ʻO Pityriasis Rubra Pilaris

Anter

• Nā ʻano o ka rubri pilaris aloha
• Nā kiʻi o PRP
• He aha ke kumu o PRP?
• Pehea hoʻoilina PRP?
• He aha nā hōʻailona o PRP?
• Pehea e ʻike ʻia ai ka PRP?
• He aha nā pilikia kūpono o PRP?
• Pehea e mālama ʻia ai ʻo PRP?
• Hiki iaʻu ke pale aku iā PRP?
• E hele aku ʻo PRP?
• E kamaʻilio me kāu kauka

Hoʻolauna

ʻO Pityriasis rubra pilaris (PRP) kahi maʻi ʻili laha ʻole. Kuhi ia i ka mumū mau a me ka hoʻokahe ʻana o ka ʻili. Hiki i ka PRP ke hoʻopili i nā ʻāpana o kou kino a i ʻole kou kino holoʻokoʻa. E hoʻomaka paha ka maʻi i ka wā kamaliʻi a makua paha. Hoʻopili like ʻo PRP i nā kāne a me nā wahine.

Nā ʻano o ka rubri pilaris aloha

Aia he ʻeono ʻano o PRP.

ʻO PRP ka hoʻomaka mua o ka makua ka ʻano maʻamau. Kū i ka wā makua. Hele pinepine nā ʻōuli ma hope o kekahi mau makahiki. I kekahi mau hihia kakaikahi, hoʻi nā ʻōuli ma hope.

Hoʻomaka ka PRP hoʻomaka mua atypical i ka wā makua. Eia naʻe, ʻoi aku ka lōʻihi o nā hōʻailona ma mua o 20 mau makahiki.

Hoʻomaka ka PRP ʻōpio ʻōpio Classical i ka wā kamaliʻi. Hele pinepine nā ʻōuli i loko o hoʻokahi makahiki, akā hoʻi paha lākou ma hope.

Hoʻomaka ka PRP kamaliʻi liʻiliʻi ma mua o ka wā ʻōpio. Hoʻohui pinepine ia i nā poho lima o nā keiki, nā wāwae o ko lākou mau wāwae, a me ko lākou mau kuli a me nā kuʻekuʻe lima. E hala paha nā ʻōuli i nā makahiki ʻōpio.

Hoʻoilina ʻia ʻo PRP ʻōpio atypical i kekahi manawa. ʻO ia ka mea i hoʻoili ʻia ma o ka ʻohana. Hiki iā ia ke noho ma ka hānau a hoʻomohala paha i ka wā kamaliʻi. Kū mau nā ʻōuli no ke ola.

Pili ka PRP pili i ka HIV me HIV. He paʻakikī loa e mālama.

Nā kiʻi o PRP

He aha ke kumu o PRP?

ʻAʻole ʻike ʻia ke kumu kūpono o PRP. Kū pinepine ʻo PRP me ke kumu ʻole. ʻOiai hoʻoilina kekahi mau hihia o PRP, ʻaʻole ka hapanui. Hoʻoikaika ka PRP hoʻoilina i ke koʻikoʻi.

Pili paha ka PRP hoʻomaka makua makua me ka maʻi ʻaʻai ʻele. Eia nō naʻe, pehea ka ʻike pinepine ʻole ʻia ʻana o ka maʻi ʻaʻai ʻili me kēia ʻano PRP. Inā loaʻa iā ʻoe ka PRP hoʻomaka mua, e ʻike pono ʻike ʻoe i kāu kauka e nānā ai no ka maʻi ʻaʻai ʻili.

Wahi a ka National Organization for Rare Disorder, hōʻike ka noiʻi mua i PRP paha ma muli o kahi pilikia i ke ʻano o ke kino e hana ai i ka huaora A. Eia naʻe, pono e ʻike hou ʻia kahi noiʻi e ʻike inā he ʻoiaʻiʻo kēia.

Pili pū paha ka PRP i kahi pane ʻōnaehana pale, e like me ka Genetic and Rare Diseases Information Center.

Pehea hoʻoilina PRP?

