ʻO Pemphigus Foliaceus

Anter

• He aha nā hōʻailona?
• He aha nā kumu?
• He aha nā koho lapaʻau?
• He aha nā pilikia?
• Ka wā e ʻike ai i ke kauka
• Outlook

Hōʻike Overview

ʻO Pemphigus foliaceus kahi maʻi autoimmune nāna e hoʻokumu i nā palahu ʻeha ma kou ʻili. He ʻāpana ia o kahi ʻohana o nā ʻano ʻili laha i kapa ʻia ʻo pemphigus e hana ana i nā palapū a i ʻole nā ​​ʻeha ma ka ʻili, i ka waha, a i ʻole i nā genital.

ʻElua ʻano nui o ka pemphigus:

• pemphigus vulgaris
• pemphigus foliaceus

ʻO Pemphigus vulgaris ka ʻano maʻamau a ʻoi loa o ke ʻano. Hoʻopili ka Pemphigus vulgaris ʻaʻole wale i ka ʻili, akā me nā membrane mucous. Mālama ia i nā palapū ʻeha ma kou waha, ma kou ʻili, a me kou genitalia.

Hoʻokumu ʻo Pemphigus foliaceus i nā palapū liʻiliʻi e hana ma ka ʻaoʻao kiʻekiʻe a me ka maka. ʻOi aku ka māmā ma mua o ka pemphigus vulgaris.

ʻO Pemphigus erythematosus kekahi ʻano pemphigus foliaceus e hana i nā palapū ma ka maka wale nō. Hoʻopili ia i ka poʻe me ka lupus.

He aha nā hōʻailona?

Hoʻokumu ʻo Pemphigus foliaceus i nā palapū piha piha i ka wai i kou ʻili, pinepine ma kou umauma, kua, a me nā poʻohiwi. I ka mua ua liʻiliʻi nā pālū, akā ulu lākou a hoʻonui i ka helu. Hiki iā lākou ke uhi i kou kino holoʻokoʻa, maka, a me ke poʻo.

Māmama wale nā ​​ʻōhū. E pio paha ka wai mai iā lākou. Inā ʻānai ʻoe i kou ʻili, hiki i ka papa luna kiʻekiʻe a pau ke kaʻawale mai ka lalo i hope a peel i kahi pepa.

Ma hope o ka hāmama ʻana o nā ʻōpala, hiki iā lākou ke hana i nā ʻeha. Pākuʻi ʻia nā ʻeha a palaoa hoʻi.

ʻOiai ʻaʻohe ʻeha ka pemphigus foliaceus i ka maʻa mau, ʻike paha ʻoe i ka ʻeha a i ʻole ka ʻā ʻana o ke ahi i ka wahi o nā palapū. ʻEkake pū paha nā ʻōhū.

He aha nā kumu?

ʻO Pemphigus foliaceus kahi maʻi autoimmune. ʻO ka maʻamau, hoʻokuʻu ka ʻōnaehana pale pale i nā protein i kapa ʻia he antibodies e kaua aku i nā mea komo haole e like me ka bacteria a me nā mea hoʻomaʻi. I ka poʻe me ka maʻi autoimmune, hele kuhi hewa nā mea ʻāpala ma hope o nā kino o ke kino.

Ke loaʻa iā ʻoe ka pemphigus foliaceus, paʻa nā mea ʻāpala i kahi protein i ka papa waho o kou ʻili, i kapa ʻia ʻo epidermis. I kēia papa o ka ʻili he mau hunaola i kapa ʻia he keratinocytes. Hoʻokumu kēia mau pūnaewele i ka protein - keratin - hāʻawi i ke kūkulu a me ke kākoʻo i kou ʻili. Ke hoʻouka nā antibodies i nā keratinocytes, hoʻokaʻawale lākou.Hoʻopiha ka wai i nā hakahaka a lākou e haʻalele ai. Hoʻokumu kēia wai i nā palapū.

