Fistula ʻaʻa Coronary

ʻO ka coristary arist fistula kahi pilina maʻamau ma waena o kekahi o nā aʻa coronary a me kahi keʻena puʻuwai a i ʻole kekahi kīʻaha koko. ʻO nā aʻa coronary nā kīʻaha koko e lawe i ke koko momona i ka puʻuwai.

ʻO ke kumu ʻo Fistula.

ʻO ka fistula artery coronary ka mea hānau pinepine, ʻo ia hoʻi aia ia ma ka wā hānau. Hana ʻia ia ke holo pono ʻole kekahi o nā aʻa coronary. Hana pinepine kēia i ka wā e ulu ana ka pēpē i loko o ka ʻōpū. Hoʻopili ke ākea coronary i kekahi o nā keʻena o ka puʻuwai (ka atrium a i ʻole ventricle) a i ʻole kekahi kīʻaha koko (e laʻa me ka aʻa o ka pulmonary).

Hiki i kekahi fistula artery coronary ke ulu ma hope o ka hānau ʻana. E kumu ʻia e:

• ʻO kahi maʻi e hoʻonāwaliwali ai i ka paia o ke aʻa a me ka puʻuwai
• Kekahi ʻano o ka ʻoki puʻuwai
• Ka hōʻeha i ka puʻuwai mai kahi ulia a ʻoki paha

ʻO ke ʻano ʻaʻano coronary arist fistula kahi ʻano maʻamau. ʻO nā pēpē i hānau ʻia me ia i kekahi manawa he kīnā kīnā ʻole nā ​​naʻau. Pākuʻi ʻia kēia mau mea:

• Hypoplastic hema puʻuwai maʻi (HLHS)
• Pulmonary atresia me ka ventricular septum kōna

ʻAʻohe o nā ʻōpio me kēia ʻano.

Inā kū nā hōʻailona, ​​hiki iā lākou ke hoʻopili:

• Ohumu puuwai
• Hōʻoluʻolu o ka umauma a ʻeha paha
• Ka luhi maʻalahi
• Ka holomua ʻole ʻana
• ʻO ke kuʻi puʻuwai wikiwiki a i ʻole kaulike (palpitations)
• Ka hanu o ka hanu (dyspnea)

I ka hapanui o nā hihia, ʻaʻole ʻike ʻia kēia ʻano a hiki i ke ola hope. Hoʻomaopopo pinepine ʻia i ka wā o nā hoʻokolohua no nā maʻi puʻuwai ʻē aʻe. Eia nō naʻe, lohe paha ka mea mālama ola i kahi ʻōhumu o ka naʻau e alakaʻi ai i ka hōʻailona me ka hoʻāʻo hou ʻana.

ʻO ka hōʻoia nui e hoʻoholo i ka nui o ka fistula kahi angiography coronary. ʻO kēia kahi hoʻāʻo x-ray kūikawā o ka puʻuwai e hoʻohana ana i ka kala e ʻike ai pehea a me kahi e kahe ana ke koko. Hana pinepine ʻia me ka catheterization puʻuwai, e pili ana i ka lawe ʻana i kahi paipu lahilahi i loko o ka puʻuwai e loiloi i ke kaomi a me ke kahe i loko o ka puʻuwai a me nā aʻa a puni.

Hiki i nā hoʻokolohua diagnostical ʻē aʻe ke:

• Ke hōʻike ultrasound o ka puʻuwai (echocardiogram)
• Ke hoʻohana nei i nā mākēneki e hana i nā kiʻi o ka puʻuwai (MRI)
• Nānā CAT o ka puʻuwai

ʻO kahi fistula liʻiliʻi e kū nei i nā hōʻailona pinepine ʻole e pono ka lāʻau. E pani kekahi o nā fistula liʻiliʻi iā lākou iho. ʻO ka pinepine, ʻoiai ʻaʻole lākou e pani, ʻaʻole lākou e hana i nā hōʻailona a pono paha i ka lāʻau.

Pono nā pēpē me kahi fistula nui e ʻoki poepoe e pani i ka pili maʻamau. Hoʻopaʻa ka mea lapaʻau i ka pūnaewele me kahi pā a i ʻole nā ​​kuʻi.

Hoʻopili kahi koho lapaʻau ʻē aʻe i ka wehe me ka ʻole o ke kaha ʻana, e hoʻohana ana i ka uea kūikawā (ʻōwili) i hoʻokomo ʻia i loko o ka puʻuwai me kahi paipu lōʻihi a lahilahi i kapa ʻia he catheter. Ma hope o ke kaʻina hana i nā keiki, pani pinepine ka fistula.

Hana maikaʻi nā kamaliʻi ʻokiʻoki i ka hapanui, ʻoiai pono e hana hou i kahi ʻoki liʻiliʻi. ʻO ka hapa nui o ka poʻe me kēia ʻano he ola maʻamau ko lākou.

Komo pū nā pilikia:

• Rhythm puʻuwai maʻamau (arrhythmia)
• Maʻi hohola
• Hewa puʻuwai
• Wehe (haki) o ka fistula
• Poor oxygen ma ka puʻuwai

ʻOi aku ka maʻalahi o nā pilikia i ka poʻe kahiko.

Hoʻomaopopo pinepine ʻia ka fistula arter Coronary i ka wā o kahi hoʻokolohua e kāu mea hāʻawi. Kāhea i kāu mea hāʻawi inā loaʻa kāu pēpē i nā ʻōuli o kēia ʻano.

ʻAʻohe ala i ʻike ʻia e pale ai i kēia ʻano.

Hōʻino puʻuwai Congenital - coristary artery fistula; Naʻau kīnā hānau - fistula arter coronary

• Angiography Coronary
• Fistula ʻaʻa Coronary

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