He aha ka Syndrome o ka make koke, a hiki paha ke pale?

Anter

• He aha ka maʻi make koke?
• ʻO wai ka pilikia?
• He aha ke kumu?
• He aha nā hōʻailona?
• Pehea ia ʻike?
• Pehea e mālama ʻia ai?
• Hiki ke pale ʻia?
• ʻO ka lawe lawe ʻana

He aha ka maʻi make koke?

ʻO ka maʻi make kūlohelohe (SDS) kahi manawa hoʻomālama i wehewehe ʻia no kahi moʻo o nā puʻuwai puʻuwai e kumu i ka hopu ʻia ʻana o ka naʻau a make paha.

ʻO kekahi o kēia mau syndrome ka hopena o nā pilikia kūkulu i ka puʻuwai. ʻO nā mea ʻē aʻe paha ka hopena o nā kūleʻa i loko o nā kahawai uila. Hiki i nā mea āpau ke kumu i ka hopu ʻia o ka puʻuwai me ka hopu ʻole ʻia, ʻoiai i ka poʻe i olakino ʻole. Make kekahi poʻe ma muli o kahi hopena.

ʻAʻole maopopo ka hapa nui o ka poʻe i ka maʻi maʻi a hiki i ka hopu ʻia ʻana o ka naʻau.

ʻAʻole ʻike ʻia ka nui o nā hihia o SDS. Ke make kekahi kanaka me SDS, hiki i ka make ke helu ʻia ma ke ʻano he kumu kūlohelohe a hōʻeha puʻuwai paha. Akā inā he ʻanuʻu kekahi i ka coroner e hoʻomaopopo i ke kumu kikoʻī, hiki iā lākou ke ʻike i nā hōʻailona o kekahi o nā syndrome o SDS.

Hōʻike kekahi mau manaʻo loiloi ma ka liʻiliʻi o ka poʻe me SDS ʻaʻohe mea kūpono ʻole o ke ʻano, ʻo ia ka maʻalahi e hoʻoholo ai i kahi autopsy. ʻOi aku ka paʻakikī o nā hemahema i nā kahawai uila.

ʻOi aku ka maʻamau o SDS i nā ʻōpio ʻōpio a me waena. I ka poʻe o kēia au, ʻike ʻia ka make i wehewehe ʻole ʻia e like me ka make ʻana o ka makua make koke (SADS).

Hiki iā ia ke hana i nā pēpē pū kekahi. ʻO kēia mau syndrome paha kekahi o nā kūlana he nui i hāʻule ma lalo o ka make koke o ka maʻi pēpē (SIDS).

ʻO kekahi ʻano, ʻo Brugada Syndrome, ke kumu o ka make ʻana i ka pō make ʻole i ka pō (SUNDS).

Ma muli o ke kuhi hewa pinepine ʻole o SDS a ʻaʻole paha i hōʻike ʻia, maopopo ʻole i ka nui o ka poʻe i loaʻa iā ia.

Manaʻo nā kuhi he 5 i ka 10,000 mau kānaka i loaʻa i ka maʻi Brugada. ʻO kekahi ʻano SDS, ʻo QT syndrome lōʻihi paha, i kū i loko. ʻOi loa ka QT pōkole. 70 wale nō hihia o ia i ʻike ʻia i loko o nā makahiki he iwakālua i hala.

Hiki i kekahi manawa ke ʻike inā pilikia ʻoe. Hiki paha iā ʻoe ke mālama i ke kumu kumu o ka hiki SDS inā ʻoe.

E nānā hou aku i nā ʻanuʻu i hiki ke lawe ʻia e ʻike pono i kekahi o nā ʻano e pili ana me SDS a pale paha i ka hopu ʻia o ka naʻau.

ʻO wai ka pilikia?

ʻO ka poʻe me SDS ke ʻano olakino maikaʻi loa ma mua o kā lākou hanana cardiac mua a make paha. ʻAʻole kumu pinepine ʻo SDS i nā hōʻailona a i ʻole nā ​​hōʻailona ʻike ʻia. Eia nō naʻe, aia kekahi mau mea pilikia e hoʻonui i ka likiki o ke kanaka i ka loaʻa ʻana o kekahi o nā ʻano e pili ana me SDS.

Ua loaʻa i nā kānaka noiʻi he mau gen kikoʻī paha e hoʻonui i ka makaʻu o ke kanaka no kekahi ʻano SDS. Inā loaʻa ka SADS i kekahi kanaka, no ka laʻana, o ko lākou mau mākelē mua (kaikaina, nā mākua, a me nā keiki) e loaʻa pū kekahi me ka maʻi maʻi pū kekahi.

ʻAʻole naʻe kēlā me kēia kanaka me SDS kekahi o kēia mau gen. ʻO 15 wale nō 30 pākēneka o nā hihia i hōʻoia o ka maʻi Brugada i loaʻa ka ʻāpana e pili ana i kēlā ʻano kūlana.

