Nā Hōʻike Porphyrin

Anter

• He aha nā hōʻike porphyrin?
• No ke aha lākou e hoʻohana ai?
• No ke aha e pono ai iaʻu kahi hōʻike porphyrin?
• He aha ka hana i ka wā o ka hoʻāʻo porphyrin?
• Pono wau e hana i kekahi mea e hoʻomākaukau ai no ka hoʻāʻo?
• Aia kekahi mau pōpilikia i nā hōʻike porphyrin?
• He aha ke ʻano o nā hopena?
• Aia kekahi mea ʻē aʻe e pono iaʻu e ʻike e pili ana i nā hōʻike porphyrin?
• Nā kūmole

He aha nā hōʻike porphyrin?

Ana nā ana ʻo porphyrin i ke kiʻekiʻe o nā porphyrins i loko o kou koko, mimi, a i ʻole ka noho. ʻO Porphyrins nā kemika e kōkua i ka hana ʻana i ka hemoglobin, kahi ʻano protein i loko o kou mau ʻulaʻula. Hāpai ʻo Hemoglobin i ka oxygen mai kou mau māmā a i ke koena o kou kino.

He mea maʻamau ka loaʻa ʻana o kahi liʻiliʻi o nā porphyrins i kou koko a me nā wai o ke kino ʻē aʻe. Akā ʻo ka nui o ka porphyrin paha ka manaʻo he ʻano porphyria kāu. ʻO Porphyria kahi maʻi laha ʻole i hiki ke hoʻopilikia i nā pilikia olakino koʻikoʻi. Māhele mau ʻia ʻo Porphyria i ʻelua mau ʻāpana:

• ʻO nā porphyrias koʻikoʻi, ka mea nui e hoʻopili i ka ʻōnaehana hopohopo a hoʻokumu i nā ʻōpū o ka ʻōpū
• ʻO nā porphyrias kūkani, ke kumu o nā ʻōuli o ka ʻili ke hōʻike ʻia ʻoe i ka lā

Hoʻopili kekahi mau porphyrias i ka ʻōnaehana hopohopo a me ka ʻili.

Nā inoa ʻē aʻe: protoporphyrin; protoporphyrin, koko; protoporhyrin, noho noho; porphyrins, nāhelehele; uroporphyrin; porphyrins, mimi; Hōʻike Mauzerall-Granick; ʻakika; ALA; porphobilinogen; PBG; protoporphyrin erythrocyte manuahi; porphyrins erythrocyte hakina; FEP

No ke aha lākou e hoʻohana ai?

Hoʻohana ʻia nā hoʻokolohua porphyrin e hōʻoia a nānā i ka porphyria.

No ke aha e pono ai iaʻu kahi hōʻike porphyrin?

Pono ʻoe i kahi hōʻike porphyrin inā loaʻa iā ʻoe nā ʻōuli o ka porphyria. Aia nā ʻōuli ʻokoʻa no nā ʻano like ʻole o ka porphyria.

ʻO nā ʻōuli o ka porphyria huehue e komo pū me:

• Abdominal eha
• Konipōpō
• ʻO Nusea a me ka luaʻi
• Mimi ʻulaʻula a ʻeleʻele paha
• Tingling a ʻeha paha ma nā lima a me / a i ʻole nā ​​wāwae
• Nāwaliwali ka ʻiʻo
• Huikau
• Nā Haleluʻa

ʻO nā ʻōuli o ka porphyria cutaneous e komo pū me:

• Oversensitivity i ka lā
• Pā i ka ʻili i kū i ka lā
• ʻO kaʻulaʻula a me ka pehu ʻana o ka ʻili ku waho
• Kāwili
• Hoʻololi i ke kala o ka ʻili

Pono paha ʻoe i kahi hōʻike porphyrin inā loaʻa i kekahi o kou ʻohana porphyria. ʻO ka hapa nui o nā ʻano porphyria i hoʻoili ʻia, ʻo ia hoʻi ua hala ke ʻano mai ka makua a ke keiki.

He aha ka hana i ka wā o ka hoʻāʻo porphyrin?

Hiki ke hoʻāʻo ʻia nā porphyrins i ke koko, mimi, a i ʻole ka noho. ʻO nā ʻano maʻamau o nā hōʻike porphyrin e helu ʻia ma lalo.

