Nā pilikia o Myelofibrosis a me nā ala e hōʻemi ai i kāu pilikia

Anter
- ʻLepala hoʻonui
- Nā Tumors (ulu ʻole noncancerous) i nā ʻāpana ʻē aʻe o kou kino
- Ka piʻi kiʻekiʻe o ka puka
- Helu pālāki haʻahaʻa
- ʻEha iwi a me ka ʻeha pū
- Goute
- Anemia ʻaʻano koʻikoʻi
- Leukemia myeloid huehue (AML)
- Ka mālama ʻana i nā pilikia ʻo MF
- E hoʻemi ana i kou makaʻu i nā pilikia ʻo MF
- ʻO ka lawe lawe ʻana
ʻO Myelofibrosis (MF) kahi ʻano mau o ka maʻi ʻaʻai koko ma kahi o nā mākala ma ka iwi o ka iwi e hoʻolohi ai i ka hana ʻana i nā hunaola olakino maikaʻi. ʻO ka hemahema o nā hunaola koko ke kumu o nā ʻōuli a me nā pilikia o MF, e like me ka luhi, palu maʻalahi, ka wela, a me ka iwi a me ka ʻeha pū.
ʻAʻole ʻike ka poʻe he nui i kekahi mau ʻōuli i ka wā mua o ka maʻi. Ke holo nei ka maʻi, hoʻomaka paha nā ʻōuli a me nā pilikia i hoʻopaʻa ʻia i nā helu o ke koko ʻino ʻole.
He mea nui e hana pū me kāu kauka e mālama pono iā MF, keu hoʻi ke hoʻomaka ʻoe e ʻike i nā hōʻailona. Hiki i ke kōkua ʻana ke kōkua i ka hōʻemi ʻana i kou pilikia o nā pilikia a hoʻonui i ke ola.
Eia kahi nānā kokoke loa i nā pilikia kūpono o MF a pehea e hiki ai iā ʻoe ke hōʻemi i kou makaʻi.
ʻLepala hoʻonui
Kōkua kou puʻupuʻu i ke kaua ʻana i nā maʻi a kānana i nā kino koko i hōʻino ʻia. Mālama pū kekahi ia i nā ʻulaʻula a me nā pāpale e kōkua i kou koko koko.
Ke loaʻa iā MF, ʻaʻole hiki i kou iwi iwi ke hana i lawa ke koko ma muli o ka scarring. Hana ʻia nā hunaola koko ma waho o ka iwi iwi i nā ʻāpana ʻē aʻe o kou kino, e like me kou puʻupaʻa.
Kuhi ʻia kēia ma ke ʻano hematopoiesis extramedullary. Lilo ka ʻōpala i kekahi manawa i mea maʻamau ʻole ke hana ʻoi aku ka paʻakikī e hana i kēia mau hunaola.
Hiki i kahi spleen hoʻonui ʻia (splenomegaly) ke hana i nā ʻōuli hōʻoluʻolu ʻole. Hiki iā ia ke hōʻeha i ka ʻeha o ka ʻōpū ke kūʻē ia i nā mea ʻē aʻe a hōʻona iā ʻoe inā ʻaʻole ʻoe i ʻai nui.
Nā Tumors (ulu ʻole noncancerous) i nā ʻāpana ʻē aʻe o kou kino
Ke hana ʻia nā hunaola koko ma waho o ka iwi iwi, noncancerous tumors of hoʻomoʻa ʻana i nā hunaola koko i kekahi manawa ma nā wahi ʻē aʻe o ke kino.
Hiki i kēia mau tumors ke kumu i ke kahe ʻana o ka wai i loko o kāu ʻōnaehana gastrointestinal. Hana paha kēia iā ʻoe i ka huehue a kuha i ke koko. Hiki i nā tumors ke ʻomi i kou kaula kuʻikuʻi a i ʻole ke kumu o ka hopu ʻana.
Ka piʻi kiʻekiʻe o ka puka
Kahe ke koko mai ke ākea i ke ake ma o ka veins portal. ʻO ka hoʻonui ʻia o ke kahe o ke koko i kahi ākea ākea i ka MF ke kumu o ke kahe o ke koko kiʻekiʻe i ka veins portal.
ʻO ka hoʻonui ʻia o ke kahe o ke koko i kekahi manawa e hoʻoikaika i ka nui o ke koko i loko o ka ʻōpū a me ka esophagus. Hiki paha i kēia ke haki i nā veins liʻiliʻi a hana i ke kahe ʻana o ke kahe. E pili ana i ka poʻe me MF ʻike i kēia pilikia.
Helu pālāki haʻahaʻa
Kōkua nā platelet i ke koko i kou koko e ʻūlū ma hope o kahi ʻeha. Hiki ke hāʻule i ka helu platelet ma lalo o ka maʻamau ke holo a MF. ʻO kahi helu haʻahaʻa o nā platelet i ʻike ʻia ma ke ʻano he thrombositopenia.
Me ka lawa ʻole o nā platelet, ʻaʻole hiki i kou koko ke hoʻopili pono. Hiki i kēia ke hana iā ʻoe i ke kahe maʻalahi.