ʻAʻole maopopo i nā kauka ke kumu o ka pemphigus foliaceus. Hiki i kekahi mau mea ke hoʻonui i kou likelike o ka loaʻa ʻana o kēia ʻano, me:

• he lālā ʻohana me ka pemphigus foliaceus
• ke waiho lā i ka lā
• ke kiʻi ʻana i kahi nahu ʻāpala (ma nā ʻāina ʻAmelika Hema)

Ua pili pū kekahi mau lāʻau i ka pemphigus foliaceus, me:

• penicillamine (Cuprimine), hoʻohana ʻia e mālama i ka maʻi o Wilson
• ʻo ka angiotensin e hoʻohuli nei i nā mea kūpale enzyme e like me captopril (Capoten) a me enalapril (Vasotec), hoʻohana ʻia e mālama i ke koko kiʻekiʻe
• angiotensin-II receptor blockers e like me candesartan (Atacand), i hoʻohana ʻia e mālama i ke koko kiʻekiʻe
• antibiotics e like me rifampicin (Rifadin), hoʻohana ʻia e mālama i nā maʻi bacteria
• nā lāʻau anti-inflammatory nonsteroidal (NSAIDs)

Hiki ke hoʻomaka ʻo Pemphigus foliaceus i kēlā me kēia makahiki, akā pili pinepine ia i nā makahiki 50 a 60 paha. ʻO ka poʻe i hoʻoilina Iudaio i ka nui o ka makaʻu no ka pemphigus vulgaris.

He aha nā koho lapaʻau?

ʻO ka pahuhopu o ka mālama ʻana e hoʻopau i nā palapū a hoʻōla i nā maʻi i loaʻa iā ʻoe. Kauoha paha kāu kauka i ka huakine a i ʻole nā ​​lāʻau pākiko. Lawe kēia lāʻau i lalo i ka mumū i kou kino. Hiki i nā koina kiʻekiʻe o nā corticosteroids ke kumu i nā hopena ʻē aʻe e like me ka hoʻonui ʻana o ke kō i ke kō, loaʻa ke kaupaona, a me ka nalo ʻana o ka iwi.

Hoʻohana ʻia nā lāʻau ʻē aʻe e mālama i ka pemphigus foliaceus:

• Nā mea hoʻopōkō Immune. ʻO nā lāʻau e like me azathioprine (Imuran) a me mycophenolate mofetil (CellCept) pale i kāu ʻōnaehana pale maʻi mai ka hoʻouka kaua ʻana i nā kino ponoʻī o kou kino. ʻO ka hopena ʻaoʻao nui mai kēia mau lāʻau ka hoʻonui i ka makaʻu no ka maʻi.
• Nā Antibiotics, nā lāʻau antiviral, a me nā lāʻau antifungal. Hiki i kēia mau mea ke pale aku i nā maʻi lele mai nā mea āpau inā hāmama lākou.

Inā uhi ka nui i kou ʻili, pono paha ʻoe e noho i ka haukapila no ka mālama ʻana. E hoʻomaʻemaʻe nā kauka a me nā kahu i kou ʻeha e pale aku i ka maʻi. Loaʻa paha iā ʻoe nā wai e pani i nā mea āu i nalo ai mai nā ʻeha.

He aha nā pilikia?

Hiki i nā pāhaʻi hāmama ke lilo i maʻi me nā koʻohune. Inā komo ka bacteria i kou kahe koko, hiki iā lākou ke kumu i kahi maʻi hoʻoweliweli e kapa ʻia sepsis.

Ka wā e ʻike ai i ke kauka

E ʻike i kāu kauka inā he palapū kou ʻili, keu hoʻi inā hāmama lākou.

E nīnau kāu kauka e pili ana i kāu mau hōʻailona a nānā i kou ʻili. Hiki iā lākou ke hemo i kahi ʻāpana o ke kiko mai ka blister a hoʻouna iā ia i kahi keʻena hoʻokolohua no ka hoʻāʻo ʻana. Kāhea ʻia kēia he biopsy ʻili.

Hiki paha iā ʻoe ke hoʻāʻo i ke koko e nānā no nā mea ʻohola a kou ʻōnaehana pale e hua ai ke loaʻa iā ʻoe ka pemphigus foliaceus.

Inā ua ʻike ʻia ʻoe me ka pemphigus, pono ʻoe e hoʻokaʻaʻike i kāu kauka inā hoʻomohala ʻoe:

• ʻūlū hou a ʻeha hoʻi
• he palahalaha koke ʻana ma ka helu o nā ʻeha
• fiva
• ʻulaʻula a pehu paha
• haʻalulu
• nāwaliwali a ʻaʻa hoʻi i nā mākala a i ʻole nā ​​ami

Outlook

E ʻoi aku ka maikaʻi o kekahi poʻe me ka ʻole o ka lāʻau. Noho paha nā poʻe ʻē aʻe me ka maʻi no nā makahiki he nui. Pono ʻoe e ʻai i ka lāʻau no nā makahiki he nui i mea e pale ʻole ai i nā ʻōhū.

Inā ua hana kahi lāʻau i ka pemphigus foliaceus, ke kū ʻana i ka lāʻau hiki ke hoʻomaʻemaʻe pinepine i ka maʻi.