ʻO Hugles-Stovin Syndrome Nā hōʻailona a me ka mālama ʻana

Anter

• Nā ʻōuli
• Lapaʻau
• Nā pilikia

ʻO ka maʻi Hugles-stovin kahi maʻi liʻiliʻi loa a koʻikoʻi hoʻi e kumu i nā aneurysms he nui i ke aʻa aʻa a me nā hihia o ka thrombosis hohonu i ke ola. Mai ka wehewehe mua o kēia maʻi ma ka honua holoʻokoʻa, ma lalo o 40 ka poʻe i ʻike ʻia e ka makahiki 2013.

Hiki i ka maʻi ke hōʻike iā ia iho i nā hanana like ʻole he 3, kahi e hōʻike mau ai ka mua me ka thrombophlebitis, ka pae ʻelua me nā aneurysms pulmonary, a ʻo ke kolu a me ka pae hope loa i hōʻike ʻia e ka haki ʻana o kahi aneurism e hiki ai ke hōʻeha i ke koko a me ka make.

ʻO ke kauka kūpono loa e kuhikuhi a mālama i kēia maʻi ʻo ia ka rheumatologist a ʻoiai ʻaʻole i ʻike piha ʻia kāna kumu, manaʻo ʻia he pili paha ia i kahi vasculitis ʻōnaehana.

Nā ʻōuli

ʻO nā hōʻailona ʻo Hugles-stovin:

• E hoʻomake ana i ke koko;
• Hanu paʻakikī;
• Manaʻo o ka pōkole o ka hanu;
• ʻEha poʻo poʻo;
• Kiʻekiʻena, hoʻomau kuni;
• Loaʻa o 10% o ke kaupaona me ke kumu ʻole;
• ʻO Papilledema, kahi dilation o ka optic papilla e hōʻike ana i ka hoʻonui ʻana o ke kaomi i loko o ka lolo;
• ʻO ka pehu a me ka ʻeha nui i ka bipi keiki;
• ʻIke pālua a
• Nā manaʻo hoʻohoka.

ʻO ka maʻamau he kanaka me ka maʻi Hugles-stovin i loaʻa nā ʻōuli no nā makahiki he nui a hiki ke huikau ʻia ka maʻi me ka maʻi o Behçet a manaʻo kekahi poʻe noiʻi ʻo kēia maʻi he ʻano piha ʻole o ka maʻi o Behçet.

ʻAʻohe ʻike iki ʻia kēia maʻi i ka wā kamaliʻi a hiki ke ʻike ʻia i ka wā ʻōpio a makua paha ma hope o ka hōʻike ʻana i nā ʻōuli i hōʻike ʻia aʻe nei a me nā hoʻokolohua ʻana e like me nā hoʻokolohua koko, nā X-ray umauma, MRI a i ʻole ka tomography i helu ʻia o ke poʻo a me ka umauma, ma kahi o ka ultrasound doppler e nānā. kahe o ke koko a me ka naʻau. ʻAʻohe kumu hoʻohālikelike a me ke kauka e kānalua i kēia maʻi ma muli o ka like me ka maʻi o Behçet, akā me ka ʻole o kāna mau ʻano āpau.

ʻO nā makahiki o ka poʻe i ʻike ʻia me kēia maʻi ʻokoʻa ma waena o 12 a me 48 mau makahiki.

Lapaʻau

ʻAʻole kikoʻī ka lapaʻau ʻana no ka maʻi ʻo Hugles-Stovin, akā hiki i ke kauka ke koi aku i ka hoʻohana ʻana i nā corticosteroids e like me ka hydrocortisone a i ʻole prednisone, nā anticoagulants e like me enoxaparin, pulse therapy a me nā immunosuppressants e like me Infliximab a i ʻole Adalimumab i hiki ke hoʻēmi i ka makaʻi a me nā hopena pū kekahi. o nā aneurysms a me ka thrombosis, no laila hoʻomaikaʻi i ka maikaʻi o ke ola a me ka hōʻemi ʻana i ka make o ka make.

Nā pilikia

Hiki i ka Hugles-Stovin maʻi ke paʻakikī e mālama a he make nui kona no ka mea ʻaʻole i ʻike ʻia ke kumu o ka maʻi a no laila ʻaʻole lawa paha nā mālama e mālama ai i ke olakino o ka mea i hoʻopilikia ʻia. No ka mea aia kekahi mau hihia i ʻike ʻia ma ka honua holoʻokoʻa, ʻaʻole maʻa mau nā kauka i kēia maʻi, kahi e lilo ai ka paʻakikī a me ka hoʻomaʻamaʻa ʻana.

Hoʻohui ʻia, pono e hoʻohana me ka mālama nui i nā anticoagulants no ka mea i kekahi mau hihia hiki iā lākou ke hoʻonui i ka makaʻu o ke kahe ʻana ma hope o ka haki ʻana o ka aneurysm a me ke kahe o ke koko i mea e pale ai i ka mālama ʻana i ke ola.