ʻO ka maʻi Hemoglobin C

ʻO ka maʻi Hemoglobin C kahi maʻi koko i iho ʻia i waena o nā ʻohana. Ke alakaʻi ia i kahi ʻano anemia, e hana ʻia ke wā e wāwahi ai nā hunaola ʻulaʻula ma mua o ka maʻamau.
He hemoglobin C kekahi ʻano hemoglobin, ka protein i loko o nā hunaola ʻulaʻula e lawe ana i ka oxygen. He ʻano hemoglobinopathy. Hoʻokumu ʻia ka maʻi e kahi pilikia me kahi gen i kapa ʻia ʻo beta globin.
Kū pinepine ka maʻi i ʻAmelika ʻAmelika. Loaʻa paha iā ʻoe ka maʻi hemoglobin C inā i loaʻa i kekahi o kou ʻohana.
ʻAʻohe o ka hapanui o ka poʻe. I kekahi mau hihia, hiki i ka jaundice ke kū. Hoʻokumu paha kekahi poʻe i nā pōhaku e pono e mālama ʻia.
Hōʻike kahi hoʻokolohua kino i kahi lōlō hoʻonui.
ʻO nā hoʻāʻo e hana ʻia ana paha:
- Helu piha koko
- Electrogoresis Hemoglobin
- Poni i ke koko peripheral
- Hemoglobin koko
I ka hapanui o nā hihia, ʻaʻohe pono e pono ai. Hiki i nā mea kōkua Folic acid ke kōkua i kou kino e hana i nā hunaola ʻulaʻula maʻamau a hoʻomaikaʻi i nā hōʻailona o ka anemia.
Hiki i nā poʻe me ka maʻi hemoglobin C ke manaʻo e alakaʻi i kahi ola maʻamau.
Komo pū nā pilikia:
- Anemia
- Maʻi maʻi gallbladder
- Hoʻonui o ka pākī
Kāhea i kāu kauka lawelawe inā loaʻa nā ʻōuli o ka maʻi hemoglobin C.
Makemake paha ʻoe e ʻimi i nā ʻōlelo aʻoaʻo kūpuna inā nui kou makaʻu no ka maʻi a ke noʻonoʻo nei i ka loaʻa ʻana o kahi pēpē.
Hemoglobin maʻi C
Nā pūnaewele koko
ʻO Howard J. Sickle cell maʻi a me nā hemoglobinopathies ʻē aʻe. I: Goldman L, Schafer AI, eds. ʻO ka lāʻau lapaʻau Goldman-Cecil. 26th ed. Piladelapia, PA: Elsevier; 2020: chap 154.
Smith-Whitley K, Kwiatkowski JL. Hemoglobinopathies. I: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. ʻO Puka Textbook of Pediatrics ʻo Nelson. 21st ed. Piladelapia, PA: Elsevier; 2020: chap 489.
ʻO Wilson CS, Vergara-Lluri ME, ʻo Brynes RK. ʻO ka loiloi o anemia, leukopenia, a me thrombositopenia. I: Jaffe ES, Arber DA, Campo E, Harris NL, Quintanilla-Martinez L, huaʻi. Hematopathology. ʻElua ed. Piladelapia, PA: Elsevier; 2017: chap 11.