Mea Kākau: Louise Ward
Lā O Ka Hana: 4 Pepeluali 2021
HōʻAno Hou I Ka Lā: 1 Iulai 2025
Anonim
Nā pilikia o Myelofibrosis a me nā ala e hōʻemi ai i kāu pilikia - Ola Kino
Nā pilikia o Myelofibrosis a me nā ala e hōʻemi ai i kāu pilikia - Ola Kino

Anter

ʻO Myelofibrosis (MF) kahi ʻano mau o ka maʻi ʻaʻai koko ma kahi o nā mākala ma ka iwi o ka iwi e hoʻolohi ai i ka hana ʻana i nā hunaola olakino maikaʻi. ʻO ka hemahema o nā hunaola koko ke kumu o nā ʻōuli a me nā pilikia o MF, e like me ka luhi, palu maʻalahi, ka wela, a me ka iwi a me ka ʻeha pū.

ʻAʻole ʻike ka poʻe he nui i kekahi mau ʻōuli i ka wā mua o ka maʻi. Ke holo nei ka maʻi, hoʻomaka paha nā ʻōuli a me nā pilikia i hoʻopaʻa ʻia i nā helu o ke koko ʻino ʻole.

He mea nui e hana pū me kāu kauka e mālama pono iā MF, keu hoʻi ke hoʻomaka ʻoe e ʻike i nā hōʻailona. Hiki i ke kōkua ʻana ke kōkua i ka hōʻemi ʻana i kou pilikia o nā pilikia a hoʻonui i ke ola.

Eia kahi nānā kokoke loa i nā pilikia kūpono o MF a pehea e hiki ai iā ʻoe ke hōʻemi i kou makaʻi.

ʻLepala hoʻonui

Kōkua kou puʻupuʻu i ke kaua ʻana i nā maʻi a kānana i nā kino koko i hōʻino ʻia. Mālama pū kekahi ia i nā ʻulaʻula a me nā pāpale e kōkua i kou koko koko.

Ke loaʻa iā MF, ʻaʻole hiki i kou iwi iwi ke hana i lawa ke koko ma muli o ka scarring. Hana ʻia nā hunaola koko ma waho o ka iwi iwi i nā ʻāpana ʻē aʻe o kou kino, e like me kou puʻupaʻa.


Kuhi ʻia kēia ma ke ʻano hematopoiesis extramedullary. Lilo ka ʻōpala i kekahi manawa i mea maʻamau ʻole ke hana ʻoi aku ka paʻakikī e hana i kēia mau hunaola.

Hiki i kahi spleen hoʻonui ʻia (splenomegaly) ke hana i nā ʻōuli hōʻoluʻolu ʻole. Hiki iā ia ke hōʻeha i ka ʻeha o ka ʻōpū ke kūʻē ia i nā mea ʻē aʻe a hōʻona iā ʻoe inā ʻaʻole ʻoe i ʻai nui.

Nā Tumors (ulu ʻole noncancerous) i nā ʻāpana ʻē aʻe o kou kino

Ke hana ʻia nā hunaola koko ma waho o ka iwi iwi, noncancerous tumors of hoʻomoʻa ʻana i nā hunaola koko i kekahi manawa ma nā wahi ʻē aʻe o ke kino.

Hiki i kēia mau tumors ke kumu i ke kahe ʻana o ka wai i loko o kāu ʻōnaehana gastrointestinal. Hana paha kēia iā ʻoe i ka huehue a kuha i ke koko. Hiki i nā tumors ke ʻomi i kou kaula kuʻikuʻi a i ʻole ke kumu o ka hopu ʻana.

Ka piʻi kiʻekiʻe o ka puka

Kahe ke koko mai ke ākea i ke ake ma o ka veins portal. ʻO ka hoʻonui ʻia o ke kahe o ke koko i kahi ākea ākea i ka MF ke kumu o ke kahe o ke koko kiʻekiʻe i ka veins portal.

ʻO ka hoʻonui ʻia o ke kahe o ke koko i kekahi manawa e hoʻoikaika i ka nui o ke koko i loko o ka ʻōpū a me ka esophagus. Hiki paha i kēia ke haki i nā veins liʻiliʻi a hana i ke kahe ʻana o ke kahe. E pili ana i ka poʻe me MF ʻike i kēia pilikia.


Helu pālāki haʻahaʻa

Kōkua nā platelet i ke koko i kou koko e ʻūlū ma hope o kahi ʻeha. Hiki ke hāʻule i ka helu platelet ma lalo o ka maʻamau ke holo a MF. ʻO kahi helu haʻahaʻa o nā platelet i ʻike ʻia ma ke ʻano he thrombositopenia.

Me ka lawa ʻole o nā platelet, ʻaʻole hiki i kou koko ke hoʻopili pono. Hiki i kēia ke hana iā ʻoe i ke kahe maʻalahi.

ʻEha iwi a me ka ʻeha pū

Hiki iā MF ke paʻakikī i kou momona iwi. Hiki iā ia ke alakaʻi i ka mumū i nā pūnaewele hoʻopili a puni nā iwi. ʻO kēia ke alakaʻi i ka iwi a me ka ʻeha pū.

