Nā Nānā Nutr a me nā Metabolism

Anter

• Pehea e hana ai kāu metabolism?
• He aha ka maʻi metabolic?
• He aha ke kumu o nā maʻi metabolic?
• Nā ʻano o nā maʻi metabolic
• Maʻi ʻo Gaucher
• ʻO Glucose galactose malabsorption
• Hemochromatosis hoʻoilina
• ʻO ka maʻi mimi syrup maple (MSUD)
• Phenylketonuria (PKU)
• Outlook

Pehea e hana ai kāu metabolism?

ʻO ka Metabolism ka hana kemika a kou kino e hoʻohana ai e hoʻololi i ka meaʻai āu e ʻai ai i ka wahie e mālama ai iā ʻoe e ola.

ʻO nā meaʻai (nā meaʻai) nā proteins, nā kālika, a me nā momona. Uhaʻi ʻia kēia mau mea e nā enzyme i loko o kāu ʻōnaehana digestive, a laila lawe ʻia i nā hunaola kahi e hiki ai ke hoʻohana ʻia i wahie. Hoʻohana koke kou kino i kēia mau mea, a i ʻole mālama ʻia i ke ake, ka momona o ke kino, a me nā mākala no ka hoʻohana ma hope.

He aha ka maʻi metabolic?

Hana ʻia kahi maʻi metabolic ke holo pono ke kaʻina hana a hana i ke kino e nui a liʻiliʻi paha o nā mea pono e pono ai ke olakino.

Pilikino loa ko mākou kino i nā hewa i ka metabolism. Pono i ke kino nā amino acid a me nā ʻano protein e hana i kāna hana āpau. ʻO kahi laʻana, pono ka lolo i ka calcium, potassium, a me ka sodium e hana i nā impulses uila, a me nā lipids (nā momona a me nā aila) e mālama i kahi ʻōnaehana ʻōnaehana olakino.

Hiki i nā maʻi Metabolic ke ʻano he nui. Pākuʻi ʻia kēia:

• kahi enzyme nalo a i ʻole ka wikamina e pono ai no ka hopena kemika koʻikoʻi
• nā hopena kemika ʻino e ālai ai i nā hana metabolic
• kahi maʻi i ke akepaʻa, pancreas, endocrine glands, a i ʻole nā ​​mea ʻē aʻe i pili i ka metabolism
• hemahema o ka meaʻai

He aha ke kumu o nā maʻi metabolic?

Hiki iā ʻoe ke hoʻomohala i kahi maʻi metabolic inā kekahi mau lālā - no ka laʻana, ka pancreas a me ke akepaʻa - hooki i ka hana kūpono. Hiki i kēia ʻano ʻano maʻi ke hopena o nā genetics, kahi hemahema i kekahi hormone a i ʻole enzyme, e ʻai nui ana i kekahi mau meaʻai, a i ʻole nā ​​helu ʻē aʻe.

Aia he mau haneli o nā maʻi metabolic genetic e hopena ʻia e nā genes hoʻokahi. Hiki ke hoʻoili ʻia kēia mau hoʻololi i nā hanauna ʻohana. Wahi a ka, kekahi mau lāhui a lāhui paha i ʻoi aku ka nui ma luna o nā genet mutated no kekahi mau maʻi hānau. ʻO ka maʻamau o kēia mau mea:

• anemia maʻi ʻaʻaiwi ma ʻAmelika ʻAmelika
• cystic fibrosis i ka poʻe hoʻoilina o ʻEulopa
• maʻi maʻi mimi syrup maple ma nā kaiāulu Mennonite
• ʻO ka maʻi ʻo Gaucher i ka poʻe Iudaio mai ʻEulopa Hema
• hemochromatosis ma Caucasians ma ʻAmelika Hui Pū ʻIa

Nā ʻano o nā maʻi metabolic

ʻO ka maʻi diabetes ka maʻi metabolic maʻamau. Aia ʻelua mau ʻano diabetes:

• ʻAno 1, ke kumu o ka ʻike ʻole ʻia, ʻoiai hiki ke lilo i kumu kūlohelohe.
• ʻAno 2, hiki ke loaʻa, a i ʻole hoʻokumu ʻia e nā kumu kūlohelohe pū kekahi.

