ʻO Porphyria: he aha ia, nā ʻōuli a pehea e hana ʻia ai ka mālama ʻana

Anter

• Nā ʻōuli o Porphyria
• Pehea e hana ai i ka lāʻau

Kūlike ʻo Porphyria i kahi hui o nā maʻi kūlohelohe a me nā maʻi maʻamau i ʻike ʻia e ka hōʻiliʻili ʻana o nā mea i hana i ka porphyrin, kahi protein i kuleana no ka lawe ʻana o ka oxygen i ke kahe o ke koko, he mea nui ia no ka hoʻokumu ʻana i ka heme a, no laila, hemoglobin. Hoʻopili nui kēia maʻi i ka ʻōnaehana, ʻili a me nā mea ʻē aʻe.

Ua hoʻoilina ʻia ʻo Porphyria, a i ʻole hoʻoilina ʻia mai nā mākua, akā naʻe, i kekahi mau hihia, loaʻa i ke kanaka ka hoʻololi ʻana akā ʻaʻole hoʻomohala i ka maʻi, kapa ʻia ʻo porphyria latent. No laila, hiki i kekahi mau hanana kaiapuni ke hoʻonāukiuki i ka hiʻona o nā hōʻailona, ​​e like me ka lā lā, nā pilikia o ke ake, ka hoʻohana ʻana i ka waiʻona, ka puhipaka, ka naʻau kaumaha a me ka nui o ka hao i loko o ke kino.

ʻOiai ʻaʻohe lāʻau lapaʻau no porphyria, kōkua ka lāʻau e hōʻemi i nā ʻōuli a pale i ka lapalapa ʻana, a he mea nui ka ʻōlelo a ke kauka.

Nā ʻōuli o Porphyria

Hiki ke hoʻokaʻawale ʻia ʻo Porphyria e like me nā hōʻike pilikino i loko o ka huʻi a me ka lōʻihi. ʻO ka porphyria huehue pū kekahi me nā ʻano o ka maʻi e kumu ai nā ʻōuli i ka ʻōnaehana ʻōiwi a ʻike koke ʻia, a hiki ke hala ma waena o 1 a 2 mau pule a hoʻomaikaʻi holomua I ka hihia o ka porphyria mau, ʻaʻole pili hou nā ʻōuli i ka ʻili a hiki ke hoʻomaka i ka wā kamaliʻi a i ʻole ke ʻōpio a mau no kekahi mau makahiki.

ʻO nā hōʻailona nui:

• Porphyria huehue

  • ʻEha nui a ʻūhū ma ka ʻōpū;
  • ʻEha ma ka umauma, nā wāwae a i ʻole ke kua;
  • ʻO ka paʻa ʻana a i ʻole ka pehu paha;
  • ʻO ka luaʻi;
  • ʻO ka hiamoe ʻole, ka hopohopo a me ka hoʻonāukiuki;
  • Palpitations a me ke koko kiʻekiʻe;
  • Hoʻololi i ka noʻonoʻo, e like me ka huikau, nā haʻalulu, ka disorientation a i ʻole ka paranoia;
  • Nā pilikia hanu;
  • ʻEha puʻupuʻu, ʻūlū ʻana, numbness, nāwaliwali a i ʻole palapū;
  • Mimi ʻulaʻula a ʻeleʻele paha.

• Porphyria maʻi a i ʻole cutaneus:

  • ʻIke i ka lā a me ka mālamalama hana, i kekahi manawa e ʻeha ana a e ʻā ana i ka ʻili;
  • ʻUlaʻula, pehu, ʻeha a ʻili hoʻi o ka ʻili;
  • Pahū ma ka ʻili i hala he mau pule e hoʻōla;
  • ʻIli lahilahi;
  • Mimi ʻulaʻula a ʻeleʻele paha.

Hana ʻia ke kuhi o ka porphyria ma o nā hoʻokolohua hoʻokolohua, kahi a ke kauka e nānā ai i nā ʻōuli i hōʻike ʻia a wehewehe ʻia e ke kanaka, a ma o nā hoʻokolohua hoʻokolohua, e like me nā hoʻokolohua koko, ka noho a me ka mimi. Eia hou, ʻoiai he maʻi maʻi ia, e koi ʻia kahi hoʻāʻo genetics e ʻike i ka hoʻololi no ke porphyria.

Pehea e hana ai i ka lāʻau

Hoʻololi ka hoʻomaʻamaʻa e like me ke ʻano o ka porphyria o ke kanaka. I ka hihia o ka porphyria huehue, no ka laʻana, hana ʻia ka lapaʻau ma ka haukapila me ka hoʻohana ʻana i nā lāʻau e hōʻoluʻolu ai i nā ʻōuli, a me ka lawelawe ʻana o ke serum i loko o ke aa o ka mea maʻi e pale ai i ka make wai a me nā injection o ka hemin i mea e palena ai ka hana porphyrin.

I ka hihia o ka porphyria cutaneous, pono ia e hōʻalo i ka lā a hoʻohana i nā lāʻau, e like me beta-carotene, nā mea hoʻohui vitamin D a me nā lāʻau e mālama ai i ka malaria, e like me Hydroxychloroquine, ka mea e kōkua ai e omo i ka nui o ka porphyrin. Eia hou, i kēia hihia, hiki ke lawe ʻia ke koko e hoʻoliʻiliʻi i ka nui o ka hao o ka hao a, no laila, ka nui o ka porphyrin.