• Hōʻike Koko
  • E lawe kahi ʻoihana mālama ola i kahi laʻana koko mai kahi aa i kou lima, e hoʻohana ana i kahi nila kuʻikuʻi. Ma hope o ka hoʻokomo ʻia ʻana o ka nila, e hōʻiliʻili ʻia kahi koko liʻiliʻi i loko o kahi pahu hoʻāʻo a ipu paha. Hiki paha iā ʻoe ke ʻoni iki i ka wā e hele ai a kuʻi paha ka nila. Lōʻihi kēia ma mua o ʻelima mau minuke.
• Laʻana Urine 24-Hour
  • E hōʻiliʻili ʻoe i kāu mimi āpau ma kahi o 24 mau hola. No kēia hōʻoia, e hāʻawi aku kāu mea mālama ola a i ʻole ke keʻena hoʻokolohua iā ʻoe i kahi ipu a me nā ʻikepili kikoʻī e pili ana i ka hōʻiliʻili ʻana i kāu mau hōʻailona ma ka home E mālama pono i nā ʻōkuhi āpau. Hoʻohana ʻia kēia hōʻike hāpana 24-hola no ka mea o ka nui o nā mea i loko o ka mimi, me ka porphyrin, hiki ke loli i ka lā holoʻokoʻa. No laila ʻo ka hōʻiliʻili ʻana i kekahi mau laʻana i ka lā e hāʻawi i kahi kiʻi ʻoi aku ka pololei o kāu ʻike mimi.
• Hōʻike Urine Random
  • Hiki iā ʻoe ke hoʻolako i kāu hāpana i kēlā me kēia manawa o ka lā, me ka ʻole o ka hoʻomākaukau kūikawā a me ka lawelawe ʻana i pono. Hana pinepine ʻia kēia hōʻike ma kahi keʻena ʻoihana mālama olakino a i kahi lab.
• ʻO Stool Test (i kapa ʻia ʻo protoporphyrin i ka noho.
  • E hōʻiliʻili ʻoe i kahi laʻana o kāu pahu a waiho i loko o kahi pahu kūikawā. E hāʻawi aku kāu mea mālama ola iā ʻoe i nā ʻōkuhi pehea e hoʻomākaukau ai i kāu hāpana a hoʻouna iā ia i kahi lab.

Pono wau e hana i kekahi mea e hoʻomākaukau ai no ka hoʻāʻo?

ʻAʻole pono ʻoe i kahi hoʻomākaukau kūikawā no nā hoʻokolohua koko a mimi paha.

No kahi hōʻike stool, kauoha ʻia ʻoe e ʻai ʻole i ka ʻiʻo a i ʻole lawe i kekahi lāʻau i loaʻa i ka aspirin no ʻekolu mau lā ma mua o kāu hōʻike.

Aia kekahi mau pōpilikia i nā hōʻike porphyrin?

ʻAʻohe liʻiliʻi loa i ka hōʻoia ʻana o ke koko. Loaʻa paha iā ʻoe ka ʻeha a ʻeha paha ma kahi o ka nila i hoʻokomo ʻia ai, akā ʻo ka hapa nui o nā ʻōuli e hele wikiwiki aku.

ʻAʻohe hopohopo i ʻike ʻia i ka mimi a i ʻole nā ​​hōʻaihue.

He aha ke ʻano o nā hopena?

Inā loaʻa nā pae kiʻekiʻe o ka porphyrin i kou koko, mimi, a i ʻole ka noho, e kauoha paha kāu mea mālama mālama ola i nā hoʻokolohua hou aku e hōʻoia i kahi hōʻailona a e ʻike i ke ʻano o ka porphyria āu. ʻOiai ʻaʻohe lāʻau lapaʻau no porphyria, hiki ke mālama ʻia ke ʻano. Hiki ke hoʻololi i kekahi ʻano nohona a / a i ʻole nā ​​lāʻau i pale i nā ʻōuli a me nā pilikia o ka maʻi. Pili ka mālama pilikino i ke ʻano o ka porphyria āu e loaʻa ai. Inā he nīnau kāu e pili ana i kāu hopena a e pili ana paha i ka porphyria, e kamaʻilio me kāu kauka olakino.

E aʻo hou aʻe e pili ana i nā hoʻokolohua hoʻokolohua, nā pae kuhikuhi, a me ka hoʻomaopopo ʻana i nā hopena.

Aia kekahi mea ʻē aʻe e pono iaʻu e ʻike e pili ana i nā hōʻike porphyrin?

ʻOiai ka hoʻoilina o ka nui o nā ʻano porphyria, hiki ke loaʻa ʻia kekahi mau ʻano porphyria. Hiki ke kumu ʻia ka porphyria e nā ʻano like ʻole, e like me ka hōʻike nui ʻana i ke kēpau, HIV, hepatitis C, ka nui o ka hao, a me / a i ʻole ka hoʻohana nui ʻana i ka waiʻona.

Nā kūmole

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ʻAʻole pono e hoʻohana i ka ʻike ma kēia pūnaewele i pani no ka mālama olakino ʻoihana a ʻōlelo aʻoaʻo paha. Kāhea aku i ka mea mālama ola inā he nīnau kāu e pili ana i kou olakino.