He aha ka granulomatosis a Wegener a pehea e mālama ai

Anter

• Nā hōʻailona nui
• Pehea e mālama ai
• Pehea e hana ʻia ai ke kuhi
• He aha ke kumu o ka granulomatosis a Wegener

ʻO ka granulomatosis a Wegener, i ʻike ʻia he granulomatosis me polyangiitis, kahi maʻi laha ʻole a holomua hoʻi e hoʻoulu ai i nā kīʻaha koko ma nā ʻāpana like ʻole o ke kino, e hana ana i nā ʻōuli e like me ke kahamaha o ke ala, ka hanu ʻana o ka hanu, nā ʻili ʻili, nā ihu, nā mumū i nā pepeiao, ke kuni. , malaise, nalo o ka makemake ʻole a hoʻonāukiuki paha o ka maka.

ʻOiai he maʻi ia i hoʻololi ʻia e nā loli autoimmune, hana nui ʻia kāna mālama ʻana me nā lāʻau e hoʻoponopono i ka ʻōnaehana inume, e like me nā corticosteroids a me nā immunosuppressants, a ʻoiai ʻaʻohe lāʻau lapaʻau, mālama maikaʻi ʻia ka maʻi, e ʻae ana i kahi ola maʻamau.

ʻO Wegener's granulomatosis kahi ʻāpana o kahi hui o nā maʻi i kapa ʻia ʻo vasculitis, i hōʻike ʻia e ka hoʻoulu ʻana a me ka hōʻino ʻana i nā kīʻaha koko, kahi e hōʻino ai i ka hana o nā mea like ʻole. Hoʻomaopopo maikaʻi i nā ʻano vasculitis e ola nei a pehea e ʻike ai iā lākou.

Nā hōʻailona nui

ʻO kekahi o nā hōʻailona nui i hoʻokumu ʻia e kēia maʻi nā:

• Sinusitis a me nā ihu;
• Cough, ʻeha o ka umauma a me ka liʻiliʻi o ka hanu;
• Ke hoʻokumu ʻia ʻana o nā ulcer i ka mucosa o ka ihu, hiki ke alakaʻi i kahi deformity i ʻike ʻia me ka ihu noho lio;
• Hoʻonā i nā pepeiao;
• Conjunctivitis a me nā mumū ʻē aʻe i nā maka;
• ʻO ka wela a me ka hou ka pō;
• Ka luhi a me ka luhi.
• Ka nele o ka makemake a me ka pohō kaumaha;
• ʻEha puʻupuʻu a me ka huʻihuʻi ʻana o nā hono.
• Loaʻa ke koko i ka mimi.

I nā hihia kakaʻikahi, aia paha kekahi hōʻino ʻia o ka puʻuwai, e alakaʻi ana i nā pericarditis a i ʻole nā ​​leona i nā aʻa coronary, a i ʻole nā ​​ʻōnaehana hopohopo, e alakaʻi ana i nā ʻōuli neurological.

Eia hou, ua hoʻonui ka poʻe maʻi me kēia maʻi i ka hoʻonui i ka thrombosis, a pono e nānā i nā ʻōuli e hōʻike ana i kēia pōpilikia, e like me ka pehu ʻana a me ka ʻula o nā lālā.

Pehea e mālama ai

ʻO ka mālama ʻana i kēia maʻi e komo pū me ka hoʻohana ʻana i nā lāʻau e kōkua i ka kaohi ʻana i ka ʻōnaehana paleʻea, e like me Methylprednisolone, Prednisolone, Cyclophosphamide, Methotrexate, Rituximab a i ʻole nā ​​lāʻau olaola.

Hiki ke hoʻopili ʻia ka lāʻau antibiotic sulfamethoxazole-trimethoprim me ka mālama ʻana ma ke ʻano he ala e hōʻemi ai i ka hoʻi hou ʻana o kekahi ʻano o nā maʻi.

Pehea e hana ʻia ai ke kuhi

I mea e kuhikuhi ai i ka granulomatosis a Wegener, e loiloi ke kauka i nā ʻōuli i hōʻike ʻia a me ka hoʻokolokolo kino ʻana, i hāʻawi ʻia ai nā hōʻailona mua.

A laila, e hōʻoia i ke kuhi, ʻo ka hoʻokolokolo nui ka hana ʻana i kahi biopsy o nā ʻino i hoʻopili ʻia, kahi e hōʻike ai i nā loli i kūlike me ka vasculitis a i ʻole ka necrotizing granulomatous inflammation. E kauoha ʻia paha nā hoʻāʻo, e like me ke ana ANCA antibody.

Eia hou, he mea nui e hoʻokaʻawale ke kauka i kēia maʻi mai nā poʻe ʻē aʻe i loaʻa like nā ʻano like, e like me ka maʻi ʻaʻaʻa, lymphoma, ka hana ʻana a ka cocaine a i ʻole lymphomatoid granulomatosis, no ka laʻana.

He aha ke kumu o ka granulomatosis a Wegener

ʻO nā kumu kikoʻī e alakaʻi i ka hoʻomaka ʻana o kēia maʻi ʻaʻole i ʻike ʻia, akā naʻe, ʻike ʻia e pili ana ia i nā loli i ka pane pale pale, i hiki ke lilo i nā ʻāpana o ke kino ponoʻī a i ʻole nā ​​mea kūwaho e komo i ke kino.