ʻO nā kumu ʻē aʻe e pili pū me:

• Moekolohe ʻOi aku ka nui o ka loaʻa o ka SDS o nā kāne ma mua o nā wahine.
• Heihei. ʻOi aku ka nui o ka makaʻu o nā kānaka mai Iapana a me Hikina Hema Asia no ka maʻi Brugada.

Ma waho aʻe o kēia mau kumuhana pilikia, hiki i kekahi mau ʻano olakino ke hoʻonui i ka makaʻu o SDS, e like me:

• Bipolar kāna hana. Hoʻohana ʻia ka lithium i kekahi manawa e mālama i ka maʻi bipolar. Hiki i kēia lāʻau ke hoʻoulu iā Brugada Syndrome.
• Maʻi maʻi puʻuwai. ʻO ka maʻi o ke aʻa coronary ka maʻi maʻamau i pili pinepine ʻia e pili ana iā SDS. ʻO ke kumu o ka maʻi coronary artery ka hikiwawe. ʻO ka hōʻailona mua o ka maʻi ka hopu ʻana i ka naʻau.
• Epilepsy. I kēlā me kēia makahiki, make koke ʻole ka epilepsy (SUDEP) e pili ana i ka maʻi ʻeha. ʻO ka hapa nui o nā make e kū koke ma hope o ka hopu ʻana.
• ʻO Arrhythmias. ʻO ka arrhythmia kahi puʻuwai puʻuwai a i ʻole ritmo. Pākuʻi paha ka puʻuwai a i ʻole wikiwiki paha. Hiki paha iā ia ke hoʻohālikelike kūpono ʻole. Hiki iā ia ke alakaʻi i nā ʻōuli e like me ka poni ʻana a i ʻole puʻupuʻu. ʻO ka make hikiwawe kekahi hiki.
• Hypertrophic cardiomyopathy. ʻO kēia ʻano ke mānoanoa nā paia o ka puʻuwai. Hiki iā ia ke hoʻopilikia i ka ʻōnaehana uila. Hiki i nā mea ʻelua ke alakaʻi i kahi puʻuwai puʻuwai a i ʻole wikiwiki (arrhythmia).

He mea nui e hoʻomaopopo ma muli o kēia mau mea kūpilikiʻi i ʻike ʻia, ʻaʻole lākou manaʻo he SDS kāu. ʻO kēlā me kēia makahiki a i kekahi kūlana olakino hiki ke loaʻa iā SDS.

He aha ke kumu?

ʻAʻole maopopo i ke kumu o SDS.

Ua hoʻopili ʻia ka hoʻololi ʻana o nā Gene i ka nui o nā syndrome e hāʻule ma lalo o ka malu o SDS, akā ʻaʻole kēlā me kēia kanaka me SDS nā ʻāpana. He mea pili paha nā genes ʻē aʻe i SDS, akā ʻaʻole lākou i ʻike ʻia i kēia manawa. A ʻo kekahi mau kumu SDS ʻaʻole genetiko.

Hiki i kekahi mau lāʻau ke kumu i nā syndrome e alakaʻi i ka make koke. ʻO kahi laʻana, ʻo QT syndrome ka hopena ma muli o ka hoʻohana ʻana:

• antihistamines
• decongestants
• antibiotic
• diuretics
• lāʻau antidepressants
• antipsychotics

Pēlā nō, ʻaʻole hiki i kekahi poʻe me SDS ke hōʻike i nā hōʻailona a hoʻomaka lākou e lawe i kēia mau lāʻau. A laila, e ʻike ʻia ka SDS i hoʻokomo ʻia i ka lāʻau.

He aha nā hōʻailona?

Minamina, ʻo ka hōʻailona mua a hōʻailona paha o SDS hiki i ka make koke a me ka make ʻole.

Eia nō naʻe, hiki i ka SDS ke hana i nā ʻōuli ʻulaʻula hae:

• ʻeha o ka umauma, keu hoʻi i ka hoʻoikaika kino
• nalowale o ka ʻike
• paʻakikī i ka hanu ʻana
• ʻūpā
• palpitations puʻuwai a i ʻole manaʻo flutter
• maʻule ʻole ʻole ʻia, ʻoi aku i ka wā hoʻoikaika kino

Inā ʻoe a ʻo kāu keiki paha e ʻike i kekahi o kēia mau ʻōuli, e ʻimi koke i ka lāʻau. Hiki i ke kauka ke hana i nā hoʻokolohua e hoʻoholo ai i ke kumu o kēia mau hōʻailona i manaʻo ʻole ʻia.

Pehea ia ʻike?

