Wiskott-Aldrich maʻi

Anter

• Nā ʻōuli o Wiskott-Aldrich Syndrome
• Hoʻomaʻo no Wiskott-Aldrich Syndrome

ʻO Wiskott-Aldrich Syndrome kahi maʻi maʻi, ka mea e hoʻopilikia ai i ka ʻōnaehana pale maʻi e pili ana i nā T a me nā lymphocytes, a me nā aʻa koko e kōkua ai i ka kaohi ʻana i ke kahe ʻana, nā platelet.

Nā ʻōuli o Wiskott-Aldrich Syndrome

ʻO nā ʻōuli o wiskott-Aldrich Syndrome hiki ke:

ʻO ka maʻamau i ke kahe ʻana:

• Hoʻemi ʻia ka helu a me ka nui o nā platelet i loko o ke koko;
• ʻO nā hemorrhages cutaneity i ʻike ʻia e nā kiko ʻulaʻula-polū i ka nui o ke poʻo pin, i kapa ʻia ʻo "petechiae", a i ʻole ʻoi aku ka nui a like paha me nā ʻeha;
• Nā noho koko (keu hoʻi i ka wā kamaliʻi), nā hāwele koko a me nā ihu lōʻihi.

ʻO nā maʻi pinepine pinepine ʻia e nā ʻano microorganism e like me:

• Mediaitis Otitis, sinusitis, pulumonia;
• ʻO Meningitis, pulumonia i hoʻokumu ʻia e Pneumocystis jiroveci;
• ʻO ka maʻi ʻili Viral i hoʻokumu ʻia e molluscum contagiosum.

Eczema:

• Nā maʻi pinepine o ka ʻili;
• Nā kiko ʻeleʻele i ka ʻili.

Nā hōʻike a Autoimmune:

• Vasculitis;
• Hemolytic anemia;
• Idiopathic thrombocytopenic purpura.

ʻO ke kuhi no kēia maʻi hiki ke hana ʻia e ka pediatrician ma hope o ka nānā pono ʻana i nā ʻōuli a me nā hoʻokolohua kikoʻī. ʻO ka loiloi i ka nui o nā platelet kekahi o nā ala e hōʻoia ai i ka maʻi, ʻoiai he kakaikahi nā maʻi i loaʻa kēia ʻano.

Hoʻomaʻo no Wiskott-Aldrich Syndrome

ʻO ka lapaʻau kūpono loa no ka Wiskott-Aldrich syndrome ka hoʻoneʻe iwi o ka iwi. ʻO nā ʻano lapaʻau ʻē aʻe ka hemo ʻana o ka pelepelu, no ka mea, luku kēia ʻōpū i ka liʻiliʻi o nā platelet i loaʻa i ka poʻe me kēia maʻi, ka hoʻohana ʻana o hemoglobin a me ka hoʻohana ʻana i nā lāʻau ʻaloʻalo.

ʻO ke kali ola no nā poʻe me kēia maʻi he haʻahaʻa, ʻo ka poʻe i ola ma hope o ka makahiki he ʻumi e hoʻomohala pinepine i nā tumors e like me lymphoma a me leukemia.