Hiki ke hoʻoilina ʻia PRP. Hiki iā ʻoe ke hoʻoilina iā PRP inā haʻalele kekahi o kou mau mākua i ka ʻāpana i kumu i kēia maʻi. Hiki i kou makua ke lawe i ka ʻāpana, ʻo ia hoʻi he ʻāpana ko lākou akā ʻaʻohe o lākou maʻi. Inā lawe kekahi o kou mau mākua i ka ʻāpana, aia kahi 50 pakeneka o ka manawa i hāʻawi ʻia ai ka ʻāpana iā ʻoe. Eia nō naʻe, ʻaʻole hiki iā ʻoe ke hoʻomohala i ka PRP inā ua hoʻoilina ʻoe i ka ʻāpana.

He aha nā hōʻailona o PRP?

Hoʻokumu ʻo PRP i nā pālahalaha ʻulaʻula, ʻulaʻula, a ʻalani-ʻulaʻula i kou ʻili. ʻIke mau nā pālaha. Loaʻa paha iā ʻoe nā pāleo scaly ma kekahi mau ʻāpana o kou kino. Kū pinepine lākou ma ka:

• kuʻekuʻe lima
• nā kuli
• lima
• wawae
• kuʻekuʻe wāwae

E ʻulaʻula a mānoanoa hoʻi ka ʻili ma nā poho lima o kou mau lima a me kou mau wāwae. E pāhola paha nā pālahalaha ma luna o ke kino holoʻokoʻa.

Pehea e ʻike ʻia ai ka PRP?

Kuhi hewa pinepine ʻo PRP no nā ʻano ʻili ʻē aʻe i ʻike pinepine ʻia, e like me psoriasis. Hiki ke kuhihewa ʻia no nā mea liʻiliʻi, e like me ka lichen planus a me ka roseriasis rosea. Kaha ʻia ka Ps Ps e itchy, scaly patches o ka ʻili i ʻulaʻula pinepine. Eia naʻe, ʻokoʻa PRP, hiki ke maʻalahi a mālama maikaʻi ʻia ʻo psoriasis. ʻAʻole paha e ʻike ʻia ʻo PRP a hiki i ka pane ʻole ʻana o nā patch scaly i ka mālama ʻana iā psoriasis.

Inā kānalua kāu kauka iā PRP, hana paha lākou i kahi biopsy o ka ʻili e kōkua iā lākou e hana i kahi kuhi. No kēia kaʻina hana, lawe aku kāu kauka i kahi laʻana liʻiliʻi o kou ʻili. Nānā lākou ma lalo o ka microscope e kālailai ia.

He aha nā pilikia kūpono o PRP?

No ka hapa nui, hiki i ka PRP ke huehue a hōʻoluʻolu ʻole. Hiki i kēia mau ʻōuli ke hōʻemi i ka manawa, ʻoiai ke nānā aku ka ʻōpala e like me ka mea e ʻino ana. ʻAʻole kū ke ʻano i nā pilikia he nui.

Eia nō naʻe, kahakaha ka Pūʻulu Kākoʻo PRP i kekahi manawa hiki i ka ʻūlū ke alakaʻi i nā pilikia ʻē aʻe, e like me ka ectropion. I kēia kūlana, huli ka eyelid, e hōʻike ana i ka maka o ka maka. Hiki i ka PRP ke alakaʻi i nā pilikia me ka uhi o ka waha. Hiki i kēia ke hopena i ka huhū a me ka ʻeha.

Ma hope o ka manawa, hiki i ka PRP ke alakaʻi i keratoderma. Kuhi kēia pilikia i ka ʻili ma kou mau lima a me nā wāwae o kou wāwae e mānoanoa. Hiki ke hoʻomohala i nā māwae hohonu i ka ʻili, i kapa ʻia nā māwae.

Pilikia pū kekahi poʻe me PRP i ka mālam. Hiki paha iā lākou ke pilikia i ka hou ʻana a i ʻole ka kaohi ʻana i ka mahana o ko lākou kino ke wela.

Pehea e mālama ʻia ai ʻo PRP?

