He aha ʻo Pancytopenia?

Anter
- Nā ʻōuli o ka pancytopenia
- ʻO Pancytopenia nā kumu a me nā kumu pilikia
- Nā pilikia i hoʻokumu ʻia e pancytopenia
- Pehea e ʻike ʻia ai ka pancytopenia
- Nā koho lapaʻau
- Outlook
- Kāohi ʻana i ka pancytopenia
Hōʻike Overview
ʻO Pancytopenia kahi ʻano i loaʻa i ke kino o ke kanaka he mau ʻulaʻula o ke koko ʻulaʻula, nā hunaola keʻokeʻo, a me nā platelet. He hana ʻokoʻa ko kēlā me kēia ʻano ʻāpana koko i ke kino.
- Hāpai nā hunaola ʻulaʻula i ka oxygen ma loko o kou kino.
- ʻO nā hunaola keokeo kahi o kāu ʻōnaehana pale a kōkua i ke kaua aku i nā maʻi.
- ʻAe nā platelet i kou koko e hana i nā clots.
Inā loaʻa iā ʻoe ka pancytopenia, loaʻa iā ʻoe kahi hui o ʻekolu mau maʻi koko ʻokoʻa.
- anemia, a i ʻole pae haʻahaʻa o nā hunaola ʻulaʻula
- leukopenia, a i ʻole pae haʻahaʻa o nā hunaola keokeo
- thrombositopenia, aiʻole nā pae platelet haʻahaʻa
Ma muli o kou kino e pono ai i kēia mau huna koko, hiki i ka pancytopenia ke koʻikoʻi loa. Hiki iā ia ke hoʻoweliweli i ke ola inā ʻaʻole ʻoe e mālama iā ia.
Nā ʻōuli o ka pancytopenia
ʻAʻole pinepine ka pancytopenia māmā i nā ʻōuli. E ʻike paha kāu kauka iā ia e hana ana i kahi hoʻokolohua koko no kekahi kumu ʻē aʻe.
Hiki i ka pancytopenia ʻoi loa ke kumu i nā ʻōuli e like me:
- pokole o ka hanu
- ʻili mae
- luhi
- nāwaliwali
- fiva
- ʻūpā
- paopao maʻalahi
- kahe ana ke koko
- nā kiko poni liʻiliʻi ma kou ʻili, i kapa ʻia ʻo petechiae
- nā kiko poni nui aʻe ma kou ʻili, i kapa ʻia ʻo purpura
- nā kāʻei koko a me nā ihu ihu
- wikiwiki o ka puʻuwai
Inā ʻo ʻoe a ʻo kekahi mea kokoke paha iā ʻoe kekahi o nā hōʻailona koʻikoʻi a me ka pancytopenia, e mālama koke i ka lāʻau.
- fiva ma luna o 101˚F (38.3˚C)
- ka hopu ʻana
- kahe nui ke koko
- pōkole loa o ka hanu
- huikau
- nalowale o ka ʻike
ʻO Pancytopenia nā kumu a me nā kumu pilikia
Hoʻomaka ʻo Pancytopenia ma muli o kahi pilikia me kou iwi iwi. ʻO kēia kiko spongy i loko o nā iwi kahi e hana ʻia ai nā hunaola koko. Hiki i nā maʻi a me ke kū ʻana i kekahi mau lāʻau a me nā kemika ke alakaʻi i kēia ʻino pū iwi.
E hoʻolālā paha ʻoe i ka pancytopenia inā loaʻa iā ʻoe kekahi o kēia mau ʻano:
- nā maʻi 'aʻai e hoʻololi i ka momona o ka iwi, e like me:
- maʻi leukemia
- myeloma maha
- ʻO Hodgkin's a i ʻole non-Hodgkin's lymphoma
- myelodysplastic syndrome
- megaloblastic anemia, kahi ʻano a kou kino e hoʻopuka ai i nā hunaola ʻulaʻula ma mua o ka maʻamau, a he helu koko kōulaʻula kou.
- aplastic anemia, kahi ʻano e pau ai kou kino i ka hana ʻana i nā huna koko hou
- paroxysmal nocturnal hemoglobinuria, kahi maʻi koko laha ʻole e hoʻopau ʻia nā hunaola ʻulaʻula
- nā maʻi viral, e like me:
- ʻO ka maʻi Epstein-Barr, ke kumu o ka mononucleosis
- cytomegalovirus
- HIV
- maʻi hepa
- malaria
- sepsis (kahi maʻi koko)
- nā maʻi e hōʻino ai i ka iwi iwi, e like me ka maʻi Gaucher
- poino mai ka chemotherapy a i ʻole nā hana radiation no ka maʻi ʻaʻai
- ka hōʻike ʻana i nā kemika i ke kaiapuni, e like me ka radiation, arsenic, a i ʻole benzene
- nā maʻi pūpū o ka iwi e holo i loko o nā ʻohana
- nā hemahema o ka wikamina, e like me ka nele o ka wikamina B-12 a i ʻole ka folate
- hoʻonui ʻana o kāu lola, ʻike ʻia splenomegaly
- maʻi maʻi ate
- hoʻohana nui i ka waiʻona e hōʻino ai i kou ake
- nā maʻi autoimmune, e like me systemic lupus erythematosus
Ma kahi o ka hapalua o nā hihia āpau, ʻaʻole hiki i nā kauka ke loaʻa kahi kumu no ka pancytopenia. Kapa ʻia kēia ʻo idiopathic pancytopenia.
