Hoʻi ka huakaʻi anomaly pulmonary venous

ʻO ka huina hoʻi anomaly pulmonary venous return (TAPVR) kahi maʻi puʻuwai kahi e hoʻopili ʻole ai nā ʻehā i lawe i ke koko mai nā akemāmā i ka puʻuwai i ka atrium hema (keena hema o ka puʻuwai Akā, hoʻopili lākou i kekahi kīʻaha koko a i ʻole ʻāpana hewa o ka puʻuwai. Aia ia i ka wā hānau (maʻi puʻuwai congenital).

ʻO ke kumu o ka hoʻi anomaly pulmonary venous hoʻi ʻaʻole ʻike ʻia.

I ka holo maʻamau, hoʻouna ʻia ke koko mai ka ventricle ʻākau e kiʻi i ka oxygen ma nā akemāmā. Hoʻi ia ma o nā uaua pulmonary (lung) i ka ʻaoʻao hema o ka puʻuwai, e hoʻouna ai i ke koko ma o ka aorta a puni ke kino.

I ka TAPVR, hoʻi ke koko momona o ka oxygen mai nā akemāmā i ka atrium ʻākau a i kahi aa koko e kahe ana i ka atrium ʻākau, ma kahi o ka ʻaoʻao hema o ka puʻuwai. I nā huaʻōlelo ʻē, pōʻai wale ke koko i a mai nā māmā a ʻaʻole loa e hele i waho i ke kino.

No ke keiki e ola, kahi hemahema septial atrial (ASD) a i ʻole ovary foramen ovale (ke hele i waena o ka atria hema a me ka ʻākau) pono e ʻae i ke kahe oxygenated e kahe i ka ʻaoʻao hema o ka puʻuwai a me ke koena o ke kino.

Aia ke kaumaha o kēia ʻano ma muli o ka ālai a ālai ʻia paha o nā uaua pulmonary i ka wā e kahe ai lākou. Hoʻopilikia ʻia ʻo TAPVR i nā ʻōuli i ke ola a hiki ke lilo i mea make loa inā ʻaʻole i loaʻa a hoʻoponopono ʻia me ke ʻoki.

ʻIke paha ke pēpē i ka maʻi nui a loaʻa paha i kēia mau ʻōuli:

• ʻO kaʻula Bluish o kaʻili (cyanosis)
• ʻO nā maʻi hanu pinepine
• Lethargy
• ʻAi hānai maikaʻi ʻole
• Piʻi maikaʻi ʻole
• Hanu wikiwiki

Kaha: i kekahi manawa, ʻaʻohe o nā ʻōuli i ka wā pēpē a i ʻole ke keiki kamaliʻi.

E komo pū paha nā hoʻāʻo:

• Hiki i ka catheterization cardiac ke hōʻoia i ka hōʻailona ma o ka hōʻike ʻana e pili pono ʻole nā ​​kīʻaha koko
• Hōʻike ka ECG i ka hoʻonui ʻana o nā ventricle (hypertrophy ventricular)
• Hōʻike paha ʻo Echocardiogram i ka hoʻopili ʻia o nā moku pulmonary
• Hiki i ka MRI a i ʻole CT scan o ka puʻuwai ke hōʻike i nā pilina ma waena o nā moku pulmonary
• Hōʻike ka X-ray o ka umauma i kahi maʻamau i ka puʻuwai liʻiliʻi me ka wai i nā akemāmā

Pono ke ʻoki kino e hoʻoponopono i ka pilikia i ka wā hiki loa. I ke kahakaha ʻana, pili nā uaua pulmonary i ka atrium hema a pani ʻia ka hemahema ma waena o ka atrium ʻākau a me ka hema.

Inā mālama ʻole ʻia kēia ʻano, e nui ana ka naʻau, e alakaʻi ana i ka holo pono ʻole o ka naʻau. ʻO ka hoʻoponopono ʻana i ka hemahema i ka wā mua e hāʻawi i nā hopena maikaʻi inā ʻaʻohe paʻa o nā uaua pulmonary i ka pili hou i ka puʻuwai. ʻO nā pēpē nāna i ālai i nā uaua i hōʻemi i ke ola.

Komo pū nā pilikia:

• Nā pilikia hanu
• Hewa puʻuwai
• Hewa, wikiwiki nā puʻuwai puʻuwai (arrhythmia)
• Nā maʻi lele
• Hypertension pulmonary

ʻIke paha kēia ʻano i ka manawa hānau. Eia nō naʻe, ʻaʻole e loaʻa nā ʻōuli a ma hope.

Kāhea i kāu mea mālama ola inā ʻike ʻoe i nā ʻōuli o TAPVR. Koi ʻia ka nānā koke.

ʻAʻohe ala i ʻike ʻia e pale aku ai iā TAPVR.

TAPVR; Huina veins; Hewa naʻau Congenital - TAPVR; ʻO ka maʻi puʻuwai cyanotic - TAPVR

• Puʻuwai - ʻāpana ma waena o ka waena
• ʻO ka hoʻi hou ʻana i anomous pulmonary venous pulmonary - X-ray
• ʻO ka hoʻi anomaly pulmonary venous hoʻi - x-ray
• ʻO ka hoʻi hou ʻana i anomous pulmonary venous pulmonary - X-ray

Fraser CD, Kane LC. Maʻi maʻi ʻōpū. I: Townsend CM Jr, Beauchamp RD, Evers BM, Mattox KL, eds. ʻO Sabiston Textbook of Surgery: Ke kumu kumu olaola o ka hana ʻoki ʻana o kēia ao. 20 ouk. Piladelapia, PA: Elsevier; 2017: chap 58.

Webb GD, Smallhorn JF, Therrien J, Redington AN. ʻO ka maʻi puʻuwai Congenital i ke kanaka makua a me ka mea maʻi pediatric. I: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. ʻO ka maʻi puʻuwai ʻo Braunwald: He puke aʻo no ka lāʻau Cardiovascular. 11th hua. Piladelapia, PA: Elsevier; 2019: chap 75.