Wahi a ka American Diabetes Association, 30.3 miliona mau keiki a me nā mākua, a ma kahi paha o ka 9.4 pakeneka o ko U.S. heluna kanaka i loaʻa i ka maʻi diabetes.

I ka maʻi diabetes ʻano ʻ 1, hoʻouka a pepehi nā hunaola T i nā hunaola beta i ka pancreas, nā hunaola e hoʻopuka i ka insulin. Ma hope o ka manawa, hiki i ka nele o ka insulin ke kumu:

• ʻino nā nerve a me nā puʻupaʻa
• hoʻohaʻahaʻa maka
• hoʻonui i ka makaʻu o ka naʻau a me nā maʻi vaskular

Ua ʻike ʻia he mau haneli hewa hewa i loko o ka metabolism (IEM), a ʻo ka hapa nui he kākaʻikahi loa. Eia nō naʻe, ua koho ʻia he pili like ka IEM i 1 i kēlā me kēia pēpē 1,000. ʻO ka hapa nui o kēia mau maʻi e hiki ke mālama ʻia e ka palena ʻana i ka lawe ʻana i nā meaʻai a nā mea a i ʻole hiki i ke kino ke hana.

ʻO nā ʻano maʻamau o nā maʻi nutritional a me nā metabolic maʻi e komo pū me:

Maʻi ʻo Gaucher

ʻO kēia ʻano ke kumu o ka hiki ʻole ke wāwahi i kekahi ʻano momona, i hōʻiliʻili ʻia i ke akepaʻa, ka iwi, a me ka iwi iwi. Hiki i kēia hiki ʻole ke hopena i ka ʻeha, hōʻino iwi, a me ka make pū kekahi. Mālama ʻia ia me ka hoʻōla hou ʻana i ka enzyme.

ʻO Glucose galactose malabsorption

He kīnā kēia i ka lawe ʻana o glucose a me nā galactose ma o ka uhi ʻōpū e hiki ai i ka maʻi nui a me ka make wai. Mālama ʻia nā ʻōuli e ka lawe ʻana i ka lactose, ka sucrose, a me ka glucose mai ka papaʻai.

Hemochromatosis hoʻoilina

I kēia kūlana, waiho ʻia ka hao ʻoi aku i nā ʻōnaehana he nui, a hiki ke kumu:

• ate cirrhosis
• maʻi ʻaʻai ate
• diabetes
• maʻi maʻi puʻuwai

Mālama ʻia ia e ka lawe ʻana i ke koko mai ke kino (phlebotomy) i kahi manawa maʻamau.

ʻO ka maʻi mimi syrup maple (MSUD)

Hoʻopilikia ka MSUD i ka metabolism o kekahi mau amino acid, e hoʻoliʻiliʻi wikiwiki ʻana o nā neurons. Inā mālama ʻole ʻia, make ia i loko o nā mahina mua ma hope o ka hānau ʻana. Hoʻomanaʻo ka mālama ʻana i ka palena ʻana i ka papaʻai o nā amino acid branched-chain.

Phenylketonuria (PKU)

Hoʻokumu ʻo PKU i ka hiki ʻole ke hana i ka enzyme, phenylalanine hydroxylase, e hopena i nā kino o ke kino, ka lohi o ka noʻonoʻo, a me ke ʻano maʻamau. Mālama ʻia ia e ka palena ʻana i ka papaʻai papaʻai o kekahi ʻano protein.

Outlook

Kūpilikiʻi a kākaʻikahi nā maʻi Metabolic. ʻOiai, ʻo lākou ke kumuhana o ka noiʻi mau, kahi e kōkua pū nei i ka ʻepekema e hoʻomaopopo pono i nā kumu kumu o nā pilikia maʻamau e like me ka lactose, sucrose, a me ka hoʻomanawanui ʻole o ka glucose, a me ka nui o kekahi mau protein.

Inā loaʻa ʻoe i kahi maʻi metabolic, hiki iā ʻoe ke hana pū me kāu kauka e ʻike i kahi hoʻolālā lapaʻau kūpono iā ʻoe.