ʻEha iwi a me ka ʻeha pū
Hiki iā MF ke paʻakikī i kou momona iwi. Hiki iā ia ke alakaʻi i ka mumū i nā pūnaewele hoʻopili a puni nā iwi. ʻO kēia ke alakaʻi i ka iwi a me ka ʻeha pū.
Goute
Hoʻokumu ʻo MF i ke kino e hana i nā waikawa uric ma mua o ka maʻamau. Inā crystallize ka waikawa uric, noho ʻo ia i kekahi manawa i nā hono. Kuhi ʻia kēia ma ke ʻano he gout. Hiki i ke gout ke hoʻoulu i nā hono pehu a ʻeha hoʻi.
Anemia ʻaʻano koʻikoʻi
ʻO kahi helu o ke koko ʻulaʻula haʻahaʻa i ʻike ʻia he anemia kahi hōʻailona MF maʻamau. I kekahi manawa lilo ka anemia i mea koʻikoʻi a hoʻonāukiuki i ka luhi, palapū a me nā ʻōuli ʻē aʻe.
Leukemia myeloid huehue (AML)
No kahi o 15 a 20 pākēneka o ka poʻe, holomua ʻo MF i kahi ʻano maʻi ʻoi loa o ka maʻi ʻaʻai i kapa ʻia ʻo myeloid leukemia (AML). He holomua holomua ʻo AML o ke koko a me ka iwi o ka iwi.
Ka mālama ʻana i nā pilikia ʻo MF
Kau kauka paha i kau kauka like ʻole e hoʻoponopono i nā pilikia ʻo MF. Pākuʻi ʻia kēia mau mea:
- Nā mea hoʻopuka JAK, me ruxolitinib (Jakafi) a me fedratinib (Inrebic)
- nā lāʻau lapaʻau immunomodulatory, e like me thalidomide (Thalomid), lenalidomide (Revlimid), interferons, a me pomalidomide (Pomalyst)
- corticosteroids, e like me prednisone
- wehe ʻoki o ka spleen (splenectomy)
- androgen therapy
- nā lāʻau chemotherapy, e like me hydroxyurea
E hoʻemi ana i kou makaʻu i nā pilikia ʻo MF
Pono e hana pū me kāu kauka e hoʻokele iā MF. ʻO ke kia pinepine pinepine ʻana ka mea nui e hōʻemi ai i kou pilikia o nā pilikia ʻo MF. Hiki i kāu kauka ke noi iā ʻoe e hele i loko no nā helu o ke koko a me nā hōʻike kino i hoʻokahi a ʻelua mau manawa i kēlā me kēia makahiki a i ʻole pinepine i hoʻokahi manawa i ka pule.
Inā ʻaʻohe ou ʻōuli i kēia manawa a me ka MF haʻahaʻa haʻahaʻa, ʻaʻohe hōʻike e pōmaikaʻi ʻoe mai nā hana mua. E kali paha kāu kauka e hoʻomaka i nā hana lapaʻau a hiki i ka holomua o kāu kūlana.
Inā loaʻa iā ʻoe nā hōʻailona a i ʻole MF waena waena a i ʻole pilikia nui, hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau.
Hoʻopili nā JAK i nā ruxolitinib a me fedratinib pahuhopu i nā ala maʻamau e hōʻailona ʻia e kahi mutation gen MF maʻamau. Ua hōʻike ʻia kēia mau lāʻau e hoʻoliʻiliʻi nui i ka nui o ka spleen a kuhikuhi i nā ʻōuli hoʻonāwaliwali e like me ka iwi a me ka ʻeha pū. Hiki i ka noiʻi ke hōʻemi nui i ka makaʻu o nā pilikia a hoʻonui i ke ola.
ʻO ka hoʻoneʻe ʻana o ka iwi iwi ka mea lapaʻau e hiki ke hoola iā MF. Pili ia i ka loaʻa ʻana o kahi infusion o nā hunaola kūmole mai kahi mea hāʻawi olakino, kahi e pani ai i nā pūnaʻi koʻokoʻo hewahewa e hana ana i nā ʻōuli MF.
Hāpai kēia kaʻina hana i nā pōʻino nui a weliweli paha i ke ola. Manaʻo wale ʻia ia no ka poʻe ʻōpio me ka ʻole o nā kūlana olakino preexisting ʻē aʻe.
Hoʻomohala mau ʻia nā mālama ʻana ʻo MF Hou. E hoʻāʻo e noho i kēia lā no ka noiʻi hou loa ma MF, a nīnau i kāu kauka e pili ana inā ʻoe e noʻonoʻo e kākau inoa i kahi hoʻokolohua hoʻokolohua.
ʻO ka lawe lawe ʻana
ʻO Myelofibrosis kahi maʻi ʻaʻai laha ʻole kahi e mālama ai ka scarring i kou iwi iwi mai ka hoʻohua pono ʻana i nā hunaola olakino maikaʻi. Inā loaʻa iā ʻoe ka MF waena waena a i ʻole pilikia nui, hiki i kekahi mau hōʻailona ke hoʻoponopono i nā hōʻailona, hoʻemi i kou makaʻi i nā pilikia, a hoʻonui i ke ola.
Hoʻomau ka nui o nā hoʻokolohua mau e ʻimi i nā lāʻau hou. E launa pū me kāu kauka a kūkākūkā i nā ʻano hana kūpono e kūpono iā ʻoe.