)
  • Hōʻike i ka radiation a i ʻole chemotherapy
  • Nā maʻi Autoimmune
  • Hapai keiki
  • Nā mea hoʻomaʻi

I kekahi manawa, ʻike ʻole ʻia ke kumu. I kēia hihia, ua kapa ʻia kēia maʻi he anemia idlopic aplastic.

ʻO nā ʻōuli ma muli o ka hana haʻahaʻa ʻole o nā hunaola ʻulaʻula, nā keʻokeʻo keʻokeʻo, a me nā platelet. Kūleʻa paha nā ʻōuli mai ka hoʻomaka a i ʻole hōʻemi ʻia i ka manawa ke holo ka maʻi.


Hiki i ka helu ʻulaʻula haʻahaʻa (anemia) ke kumu:

  • Ka luhi
  • Pallor (keʻokeʻo)
  • Helu puʻuwai wikiwiki
  • Ka hanu ʻana me ka hoʻoikaika kino
  • Nawaliwali
  • Ke kukui ma ke kū ʻana

Helu keʻokeʻo liʻiliʻi helu (leukopenia) ke kumu o ka hoʻonui ʻia o ka makaʻu no ka maʻi.

Hiki i ka helu platelet haʻahaʻa (thrombositopenia) ke hopena i ke kahe ʻana o ke kahe. ʻO nā hōʻailona me:

  • Pepeiao koko
  • ʻĀpiki maʻalahi
  • Kiko ihu
  • Rash, nā māka ʻulaʻula pinpoint ma ka ʻili (petechiae)
  • ʻO nā maʻi pinepine a koʻikoʻi paha (ʻoi aku ka maʻamau)

E hōʻike nā hōʻike koko:

  • Helu koko ʻulaʻula haahaa (anemia)
  • Helu keʻokeʻo haʻahaʻa keʻokeʻo haʻahaʻa (leukopenia)
  • Helu retikulii liʻiliʻi (retikulositā ka liʻiliʻi o nā huna koko ʻulaʻula)
  • Helu platelet haʻahaʻa (thrombositopenia)

Hōʻike kahi biopsy momona iwi i ka liʻiliʻi o nā keena koko a me ka hoʻonui ʻia o ka momona.

ʻO nā hihia akahai o ka anemia aplastic ʻaʻole i loaʻa nā ʻōuli e koi ʻole i ka lāʻau.


I ka lilo ʻana o ka helu o ke koko i haʻahaʻa a hoʻomohala ʻia nā ʻōuli, hāʻawi ʻia ke koko a me nā platelet ma o nā transfusions. Ma hope o ka hala ʻana o ka manawa, hiki paha i ke transfusions ke hoʻopau i ka hana ʻana, a laila e hopena ai nā helu o ke koko haʻahaʻa loa. He kūlana hoʻoweliweli kēia i ke ola.

Koi ʻia ka iwi o ka iwi, a i ʻole ke kāpili pūnaʻi koʻokoʻo no ka poʻe ʻōpio. Manaʻo ʻia ʻoi aku no kēlā mau makahiki 50 a ʻoi aku, akā hiki i ka poʻe ma luna o 50 ke loaʻa i kahi transplant inā lākou lawa ke olakino. ʻOi aku ka maikaʻi o kēia hana inā he kaikaina a kaikuaʻana paha ka mea hāʻawi. Kāhea ʻia kēia he mea hāʻawi pono na kaikaina ..

Hāʻawi ʻia ka poʻe ʻelemākule a me nā mea ʻaʻohe o ko lākou kaikaina e hāʻawi i ka lāʻau e kāohi i ka ʻōnaehana pale. ʻAe kēia mau lāʻau i ka momona o ka iwi e hana hou i nā hunaola olakino maikaʻi. Akā hoʻi paha ka maʻi (hoʻi hou). Hiki ke hoʻāʻo ʻia kahi hoʻoneʻe iwi pū me kahi mea hāʻawi pili ʻole inā ʻaʻole kōkua kēia mau lāʻau a i ʻole inā hoʻi mai ka maʻi ma hope o ka hoʻomaikaʻi ʻana.

ʻAʻole mālama ʻia, anemia aplastic koʻikoʻi e alakaʻi i ka make wikiwiki. Hiki ke kūleʻa i ka ʻōiwi iwi i ka poʻe ʻōpio. Hoʻohana ʻia ka transplant i ka poʻe ʻelemakule a i ʻole ke hoʻi mai ka maʻi ma hope o ka pau ʻana o ka hana o nā lāʻau.


Komo pū nā pilikia:

  • Nā maʻi maʻi a i ʻole ke kahe ʻana
  • Nā pilikia o ka hoʻoneʻe iwi iwi
  • Nā hopena i nā lāʻau
  • Hemochromatosis (kūkulu ʻia o ka nui o ka hao i loko o nā kino o ke kino mai nā transfusions ʻulaʻula nui)

Kāhea i kāu kahu mālama ola a i ʻole hele i ka lumi pilikia inā kū kahe ma ke kumu ʻole, a inā paʻakikī ke kahe ʻana i ke kahe. Kāhea inā ʻike ʻoe i nā maʻi pinepine a i ʻole ka māluhiluhi maʻamau.

Anemia Hypoplastic; Hoka iwi iwi ʻole - anemia aplastic

  • Hoʻoneʻe iwi iwi - hoʻokuʻu
  • ʻIʻini iwi iwi

ʻO Bagby GC. ʻO ka anemia anplastic a me nā ʻōlelo pū ʻole o ka iwi iwi e pili ana. I: Goldman L, Schafer AI, eds. ʻO ka lāʻau lapaʻau Goldman-Cecil. 26th ed. Piladelapia, PA: Elsevier; 2020: chap 156.

ʻO Culligan D, Watson HG. Koko a me ka iwi iwi. I: Cross SS, ed. Underwood's Pathology. ʻEpekema 7 Piladelapia, PA: Elsevier; 2019: chap 23.

ʻO NS ʻōpio, Maciejewski JP. Anemia anplastic. I: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Nā Kumumanaʻo a me ka Hoʻomeheu. ʻEpekema 7 Piladelapia, PA: Elsevier; 2018: chap 30.

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