Goute

Hoʻokumu ʻo MF i ke kino e hana i nā waikawa uric ma mua o ka maʻamau. Inā crystallize ka waikawa uric, noho ʻo ia i kekahi manawa i nā hono. Kuhi ʻia kēia ma ke ʻano he gout. Hiki i ke gout ke hoʻoulu i nā hono pehu a ʻeha hoʻi.

Anemia ʻaʻano koʻikoʻi

ʻO kahi helu o ke koko ʻulaʻula haʻahaʻa i ʻike ʻia he anemia kahi hōʻailona MF maʻamau. I kekahi manawa lilo ka anemia i mea koʻikoʻi a hoʻonāukiuki i ka luhi, palapū a me nā ʻōuli ʻē aʻe.

Leukemia myeloid huehue (AML)

No kahi o 15 a 20 pākēneka o ka poʻe, holomua ʻo MF i kahi ʻano maʻi ʻoi loa o ka maʻi ʻaʻai i kapa ʻia ʻo myeloid leukemia (AML). He holomua holomua ʻo AML o ke koko a me ka iwi o ka iwi.


Ka mālama ʻana i nā pilikia ʻo MF

Kau kauka paha i kau kauka like ʻole e hoʻoponopono i nā pilikia ʻo MF. Pākuʻi ʻia kēia mau mea:

  • Nā mea hoʻopuka JAK, me ruxolitinib (Jakafi) a me fedratinib (Inrebic)
  • nā lāʻau lapaʻau immunomodulatory, e like me thalidomide (Thalomid), lenalidomide (Revlimid), interferons, a me pomalidomide (Pomalyst)
  • corticosteroids, e like me prednisone
  • wehe ʻoki o ka spleen (splenectomy)
  • androgen therapy
  • nā lāʻau chemotherapy, e like me hydroxyurea

E hoʻemi ana i kou makaʻu i nā pilikia ʻo MF

Pono e hana pū me kāu kauka e hoʻokele iā MF. ʻO ke kia pinepine pinepine ʻana ka mea nui e hōʻemi ai i kou pilikia o nā pilikia ʻo MF. Hiki i kāu kauka ke noi iā ʻoe e hele i loko no nā helu o ke koko a me nā hōʻike kino i hoʻokahi a ʻelua mau manawa i kēlā me kēia makahiki a i ʻole pinepine i hoʻokahi manawa i ka pule.

Inā ʻaʻohe ou ʻōuli i kēia manawa a me ka MF haʻahaʻa haʻahaʻa, ʻaʻohe hōʻike e pōmaikaʻi ʻoe mai nā hana mua. E kali paha kāu kauka e hoʻomaka i nā hana lapaʻau a hiki i ka holomua o kāu kūlana.

Inā loaʻa iā ʻoe nā hōʻailona a i ʻole MF waena waena a i ʻole pilikia nui, hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau.

Hoʻopili nā JAK i nā ruxolitinib a me fedratinib pahuhopu i nā ala maʻamau e hōʻailona ʻia e kahi mutation gen MF maʻamau. Ua hōʻike ʻia kēia mau lāʻau e hoʻoliʻiliʻi nui i ka nui o ka spleen a kuhikuhi i nā ʻōuli hoʻonāwaliwali e like me ka iwi a me ka ʻeha pū. Hiki i ka noiʻi ke hōʻemi nui i ka makaʻu o nā pilikia a hoʻonui i ke ola.

ʻO ka hoʻoneʻe ʻana o ka iwi iwi ka mea lapaʻau e hiki ke hoola iā MF. Pili ia i ka loaʻa ʻana o kahi infusion o nā hunaola kūmole mai kahi mea hāʻawi olakino, kahi e pani ai i nā pūnaʻi koʻokoʻo hewahewa e hana ana i nā ʻōuli MF.

Hāpai kēia kaʻina hana i nā pōʻino nui a weliweli paha i ke ola. Manaʻo wale ʻia ia no ka poʻe ʻōpio me ka ʻole o nā kūlana olakino preexisting ʻē aʻe.

Hoʻomohala mau ʻia nā mālama ʻana ʻo MF Hou. E hoʻāʻo e noho i kēia lā no ka noiʻi hou loa ma MF, a nīnau i kāu kauka e pili ana inā ʻoe e noʻonoʻo e kākau inoa i kahi hoʻokolohua hoʻokolohua.

ʻO ka lawe lawe ʻana

ʻO Myelofibrosis kahi maʻi ʻaʻai laha ʻole kahi e mālama ai ka scarring i kou iwi iwi mai ka hoʻohua pono ʻana i nā hunaola olakino maikaʻi. Inā loaʻa iā ʻoe ka MF waena waena a i ʻole pilikia nui, hiki i kekahi mau hōʻailona ke hoʻoponopono i nā hōʻailona, ​​hoʻemi i kou makaʻi i nā pilikia, a hoʻonui i ke ola.

Hoʻomau ka nui o nā hoʻokolohua mau e ʻimi i nā lāʻau hou. E launa pū me kāu kauka a kūkākūkā i nā ʻano hana kūpono e kūpono iā ʻoe.

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