Nā pilikia i hoʻokumu ʻia e pancytopenia
Nā pilikia mai ka pancytopenia koʻokoʻo mai ka nele o nā hunaola ʻulaʻula, nā hunaola keʻokeʻo, a me nā platelet. Hiki i kēia mau pilikia ke:
- ʻoi aku ke kahe ʻana o ke koko inā pili ka platelet
- hoʻonui i ka makaʻu no nā maʻi inā hoʻopili ʻia nā hunaola keokeo
Hiki ke hoʻoweliweli i ka pancytopenia nui.
Pehea e ʻike ʻia ai ka pancytopenia
Inā manaʻo kāu kauka he pancytopenia ʻoe, e paipai paha lākou e ʻike i kahi hematologist - he loea e mālama i nā maʻi koko. Makemake kēia loea e aʻo i ka mōʻaukala ʻohana a me ka mōʻaukala pilikino. I ka wā o ka hoʻokolohua, e nīnau ke kauka e pili ana i kāu mau hōʻailona a nānā i kou mau pepeiao, ihu, ʻāʻī, waha, a me kou ʻili.
E hana pū ke kauka i kahi helu piha o ke koko (CBC). Ana kēia hōʻike i ka nui o nā hunaola ʻulaʻula, nā hunaola keokeo, a me nā platelet i loko o kou koko. Inā kūpono ʻole ka CBC, pono ʻoe i kahi smear koko ākea. Kau kēia hoʻokolohua i kahi kulu o kou koko ma kahi pāheʻe e nānā i nā ʻano ʻāpana o ke koko i loaʻa i loko.
E nānā i kahi pilikia me kou iwi iwi, e hana paha kāu kauka i ka ʻiʻini iwi a me ka biopsy. I kēia hoʻokolohua, hoʻohana kāu kauka i kahi nila no ka hemo ʻana i kahi wai liʻiliʻi a me nā mea mai loko o kou iwi i hiki ke hoʻāʻo a nānā ʻia i loko o kahi lab.
Hana paha kāu kauka i nā hoʻokolohua ʻokoʻa e nānā no ke kumu o ka pancytopenia. Hiki i kēia mau hoʻāʻo ke hoʻopili i nā hoʻokolohua koko e nānā ai i nā maʻi a i ʻole leukemia. Pono paha ʻoe i kahi CT scan a i ʻole nā hōʻike kiʻi ʻē aʻe e nānā no ka maʻi ʻaʻai a i ʻole nā pilikia ʻē aʻe me kāu mau ʻōpū.
Nā koho lapaʻau
E mālama kāu kauka i ka pilikia i hopena i ka pancytopenia. Pākuʻi paha kēia i ka lawe ʻana iā ʻoe i kahi lāʻau a i ʻole ke kū ʻana i kou ʻike i kekahi kemikali. Ke hoʻouka nei kāu ʻōnaehana pale pale i kou iwi iwi, e loaʻa iā ʻoe ka lāʻau e hōʻemi i ka pale o kou kino.
Nā hana no ka pancytopenia:
- nā lāʻau e hoʻoulu ai i ka hana ʻana o ke koko i kou momona o ka iwi
- nā transfusions o ke koko e pani i nā hunaola ʻulaʻula, nā hunaola keokeo, a me nā platelet
- antibiotics e mālama i kahi maʻi
- kahi iwi kuamoʻo, i ʻike ʻia ma ke ʻano he transplant cell, kahi e pani ai i ka iwi iwi i hoʻopōʻino ʻia me nā hunaola koʻokoʻo olakino e kūkulu hou i ka iwi iwi
Outlook
ʻO ka nānā no ka pancytopenia kaukaʻi ʻia i ka maʻi i hoʻokumu ai i ke ʻano a pehea e mālama ai kāu kauka. Inā he lāʻau a lāʻau paha i hoʻokumu i ka pancytopenia, pono e ʻoi aku ka maikaʻi i loko o hoʻokahi pule ma hope o kou hōʻoki ʻana i ka hōʻike. ʻO kekahi ʻano, e like me ka maʻi ʻaʻai, e hoʻolōʻihi ʻia e mālama.
Kāohi ʻana i ka pancytopenia
ʻO kekahi mau kumu o ka pancytopenia, e like me ka maʻi ʻaʻai a i ʻole nā maʻi ʻōiwi hoʻoilina i hoʻoili ʻia, ʻaʻole hiki ke pale ʻia. Hiki paha iā ʻoe ke pale aku i kekahi ʻano maʻi me nā hana hoʻomaʻemaʻe maikaʻi a me ka hōʻalo ʻana i ka launa ʻana me nā mea maʻi. Hiki iā ʻoe ke hōʻalo i nā kemika i ʻike ʻia ke kumu o kēia ʻano.