Mea Kākau: Joan Hall
Lā O Ka Hana: 28 Pepeluali 2021
HōʻAno Hou I Ka Lā: 27 Kepakemapa 2024
Anonim
Rhabdomyosarcoma (RMS) - Mayo Clinic
Wikiō: Rhabdomyosarcoma (RMS) - Mayo Clinic

ʻO Rhabdomyosarcoma kahi maʻi ʻaʻai (malignant) o nā mākala e pili ana i nā iwi. Hoʻopili kēia maʻi ʻaʻai i nā keiki.

Hiki i ka Rhabdomyosarcoma ma nā wahi he nui i ke kino. ʻO nā pūnaewele maʻamau ka poʻo a me ka ʻāʻī, ka urinary a i ʻole reproductive system, a me nā lima a me nā wāwae.

ʻAʻole ʻike ʻia ke kumu o ka rhabdomyosarcoma. He tumo laha ʻole ia me nā haneli hou he nui i kēlā me kēia makahiki i ka United States.

ʻO kekahi mau keiki me kahi mau hānau hānau i ka nui o ka makaʻu. Loaʻa i kekahi mau ʻohana kahi hoʻololi mutina e hoʻonui ai i kēia pilikia. ʻO ka hapa nui o nā keiki me ka rhabdomyosarcoma ʻaʻohe mea i ʻike ʻia i nā pilikia pilikia.

ʻO ka hōʻailona maʻamau ka nui o ka nui a ʻeha paha.

Hoʻololi nā ʻōuli ʻē aʻe i ka wahi o ka tumo.

  • Hiki i nā tumors i ka ihu a i ʻole ka puʻu ke kumu i ke kahe ʻana o ke koko, ka pīhoihoi, ka ale ʻana i nā pilikia, a i ʻole nā ​​pilikia ʻōnaehana inā hele lākou i ka lolo.
  • Hiki i nā tumors a puni nā maka ke hoʻonā i ka maka o ka maka, nā pilikia me ka ʻike, ka pehu ʻana a puni ka maka, a me ka ʻeha.
  • ʻO nā tumors i loko o nā pepeiao, hiki ke hana i ka ʻeha, ka nalo ʻana o ka lohe, a i ʻole ka pehu.
  • Hiki i nā ʻōpū a me nā puʻupuʻu wahine ke hoʻopilikia i ka hoʻomaka ʻana e mimiki a i ʻole ke neʻe ʻana o ka ʻōpū, ai ʻole ka maikaʻi ʻole o ka mimi.
  • Hiki i nā tumo muscle ke alakaʻi i kahi puʻupuʻu ʻeha, a hiki ke kuhihewa ʻia no kahi ʻeha.

Hoʻolālā pinepine ka loiloi no ka mea ʻaʻohe hōʻailona a no ka mea e ʻike ʻia ka tumo i ka manawa like me kahi ʻeha i hala iho nei. He mea nui ka ʻike mua no ka laha koke ʻana o kēia maʻi ʻaʻai.


E hana ka mea mālama ola i kahi hoʻokolohua kino. E nīnau ʻia nā nīnau kikoʻī e pili ana i nā ʻōuli a me ka mōʻaukala olakino.

ʻO nā hoʻokolohua i kauoha ʻia e komo pū:

  • Pākuʻi x-ray
  • CT scan o ka umauma e nānā no ka hoʻolaha ʻana o ka tumo
  • CT scan o ka pūnaewele tumora
  • ʻO ka biopsy iwi iwi (e hōʻike paha ua pālahalaha ʻia ka maʻi ʻaʻai)
  • ʻImi iwi e nānā no ka hoʻolaha ʻana o ka tumo
  • MRI scan o ka pūnaewele hikoko
  • Spinal tap (lumbar puncture)

Pili ka mālama ʻana i ka pūnaewele a me ke ʻano o ka rhabdomyosarcoma.

E hoʻohana ʻia i kekahi radiation a chemotherapy paha, a i ʻole ʻelua, ma mua a ma hope paha o ke kaha. Ma ka laulā, hoʻohana ʻia ke kīʻaha a me ka radiation radiation e mālama i ka pūnaewele mua o ka tumo. Hoʻohana ʻia ʻo Chemotherapy e mālama i nā maʻi ma nā pūnaewele āpau i ke kino.

ʻO Chemotherapy kahi ʻāpana nui o ka mālama ʻana e pale ai i ka hoʻolaha ʻana a me ka hoʻi hou ʻana o ka maʻi ʻaʻai. Ke hana nei nā lāʻau chemotherapy he nui e kū'ē i ka rhabdomyosarcoma. E kūkākūkā kāu mea lawelawe i kēia mau mea me ʻoe.

Hiki ke hōʻemi ʻia ke koʻikoʻi o ka maʻi ma ke komo ʻana i kahi hui kākoʻo maʻi ʻaʻai. ʻO ke kaʻana ʻana me nā poʻe ʻē aʻe i loaʻa nā ʻike a me nā pilikia maʻamau e hiki ke kōkua iā ʻoe e noʻonoʻo ʻole.


Me ka mālama nui ʻana, hiki i ka hapanui o nā keiki me ka rhabdomyosarcoma ke ola i ka wā lōʻihi. Pili ka hoʻōla i ke ʻano kikoʻī o ka tumo, kona wahi, a me ka nui o ia pālahalaha ʻana.

ʻO nā pilikia o kēia maʻi ʻaʻai a i ʻole kāna mālama ʻana:

  • Nā pilikia mai chemotherapy
  • Kahi e hiki ʻole ai ke ʻoki kino
  • Ka hohola ʻana o ka maʻi ʻaʻai (metastasis)

Kāhea i kāu mea hāʻawi inā loaʻa kāu keiki i nā ʻōuli o ka rhabdomyosarcoma.

Maʻi ʻaʻai palupalu - rhabdomyosarcoma; Sarkoma palupalu; Alveolar rhabdomyosarcoma; Embryonal rhabdomyosarcoma; ʻO Sarcoma botryoides

ʻO Dome JS, Rodriguez-Galindo C, Spunt SL, Santana VM. Nā Tumors paʻa pediatric. I: Niederhuber JE, Armitage JO, Kastan MB, Doroshow JH, Tepper JE, eds. ʻO Oncology Clinical ʻo Abboff. ʻElua huaʻōlelo Piladelapia, PA: Elsevier; 2020: chap 92.

ʻO Goldblum JR, Folpe AL, Weiss SW. Rhabdomyosarcoma. I: Goldblum JR, Folpe AL, Weiss SW, eds. ʻO nā Tumors Tissue Palupalu ʻo Enzinger a me Weiss. ʻEpekema 7 Piladelapia, PA: Elsevier; 2020: chap 19.


Pūnaewele ʻo National Cancer Institute. ʻO ka mālama ʻana i ka ʻoihana rhabdomyosarcoma ʻōpio (PDQ). www.cancer.gov/types/soft-tissue-sarcoma/hp/rhabdomyosarcoma-treatment-pdq. Hoʻohou ʻia Mei 7, 2020. Loaʻa iā Iulai 23, 2020.

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