Swyer maʻi maʻi
Anter
ʻO Swyer's Syndrome, a i ʻole XY gonadal dysgenesis maʻemaʻe, kahi maʻi laha ʻole kahi wahine i loaʻa nā chromosome kāne a ʻo ia ke kumu e ulu ʻole ai kāna mau ʻōpū a ʻaʻohe ona kiʻi wahine. Hana ʻia kāna lāʻau lapaʻau me ka hoʻohana ʻana o nā hormones wahine synthetic no ke ola, akā ʻaʻole hiki ke hāpai.
Nā ʻōuli o Swyer Syndrome
ʻO nā ʻōuli o Swyer Syndrome:
- Ka loaʻa ʻole o ka menstruation i ka wā ʻōpio;
- Liʻiliʻi paha ka ulu ʻana o ka umauma;
- ʻO ka helehelena wahine liʻiliʻi;
- ʻO ka lauoho axillary maʻamau a me ka pubic;
- He kino kiʻekiʻe paha ke kiʻekiʻe;
- Aia kekahi ʻōpū maʻamau a pēpē paha, nā paipu a me nā ʻāpana kiʻekiʻe o ka lua.
ʻIke o Swyer maʻi maʻi
No ka hōʻailona o Swyer syndrome, pono e hana i nā hoʻokolohua koko e hōʻike i nā gonadotropins kiʻekiʻe a hoʻemi ʻia nā pae o ka estrogen a me ka testosterone. Hoʻohui ʻia e koi ʻia:
- nā hoʻokolohua hoʻokolohua e nānā no nā maʻi infectious a autoimmune paha,
- kālailai analysis,
- nā aʻo molekole a
- Koi ʻia ka biopsy ʻōpala ovarian.
Hoʻomaopopo pinepine ʻia kēia maʻi maʻi i ka wā ʻōpio.
Nā kumu o Swyer Syndrome
ʻO nā kumu o Swyer syndrome he genetic.
Hoʻomaʻo no Swyer syndrome
Hana ʻia ka lāʻau no Swyer Syndrome me ka hoʻohana ʻana o nā hormones synthetic no ke ola. ʻO kēia lāʻau e hoʻonui i ka helehelena wahine i wahine, akā ʻaʻole ʻae i ka hāpai ʻana.
ʻO kahi pilikia maʻamau o ka maʻi o Swyer ka ulu ʻana o kahi tumo i nā gonad a hōʻike ʻia ke kahakaha no kona hemo ʻana ma ke ʻano he ala e pale aku ai i kēia ʻano maʻi ʻaʻai.