ʻO ka cardiomyopathy kaohi

ʻO ka cardiomyopathy kaohi e pili ana i kahi o nā loli i ka hana o ka puʻuwai puʻuwai. Hoʻopili kēia mau hoʻololi i ka puʻuwai e hoʻopihapiha maikaʻi ʻole (ʻoi aku ka maʻamau) a i ʻole kaomi ʻino ʻana (ʻoi aku ka liʻiliʻi). I kekahi manawa, aia nā pilikia ʻelua.

I kahi hihia o ka cardiomyopathy kaohi, ʻo ka mākala puʻuwai he nui maʻamau a hoʻonui iki ʻia paha. ʻO ka hapanui o ka manawa, pump hoʻi maʻamau ia. Eia naʻe, ʻaʻole ia e hoʻomaha maʻamau i ka manawa ma waena o nā puʻuwai puʻuwai ke hoʻi mai ke koko mai ke kino (diastole).

ʻOiai ʻo ka pilikia nui ka hoʻopiha ʻole o ka puʻuwai, ʻaʻole paha e puʻuwai ka puʻuwai i ke koko ke holo ka maʻi. Hiki i ka hana puʻuwai maʻamau ke hoʻololi i nā māmā, ke ake, a me nā ʻōnaehana o ke kino. Hoʻopilikia ka cardiomyopathy kaohi i kekahi a i ʻole o nā keʻena puʻuwai o lalo (ventricles). ʻO ka cardiomyopathy kaohi ʻia he ʻano laha ʻole. ʻO nā kumu maʻamau ka amyloidosis a me ka scarring o ka puʻuwai mai kahi kumu ʻike ʻole ʻia. Hiki iā ia ke hana ma hope o ke kuʻi puʻuwai.

Nā kumu ʻē aʻe o ka hoʻopaʻi ʻana i ka cardiomyopathy me:

• Amyloidosis Cardiac
• Maʻi maʻi puʻuwai Carcinoid
• Nā maʻi o ka naʻau i uhi ʻia (endocardium), e like me endomyocardial fibrosis a me Loeffler Syndrome (kākaʻikahi)
• ʻO ka hoʻouka hao (hemochromatosis)
• ʻO Sarcoidosis
• Scarring ma hope o radiation a chemotherapy paha
• Scleroderma
• Tumors o ka puʻuwai

ʻO nā ʻōuli o ka hake ʻole o ka puʻuwai ka mea maʻamau. Hoʻolālā mālie kēia mau ʻōuli ma mua o ka manawa.Eia naʻe, hoʻomaka koke nā ʻōuli i kekahi manawa a ʻino loa.

ʻO nā ʻōuli maʻamau ka:

• Cough
• Nā pilikia hanu e hana ʻia i ka pō, me ka hana a i ʻole ke moe pālahalaha ʻana
• Ka luhi a me ka hiki ʻole ke hoʻoikaika kino
• Loaʻa ka ʻai ʻole
• Pehu o ka ʻōpū
• ʻO ka pehu ʻana o nā wāwae a me nā kuʻekuʻe wāwae
• Pākuʻi kūpono ʻole a wikiwiki paha

Hiki i nā ʻōuli ʻē aʻe ke:

• ʻEha ʻeha
• ʻAʻole hiki ke noʻonoʻo
• Puka mimi haʻahaʻa
• Pono e mimiki i ka pō (i nā mākua)

E hōʻike paha kahi hōʻike kino:

• Hoʻonui (distaced) a i ʻole ʻūlū i nā ʻāʻī o ka ʻāʻī
• Ake akea
• Lele nā ​​crackle a me nā puʻuwai maikaʻi ʻole a mamao paha i ka umauma i lohe ʻia ma o kahi stethoscope
• Pākuʻi wai i nā lima a me nā wāwae
• Nā hōʻailona o ka puʻuwai puʻuwai

ʻO nā hoʻāʻo no ka hoʻopaʻi ʻana i ka cardiomyopathy me:

• ʻO ka catheterization Cardiac a me ka angiography coronary
• Scanner CT pahu
• Pākuʻi x-ray
• ECG (electrocardiogram)
• Ke aʻo ʻana ʻo Echocardiogram a me Doppler
• MRI o ka puʻuwai
• Nānā puʻuwai nuklear (MUGA, RNV)
• Nā hoʻopaʻa naʻau serum
• Nā hoʻāʻo a me ka mimi protein protein

Hiki ke ʻano like ka cardiomyopathy kaohi me ka pericarditis constrictive. Hiki paha i ka catheterization cardiac ke kōkua i ka hōʻoia ʻana i ka hōʻailona. ʻAno ʻole, koi ʻia kahi biopsy o ka puʻuwai.

Mālama ʻia ke ʻano o ka maʻi i hiki ke loaʻa.

ʻIke ʻia nā hana liʻiliʻi e hana maikaʻi no ka hoʻopili ʻana i ka cardiomyopathy. ʻO ka pahuhopu nui o ka mālama ʻana e kaohi i nā ʻōuli a hoʻomaikaʻi i ka maikaʻi o ke ola.

Hiki ke hoʻohana ʻia nā ʻano mālama aʻe e kaohi ai i nā ʻōuli a i ʻole ke pale ʻana i nā pilikia.

• Nā lāʻau hoʻomā lahilahi ke koko
• Chemotherapy (i kekahi mau hanana)
• Hoʻopau nā diuretics i ka wai a kōkua i ka hoʻomaikaʻi ʻana i ka hanu
• Nā lāʻau lapaʻau e pale a kāohi paha i nā mele puʻuwai maikaʻi ʻole
• ʻO Steroids a chemotherapy paha no kekahi kumu

E noʻonoʻo ʻia kahi hoʻoliʻiliʻi puʻuwai inā ʻilihuna loa ka naʻau a koʻikoʻi loa nā ʻōuli.

ʻO ka poʻe me kēia ʻano e hoʻomōhala pinepine i ka puʻuwai puʻuwai e ʻoi aku ka maikaʻi. ʻO nā pilikia me ka puʻuwai puʻuwai a i ʻole nā ​​lepe puʻuwai "leaky" e kū pū kekahi.

ʻO ka poʻe me ka cardiomyopathy kaohi paha he mau moho transplant puʻuwai. Aia ka nānā i ke kumu o ke ʻano, akā ʻilihune maʻamau ia. ʻO ke ola ma hope o ka hōʻoia ʻana ma mua o 10 mau makahiki.

Kāhea i kāu mea mālama ola inā loaʻa iā ʻoe nā ʻōuli o ka cardiomyopathy kaohi.

Cardiomyopathy - kaohi; Infiltrative cardiomyopathy; Idiopathic myocardial fibrosis

• Puʻuwai - ʻāpana ma waena o ka waena
• Puʻuwai - ʻike mua

Falk RH, Hershberger RE. ʻO nā cardiomyopathies i hoʻonui ʻia, kaohi ʻia, a me nā infiltrative. I: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. ʻO ka maʻi puʻuwai ʻo Braunwald: He puke aʻo no ka lāʻau Cardiovascular. 11th hua. Piladelapia, PA: Elsevier; 2019: chap 77.

McKenna WJ, Elliott PM. Nā maʻi o ka myocardium a me ka endocardium. I: Goldman L, Schafer AI, eds. ʻO ka lāʻau lapaʻau Goldman-Cecil. 26th ed. Piladelapia, PA: Elsevier; 2020: chap 54.