Hoʻomaopopo wale ʻia ʻo SDS ke hele ʻoe i ka hopu koke ʻia o ka naʻau. Hiki i kahi electrocardiogram (ECG a i ʻole EKG) ke kuhi i ka nui o nā syndrome i hiki ke make i ka make koke. Hoʻopaʻa kēia hōʻike i ka hana uila o kou puʻuwai.

Hiki i nā kānaka cardiologists hoʻomaʻamaʻa kūikawā ke nānā i nā hopena ECG a hoʻomaopopo i nā pilikia e hiki ai, e like me ka QT syndrome lōʻihi, QT syndrome pōkole, arrhythmia, cardiomyopathy, a me nā mea hou aʻe.

Inā ʻaʻole maopopo ka ECG a makemake paha ke koloologist i ka hōʻoia hou aʻe, noi paha lākou i kahi echocardiogram. ʻO kēia kahi loiloi ultrasound o ka puʻuwai. Me kēia hōʻike, hiki i ke kauka ke ʻike i kou puʻuwai e kani ana i ka manawa maoli. Hiki i kēia ke kōkua iā lākou e ʻike i nā kino o ke kino.

ʻO kēlā me kēia mea e loaʻa nei nā hōʻailona e pili ana me SDS e loaʻa iā ia kekahi o kēia mau hoʻāʻo. Pēlā nō, ʻo ka poʻe me kahi olakino a i ʻole ka mōʻaukala ʻohana e hōʻike ana he hiki paha i ka SDS ke loaʻa i kekahi o kēia mau hoʻāʻo.

Hiki ke kōkua i ka ʻike mua ʻana i ka makaʻu i ke aʻo ʻana i nā ala e pale ai i ka hopu ʻia o ka naʻau.

Pehea e mālama ʻia ai?

Inā kū kou puʻuwai ma muli o ka hopena o SDS, hiki i nā mea pane pilikia ke hoʻopakele iā ʻoe me nā hana mālama ola. Hoʻopili kēia i ka CPR a me ka defibrillation.

Ma hope o ka resuscitation, hiki i ke kauka ke hana i ke ʻoki e hoʻonoho i kahi defibrillator cardioverter implantable (ICD) inā kūpono. Hiki i kēia hāmeʻa ke hoʻouna i nā uila uila i loko o kou puʻuwai inā kū hou ia i ka wā e hiki mai ana.

Pīhoihoi paha ʻoe a hele i waho ma ke ʻano he hopena o ka hopena, akā hiki i ka mea i hoʻokomo ʻia ke hoʻomaka hou i kou puʻuwai.

ʻAʻohe mea ola i kēia manawa no ka hapa nui o nā kumu o SDS. Inā loaʻa iā ʻoe kahi hōʻailona me kekahi o kēia mau syndrome, hiki iā ʻoe ke hana i nā hana e pale ai i kahi hanana make. Pākuʻi paha kēia i ka hoʻohana ʻana o kahi ICD.

Eia naʻe, ua haehae nā kauka e pili ana i ka hoʻohana ʻana i ka lapaʻau no SDS i kahi kanaka i hōʻike ʻole i kekahi ʻano o nā hōʻailona.

Hiki ke pale ʻia?

ʻO ka hōʻailona mua kahi hana nui i ka pale ʻana i kahi hopena make.

Inā loaʻa iā ʻoe kahi moʻolelo ʻohana o SDS, hiki i ke kauka ke hoʻoholo inā he maʻi pū kekahi kou e hiki ai i ka make i manaʻo ʻole ʻia. Inā hana ʻoe, hiki iā ʻoe ke hana i nā hana e pale ai i ka make koke. Pākuʻi ʻia kēia mau mea:

• e hōʻalo nei i nā lāʻau e hoʻonāukiuki i nā hōʻailona, ​​e like me nā lāʻau antidepressants a me nā lāʻau kaloka sodium
• mālama wikiwiki ʻana i nā fiva
• me ka akahele
• e hoʻomaʻamaʻa ana i nā ana olakino olakino maikaʻi, me ka ʻai ʻana i ka papaʻai kaulike
• mālama i nā loiloi maʻamau me kāu kauka a i ʻole ka loiloi puʻuwai

ʻO ka lawe lawe ʻana

ʻOiai ʻaʻohe lapaʻau ʻo SDS, hiki iā ʻoe ke hana i nā hana e pale ai i ka make koke inā loaʻa ʻoe i kahi hōʻailona ma mua o kahi hanana make.

ʻO ka loaʻa ʻana o kahi hōʻailona hiki ke hoʻololi i ke ola a hana i nā ʻano ʻokoʻa. Ma waho aʻe o ka hana pū ʻana me kāu kauka, makemake paha ʻoe e kamaʻilio me kahi loea olakino e pili ana i ke ʻano a me kou olakino noʻonoʻo. Hiki iā lākou ke kōkua iā ʻoe e hana i ka nūhou a kū i nā loli i kāu kūlana olakino.