Pemphigus: he aha ia, nā ʻano nui, nā kumu a me ka mālama ʻana
Anter
ʻO Pemphigus kahi maʻi pale laha ʻole i ʻike ʻia e ke hoʻokumu ʻia ʻana o nā palapū palupalu, ka mea i hū maʻalahi ʻaʻole hoʻōla. ʻO ka maʻamau, ʻike ʻia kēia mau huʻa i ka ʻili, akā hiki iā lākou ke hoʻopili i nā membrane mucous, e like me ka uhi ʻana o ka waha, nā maka, ka ihu, ka ʻāʻī a me ka wahi pili.
Kaukaʻi ʻia i ke ʻano a me ke kumu o ka hoʻomaka ʻana o nā ʻōuli, hiki ke hoʻokaʻawale ʻia ka pemphigus i kekahi mau ʻano, i hoʻopili ʻia me:
- Pemphigus vulgaris: ʻo ia ka ʻano maʻa mau, i hōʻike ʻia nā palapū ma ka ʻili a ma ka waha. Kuhi ka palapū i ka ʻeha a hiki ke nalowale, akā maʻa mau he mau kiko ʻeleʻele ka mau o kekahi mau mahina.
- Bullous pemphigus: ʻIke ʻia nā huʻa ʻoʻoleʻa a hohonu hoʻi e hū ʻole maʻalahi, a ʻoi aku ka pinepine i nā ʻelemākule. E aʻo hou aʻe e pili ana i kēia ʻano pemphigus;
- Pemphigus mea kanu: he ʻano maikaʻi o ka pemphigus vulgaris, ʻano ʻia e nā pōpō i ke aʻa, nā ʻāpana lima a i ʻole ka ʻāina pili;
- ʻO Pemphigus foliaceus: ʻo ia ka maʻa mau i nā wahi tropical, ʻike ʻia e nā hiʻohiʻona o nā ʻeha a i ʻole nā palapū, ʻaʻole ʻeha, i ʻike maka ʻia ma ka maka a me ka ʻili, akā hiki ke hoʻonui i ka umauma a me nā wahi ʻē aʻe;
Pemphigus erythematosus: he ʻano benign o pemphigus foliaceus, ka mea i hōʻike ʻia e nā pōpō superficial ma ka ʻili a me ke alo, i hiki ke huikau ʻia me ka seborrheic dermatitis a i ʻole lupus erythematosus;
- ʻO Paraneoplastic pemphigus: ʻo ia ka ʻano rarest, no ka mea pili ia me kekahi ʻano maʻi ʻaʻai e like me lymphomas a i ʻole leukemias.
ʻOiai ʻoi aku ka maʻamau o nā mākua a me nā ʻelemākule, hiki ke ʻike ʻia ka pemphigus i kēlā me kēia makahiki. ʻAʻole hiki i kēia maʻi ke lele a loaʻa kahi hoʻōla, akā ʻo kāna lapaʻau ʻana, hana ʻia me ka lāʻau corticosteroid a me nā lāʻau immunosuppressive, i kuhikuhi ʻia e ka dermatologist, hiki ke hala i mau mahina a mau makahiki paha e hōʻoia i ka mālama ʻia ʻana o ka maʻi.
Pemphigus vulgaris ma ka ʻiliPemphigus vulgaris i ka wahaHe aha ke kumu o ka pemphigus
Hoʻokumu ʻia ʻo Pemphigus e ka hoʻololi o ka ʻōnaehana pale pilikino ponoʻī o ke kanaka, kahi e hana ai i ke kino e hana i nā mea ʻino e hoʻouka i nā hunaola olakino i ka ʻili a me nā membrane mucous. ʻOiai ʻike ʻole ʻia nā mea e alakaʻi ai i kēia loli, ʻike ʻia ka hoʻohana ʻia ʻana o kekahi mau lāʻau kahe koko kiʻekiʻe hiki ke ʻike ʻia nā ʻōuli, e nalo ke pau ka lāʻau.
No laila, ʻaʻohe maʻi pemphigus, no ka mea, ʻaʻole ia e kumu ʻia e kekahi mea hoʻomaʻi a me nā koʻohune. Eia nō naʻe, inā maʻi ʻia nā ʻehaʻeha, hiki ke hoʻoili i kēia mau koʻohune i kekahi kanaka i hele pololei i ka launa ʻana me nā ʻeha, a hiki i ke ʻano o ka huhū o ka ʻili.
Pehea e hana ai i ka lāʻau
Hana maʻamau no ka pemphigus i ka hoʻohana ʻana i nā lāʻau i kuhikuhi ʻia e ka dermatologist, e like me:
- Corticosteroids, e like me Prednisone a i ʻole Hydrocortisone: hoʻohana ʻia i nā hihia mehana o pemphigus e hōʻoluʻolu ai i nā ʻōuli. ʻAʻole pono e hoʻohana ʻia kēia mau lāʻau no 1 mau pule ma ka lālani;
- Nā Immunosuppressants, e like me Azathioprine a i ʻole Mycophenolate: hoʻēmi i ka hana o ka ʻōnaehana pale, pale iā ia mai ka hoʻouka ʻana i nā hunaola olakino. Eia nō naʻe, ma ka hōʻemi ʻana i ka hana o ka ʻōnaehana pale, nui aʻe ka manawa o ka maʻi a no laila, hoʻohana ʻia kēia mau lāʻau i loko o nā hihia ʻoi loa.
- Nā Antibiotics, antifungal a i ʻole antiviral: hoʻohana ʻia lākou ke ʻike ʻia kekahi ʻano maʻi i loko o nā ʻeha i waiho ʻia e nā palapū.
Hana ʻia ka lapaʻau ma ka home a hiki ke mau no kekahi mau mahina a i ʻole mau makahiki, ke kaukaʻi ʻia i ka meaola o ka mea maʻi a me ke ʻano a me ke koʻikoʻi o ka pemphigus.
I nā hihia koʻikoʻi loa, kahi e kū ai nā maʻi ʻehaʻeha, no ka laʻana, pono paha e noho i ka haukapila no kekahi mau lā a i ʻole mau pule, e hana pololei i nā lāʻau i loko o ke aa a hana i ka lapaʻau kūpono i nā ʻeha i loaʻa.