Potter maʻi maʻi

ʻO Potter Syndrome a me Potter phenotype e pili ana i kahi hui o nā hopena i pili me ka nele o ka wai amniotic a me ke kō ʻole o ke kīhāpai i kahi pēpē i hānau ʻole ʻia.

I ka maʻi Potter, ʻo ka pilikia mua ʻole o ka hakuʻala. ʻAʻole hiki i nā puʻupaʻa ke ulu kūpono i ka ulu ʻana o ka pēpē i loko o ka ʻōpū. Hoʻopuka maʻamau nā puʻupaʻa i ka wai amniotic (e like me ka mimi).

ʻO ka potter phenotype e pili ana i kahi helehelena hiʻohiʻona i kū i loko o kahi keiki hānau ke ʻole kahi wai amniotic. ʻO ka nele o ka wai amniotic i kapa ʻia ʻo oligohiddramnios. Me ka ʻole o ka wai amniotic, ʻaʻole cushioned ka pēpē mai nā paia o ka kōpū. ʻO ke kaomi o ka paia uterine e alakaʻi aku ai i kahi helehelena helehelena ʻokoʻa, me nā maka kaawale ākea.

Hiki i ka phenter potter ke alakaʻi i nā lālā kūpono ʻole, a i ʻole nā ​​lālā i paʻa i nā kūlana kūpono ʻole a me nā kuʻikahi.

Hoʻopau pū ʻo Oligioxidamnios i ka hoʻomohala ʻana o nā māmā, no laila ʻaʻole holo pono nā māmā i ka wā hānau.

ʻO nā hōʻailona me:

• Hoʻokaʻawale ʻia nā maka me nā pelu epicanthal, ke alahaka ihu ākea, nā pepeiao hoʻohaʻahaʻa haʻahaʻa, a me ka auwae e hemo ana
• Loaʻa ʻole o ka puka mimi
• Hanu paʻakikī

Hiki paha i kahi ultrasound hāpai ke hōʻike i ka nele o ka wai amniotic, ka ʻole o nā puʻupaʻa fetal, a i ʻole nā ​​puʻupaʻa koʻikoʻi ʻole i ka pēpē i hānau ʻole ʻia.

Hiki ke hoʻohana ʻia nā hoʻokolohua e hiki ai ke kōkua i ke kuhi ʻana i ke ʻano o ka hānau hou.

• X-ray o ka ʻōpū
• X-kukuna o nā māmā

Hiki ke hoʻāʻo ʻia ka hoʻōla hou ʻana ma ka lawe ʻana e kali ana i ke kuhi. E hoʻolako ʻia ka mālama ʻana no kekahi mea ākea o ka urinary.

He kūlana koʻikoʻi loa kēia. ʻO ka hapanui o ka manawa he make ia. ʻO ka hopena pōkole e pili ana i ka paʻakikī o ke komo ʻana o ka lung. ʻO ka hopena lōʻihi e pili ana i ka paʻakikī o ke komo ʻana o ka puʻupaʻa.

ʻAʻohe pale e ʻike ʻia.

ʻO ka phenotype Potter

• Wai Amniotic
• Alahaka ihu ākea

ʻO Joyce E, ʻo Ellis D, ʻo Miyashita Y. Nefetrology. I: Zitelli BJ, McIntire SC, Nowalk AJ, eds. ʻO Zitelli lāua ʻo Davis 'Atlas o ka Pediatric Physical Diagnosis. ʻEpekema 7 Piladelapia, PA: Elsevier; 2018: chap 14.

Marcdante KJ, Kliegman RM. Congenital a me ka developmental abnormalities o ka urinary tract. I: Marcdante KJ, Kliegman RM, hua. Nā Pono Nui o Pediatrics. 8th ed. Piladelapia, PA: Elsevier; 2019: chap 168.

Mitchell AL. ʻO nā anomalies kūpona. I: Martin RJ, Fanaroff AA, Walsh MC, hua. ʻO Fanaroff lāua ʻo Martin's Neonatal-Perinatal Medicine. 11th hua. Piladelapia, PA: Elsevier; 2020: chap 30.