ʻO ka maʻi ahi ahi: he aha ia, nā ʻōuli, nā kumu a me nā lāʻau

Anter
ʻO ka maʻi ahi ahi, i kapa ʻia i ka ʻepekema he pemphigus, kahi maʻi autoimmune laha ʻole kahi e hoʻopuka ai ka ʻōnaehana pale i nā mea ʻino e hoʻouka a luku i nā hunaola i loko o ka ʻili a me nā membrane mucous e like me ka waha, ka ihu, ka ʻāʻī a i ʻole nā genital, e hana ana i nā palapū a i ʻole nā ʻeha e hana i ke ahi wela. , ke ahi a me ka ʻeha, ʻo ka mea maʻamau i nā mākua a me nā poʻe kahiko, ʻoiai hiki ke hana i kēlā me kēia makahiki.
Hiki ke huikau nā ʻōuli o ke ahi ahiu me nā maʻi ʻili ʻē aʻe, e like me bullous pemphigoid, lupus erythematosus a me Hailey-Hailey maʻi, no ka laʻana. No laila, he mea nui e kūkākūkā ʻia ka dermatologist a i ʻole ka mea hana maʻamau i mea e hōʻoia ʻia ai ka ʻike ahi ahi ahi, a no laila, hiki ke hoʻomaka i ka lāʻau kūpono kūpono loa e hōʻoluʻolu i nā hōʻailona a pale i nā pilikia.

Nā hōʻailona nui
ʻO ka hōʻailona nui o ke ahi ahi ka hana ʻana i nā palapū i hiki wawe ke wāwahi a hana i nā ʻeha e hana i kahi ʻā ʻana a me ke ahi. Wahi a kahi i ʻike ʻia ai nā puʻupuʻu, hiki ke hoʻokaʻawale ʻia ka maʻi ahi ʻāhiu i ʻelua ʻano nui:
- Ke ahi ahi ahi a vulgar a i ʻole pemphigus vulgaris: Hoʻomaka ia me ka bliting i ka waha a laila ma ka ʻili a i ʻole nā membrane mucous e like me ka ʻāʻī, ka ihu a me nā genital, ʻeha mau akā ʻaʻole makaʻu. Ke ʻike ʻia i ka waha a i ʻole ka puʻu hiki iā lākou ke hana paʻakikī i ka ʻai ʻana a me ke kumu o ka hōʻino kino ʻole;
- Ke ahi ahi lau nahele a i ʻole pemphigus foliaceus: hana mau nā palapū ma ke poʻo, ka maka, ka ʻāʻī, ka umauma, kua a i ʻole nā poʻohiwi, e hoʻopili ana i ka papa o waho o ka ʻili, a hiki ke pālahalaha i loko o ke kino e hana ana i ka wela a me ka ʻeha. ʻAʻole kēia ʻano ahi ʻāhiu e kumu i nā blows mucous.
Inā ʻike ʻia nā palapū ma ka ʻili a i ʻole mucosa e hoʻōla ʻole ai, he mea nui e kūkākūkā ʻia ka dermatologist a i ʻole ka mea hana maʻamau, ʻoiai he mea hiki ke loiloi i nā ʻōuli a hōʻike ʻia nā hoʻokolohua a me nā biopsies. ʻIli a me nā mucosa e hōʻoia. ka hōʻailona o ka maʻi ahi ahi. Ke loaʻa ka maʻi o ke kanaka i ka ʻāʻī, hiki i ke kauka ke koi aku e hana i kahi endoscopy e hōʻoia i ka ahi ahi maʻamau.
Nā kumu kūpono
ʻO ke ahi ahi ahi kahi maʻi autoimmune kahi e pane ai ka ʻōnaehana pale pale kūʻē i nā hunaola i ka ʻili a i ʻole ka mucosa, e hoʻouka nei a luku aku nei i kēia mau hunaola me he mea lā he haole lākou i ke kino, e alakaʻi ai i ke ʻano o nā palapū a me nā ʻeha.
ʻO kekahi kumu o ka ahi ahi, ʻoiai ʻoi aku ka liʻiliʻi loa, ʻo ia ka hoʻohana ʻana i nā lāʻau e like me nā mea kāohi o ka angiotensin-hoʻololi i ka enzyme a i ʻole nā penicillins, i hiki ke makemake i ka hana ʻana o nā autoantibodies e hoʻouka i nā hunaola o ka ʻili, e alakaʻi ai i ke ahi lau nahele.