ʻAʻohe mea ola i kēia manawa no PRP, akā hiki i ka lapaʻau ke hōʻoluʻolu i nā ʻōuli. Kauoha paha kāu kauka i hoʻokahi a ʻoi paha o nā ʻano ma hope aʻe nei:

• ʻO nā kalima kumuhana e piha ana i ka urea a i ʻole ka waikawa lactic. Hele pololei kēia i kou ʻili.
• Retinoids waha. ʻO nā laʻana me isotretinoin a i ʻole acitretin. ʻO kēia nā kūmole o ka wikamina A e hoʻolohi i ka ulu a me ka hoʻokahe ʻana o nā ʻili ʻili.
• ʻO ka wikamina A. waha Kōkua paha kēia i kekahi poʻe, akā i nā koina kiʻekiʻe loa wale nō. ʻOi aku ka maikaʻi o nā Retinoids a hoʻohana pinepine ʻia ma mua o ka wikamina A.
• Methotrexate. ʻO kēia kahi lāʻau lapaʻau waha e hiki ke hoʻohana ʻia inā ʻaʻole holo pono nā retinoids.
• Nā Immunosuppressants. ʻO kēia nā lāʻau lapaʻau oral e kāohi i ka ʻōnaehana pale. Hoʻopili lākou iā cyclosporine a me azathioprine.
• ʻO Biologics. ʻO kēia nā lāʻau i hoʻokomo ʻia a i ʻole intravenous (IV) e hoʻopili i kāu ʻōnaehana pale. Hoʻopili lākou i nā lāʻau adalimumab, etanercept, a me infliximab.
• ʻO ka hoʻomaʻamaʻa kukui Ultraviolet. Hāʻawi ʻia kēia i ka hui pū me psoralen (kahi lāʻau e hōʻemi iā ʻoe i ka lā) a me kahi retinoid.

Hiki iaʻu ke pale aku iā PRP?

ʻAʻole hiki ke pale aku iā PRP mai ka ʻike ʻole ʻia o ke kumu a me ka hoʻomaka. Inā manaʻo ʻoe he PRP kāu, e ʻike i kāu kauka. Ke hoʻomaka nei i kahi lāʻau e hana pono iā ʻoe ke loaʻa ʻoe i kahi hōʻailona he kī nui e hōʻoluʻolu i kāu mau ʻōuli.

He mea nui ka ʻimi ʻana i kahi lapaʻau kūpono no ka mea hiki iā ʻoe ke hoʻomohala ma mua o hoʻokahi ʻano PRP ma mua o ka maʻi.

E hele aku ʻo PRP?

Kaukaʻi ʻia i ke ʻano o PRP i loaʻa iā ʻoe, a i ʻole hele paha kāu mau ʻōuli. Inā loaʻa iā ʻoe ka PRP hoʻomaka makua makua, e mau paha kāu mau hōʻailona i kekahi mau makahiki a i ʻole ka liʻiliʻi a laila ʻaʻole hoʻi e hoʻi.

ʻOi aku ka lōʻihi o nā ʻōuli o nā ʻano PRP ʻē aʻe. Eia nō naʻe, hiki i nā mālama ʻana ke hōʻemi i nā ʻōuli.

E kamaʻilio me kāu kauka

ʻO PRP kahi maʻi ʻili laha ʻole i kaha ʻia e ka mumū mau a me ka hoʻokahe ʻana o kou ʻili. Hoʻopili paha ia i kou kino holoʻokoʻa a i ʻole nā ​​ʻāpana o ia mea. Hiki iā ia ke hoʻomaka i kēlā me kēia manawa i kou ola. ʻOiai ʻaʻohe mea ola i kēia manawa, hiki i nā mālama ke kōkua i ka hōʻoluʻolu i kāu mau ʻōuli.

ʻO nā mālama ʻana no PRP e pili ana i nā lāʻau kumuhana, waha, a me nā injectable. Hoʻopili pū lākou i ka ultraviolet light therapy. Hana pū me kāu kauka e ʻike i ka lāʻau e hana maikaʻi loa e hōʻoluʻolu i kāu mau ʻōuli o PRP.