Empty Sella Syndrome
![Empty Sella Syndrome](https://i.ytimg.com/vi/Hpae8k-PH8Q/hqdefault.jpg)
Anter
- He aha ka Syndrome Sella nele?
- He aha nā hōʻailona?
- He aha nā kumu?
- ʻO Syndrome Sella hakahaka mua ʻole
- ʻO ka maʻi ʻelua Sella hakahaka
- Pehea ia ʻike?
- Pehea e mālama ʻia ai?
- He aha ke kuanaʻike
He aha ka Syndrome Sella nele?
ʻO ka maʻi Empty Sella kahi maʻi laha ʻole e pili ana i kahi ʻāpana o ka iwi poʻo i kapa ʻia ʻo ka sella turcica. ʻO ka sella turcica kahi indentation i ka iwi sphenoid ma ke kumu o kou iwi poʻo e paʻa ai ka pituitary gland.
Inā loaʻa iā ʻoe kahi maʻi maʻi hū ʻole, ʻaʻole hakahaka kāu sella turcica. I ka ʻoiaʻiʻo, ke ʻano o ka piha ʻana o kāu ʻona turcica a i ʻole piha paha me ka wai cerebrospinal (CSF). Loaʻa ka liʻiliʻi o ka pituitary glands i ka poʻe me ka sindrose Sella hakahaka. I kekahi mau hihia, ʻaʻole hōʻike nā pituitary glands i nā hoʻokolohua kiʻi.
Ke hoʻokumu ʻia ka maʻi hūnā ʻole e kahi ʻano ma lalo, ua kapa ʻia ʻo ka maʻi ʻelua ka mea kūʻai aku. Ke loaʻa ʻole kahi kumu i ʻike ʻia, ua kapa ʻia ʻo Syndrome sella hakahaka mua.
He aha nā hōʻailona?
ʻAʻohe o nā ʻōuli ma Empty Sella Syndrome. Eia nō naʻe, inā loaʻa iā ʻoe ka lua o ka lāʻau Sella hakahaka, loaʻa paha iā ʻoe nā hōʻailona e pili ana i ke ʻano o ke kumu.
He nui ka poʻe me ka maʻi make ʻole ka Sella i loaʻa i nā poʻo hina mau. ʻAʻole maopopo i nā kauka inā pili kēia i ka syndrome sella hakahaka a i ke kiʻekiʻe kiʻekiʻe o ke koko, a he nui nā poʻe me ka sadea hū ʻole i loaʻa.
I nā kūlana kakaʻikahi, pili ka maʻi sella hakahaka me ke kaomi ʻana i luna i ka iwi poʻo, a hiki ke alakaʻi iā:
- kahe mai ka wai ʻōiwi mai ka ihu
- pehu o ke aʻalolo optic i loko o ka maka
- pilikia pilikia ʻike
He aha nā kumu?
ʻO Syndrome Sella hakahaka mua ʻole
ʻAʻole maopopo ke kumu kūpono o ka Sella Syndrome hakahaka mua. Pili paha ia i kahi kīnā hānau i ka diaphragma sellae, kahi membrane e uhi ana i ka turaica sella. Hānau ʻia kekahi poʻe me kahi waimaka liʻiliʻi i ka diaphragma sellae, hiki ke hoʻoheheʻe i ka CSF i loko o ka sella turcica. ʻAʻole maopopo i nā kauka inā he kumu pololei kēia o ka maʻi sella hakahaka a i ʻole kahi mea pilikia wale nō.
Wahi a ka National Organization for Rare Disorder, ʻo ka Sella Syndrome hakahaka e pili ana i nā manawa he ʻehā mau wahine e like me nā kāne. ʻO ka hapa nui o nā wahine me ka maʻi hūnā ʻole e lilo i waena o ka makahiki, obese, a me ke kiʻekiʻe o ke koko. Eia nō naʻe, ʻike ʻole ʻia ka hapa nui o nā maʻi hakahaka o ka Sella Syndrome ma muli o ka nele o nā ʻōuli, no laila paʻakikī e ʻōlelo inā ʻo ke kāne, ke momona, ka makahiki, a i ʻole ke kaomi koko nā mea kūpilikiʻi maoli.
ʻO ka maʻi ʻelua Sella hakahaka
Hiki i nā mea he nui ke kumu i ka maʻi ʻelua o ka Sella Syndrome, e like me:
- hōʻeha poʻo
- maʻi maʻi
- huelo pituitary
- radiation therapy a ʻoki paha ma ka wahi o ka pituitary gland
- nā kūlana e pili ana i ka lolo a i ʻole ka pituitary gland, e like me Sheehan Syndrome, intracranial hypertension, neurosarcoidosis, a hypophysitis
Pehea ia ʻike?
He paʻakikī ke kuhikuhi ʻana i ka maʻi maʻi Empty Sella no ka mea ʻaʻole ia e hana i kekahi mau hōʻailona. Inā manaʻo kāu kauka he loaʻa paha kāu iā lākou, e hoʻomaka lākou me kahi hoʻokolohua kino a me ka loiloi o kāu mōʻaukala olakino. E kauoha paha lākou iā CT scans a i ʻole MRI scans.
E kōkua kēia mau scans i kāu kauka e hoʻoholo inā loaʻa iā ʻoe kahi ʻāpana a hapa paha o ka Sella Syndrome. ʻO ka Syndrome Sella hakahaka hapa ʻole ka liʻiliʻi o kāu sella ma mua o ka hapalua o ka CSF, a ʻo kou pituitary gland he 3 a 7 millimeter (mm) ka manoanoa. ʻO ka nui o ka syndrome sella hakahaka ʻoi aku ka nui ma mua o ka hapalua o kāu sella i piha me CSF, a ʻo kou pituitary gland he 2 mm ka mānoanoa a ʻoi iki paha.
Pehea e mālama ʻia ai?
ʻAʻole koi ka lāʻau Empty sella i ka lāʻau ke ʻole ke hana i nā hōʻailona. Kaukaʻi ʻia i kāu mau ʻōuli, pono ʻoe:
- ʻoki kino e pale aku ai i ka puka ʻana o CSF mai kou ihu
- ka lāʻau, e like me ibuprofen (Advil, Motrin), no ka hōʻeha ʻeha o ke poʻo
Inā loaʻa iā ʻoe ka lua o ka maʻi ʻona Sella hakahaka ma muli o ke ʻano kumu, e nānā ana kāu kauka i ka mālama ʻana i kēlā ʻano a i ʻole ka mālama ʻana i kāna mau ʻōuli.
He aha ke kuanaʻike
Ma kāna iho ponoʻī, ʻaʻohe o nā hōʻailona a me nā hopena maikaʻi ʻole i kāu olakino olakino ma kahi kūʻai Sella hakahaka. Inā loaʻa iā ʻoe ka lua o ka maʻi soma hakahaka lua, e hana pū me kāu kauka e hōʻoia a mālama i ke kumu kumu.