Pehea e hana ai i ka lāʻau
Hana ʻia ka mālama ʻana i ke ahi ahi e kaohi ai i nā ʻōuli, hoʻoliʻiliʻi i ke kūkulu ʻia ʻana o nā palapū a me nā ʻeha, a pale i nā pilikia e like me ka malnutr a i ʻole nā maʻi āpau. ʻO nā lāʻau i hiki i ka dermatologist ke ʻōlelo no ka mālama ʻana:
- Corticosteroids ma ke ʻano prednisone a prednisolone paha e hōʻemi i ka hoʻowahāwahā a hoʻēmi i ka hana o ka ʻōnaehana paleʻea, e hoʻohana ʻia i ka hana mua ʻana a me nā hihia maʻalahi;
- Nā Immunosuppressants e like me azathioprine, mycophenolate, methotrexate a i ʻole cyclophosphamide, ke kōkua nei lākou i ka pale ʻana i ka ʻōnaehana pale maʻi mai ka hoʻouka ʻana i ka ʻili a i ʻole nā mucous cells, a hoʻohana ʻia i nā hihia kahi e hoʻomaikaʻi ʻole ai nā corticosteroids a i ʻole ke kaulike i nā hihia koʻikoʻi.
- Pākuʻi monoclonal e like me rituximab, e hana nei ma ka kaohi ʻana i ka pale ʻana a me ka hōʻemi ʻana i nā hopena o ka ʻōnaehana pale ma ke kino, e hoʻohana pū ʻia me nā corticosteroids a i ʻole nā immunosuppressants no ka hana mua i nā hihia kaulike a koʻikoʻi paha.
Hoʻohui ʻia, hiki i ke kauka ke koi aku i nā lāʻau ʻē aʻe e like me nā mea hōʻoluʻolu ʻeha, antibiotic e hakakā i nā maʻi a i ʻole nā anesthetic lozenges no ka waha.
Inā ʻo ka hoʻohana ʻia ʻana o kekahi lāʻau i ke kumu o ka ʻike ʻia ʻana o nā palapū, ua lawa paha ka hōʻoki ʻana i ka hoʻohana ʻana o ka lāʻau e mālama ai i ka ahi ahi.
I nā hihia no kaʻai pono ʻole i hoʻokumu ʻia e ka papaʻai maikaʻi ʻole ma muli o nā palapū a me nā ʻeha ma ka waha a i ʻole ka ʻāʻī, hoʻokipa a me ka hoʻomaʻamaʻa ʻana me ka serum a me nā meaʻai a nā mākua, i hāʻawi pololei ʻia i ke aa, e pono a hiki i ke ola ʻana o ke kanaka.
Mālama i ka wā o ka mālama ʻana
Kūpono kekahi mau akahele i ka wā o ka mālama ʻana e kōkua iā ʻoe e ola wikiwiki a i ʻole e pale i ka hoʻi hou ʻana o nā ʻōuli.
- Mālama i nā ʻeha e like me ke kuhikuhi a ke kauka a kahu paha;
- E hoʻohana i ke kopa maʻalahi e holoi mālie i ke kino;
- Hōʻalo i ka puka ʻana o ka lā, ʻoiai hiki i ka radiation ultraviolet ke hana i nā palapū hou ma ka ʻili;
- Hōʻalo i nā meaʻai ʻono a ʻakika paha i hiki ke hoʻonāukiuki i nā huʻa i kou waha;
- Hōʻalo i nā hana kino i hiki ke hōʻeha i kou ʻili, e like me nā haʻuki pili.
I ka hanana ahi ahi ke kumu i nā pupuhi i ka waha e pale ai i ke kanaka mai ka ʻānai ʻana i nā niho a i ʻole ka flossing, pono paha ka lapaʻau kūikawā e pale ai i ka maʻi gum a i ʻole nā lua. No laila, he mea nui e nīnau aku i ka kauka niho e alakaʻi ʻia pehea e hana ai i ka hoʻomaʻemaʻe waha, e like me ke koʻikoʻi o kēlā me kēia hihia.