Mea Kākau: Lewis Jackson
Lā O Ka Hana: 14 Mei 2021
HōʻAno Hou I Ka Lā: 20 Iune 2024
Anonim
Dr. Michael Alan Hernandez explains the soft tissue sarcoma | Salamat Dok
Wikiō: Dr. Michael Alan Hernandez explains the soft tissue sarcoma | Salamat Dok

Anter

He mea maʻamau kēia?

ʻO ka sarcoma a Ewing kahi tumo maʻi ʻaʻai ʻole o ka iwi a i ʻole nā ​​mea palupalu. Kū ka hapanui i ka poʻe ʻōpio.

Ma ka hapanui, pili ia i ka poʻe ʻAmelika. Akā no nā ʻōpio he 10 a 19 mau makahiki, lele kēia i nā ʻAmelika ma kēia pae makahiki.

ʻO ke kumu kēia ma kahi o 200 mau hihia i ʻike ʻia ma ʻAmelika Hui Pū ʻIa i kēlā me kēia makahiki.

Ua kapa ʻia ka sarcoma no ke kauka ʻAmelika ʻo James Ewing, ka mea nāna i wehewehe mua i ka tum tum i ka makahiki 1921. ʻAʻole maopopo leʻa ke kumu o Ewing, no laila ʻaʻohe ʻano ʻike o ke kāohi. Hiki ke mālama ʻia ke ʻano, a, inā loaʻa i ke kakahiaka nui, hiki ke ola piha.

E hoʻomau i ka heluhelu ʻana e aʻo hou aʻe.

He aha nā hōʻailona a hōʻailona paha o ka sarcoma o Ewing?

ʻO ka hōʻailona maʻamau o ka sarcoma o Ewing ka ʻeha a i ʻole ka pehu ʻana ma kahi o ka tumo.

Hiki i kekahi poʻe ke hoʻomōhala i kahi puʻupuʻu i ʻike ʻia ma ka ʻili o ko lākou ʻili. Mahanahana paha ka wahi i pā ʻia.

ʻO nā ʻōuli ʻē aʻe e like me:

  • nalo ʻai ʻole
  • fiva
  • Kaumaha emi
  • luhi
  • manaʻo nui maikaʻi ʻole (malaise)
  • iwi e haki me ke kumu ʻole i ʻike ʻia
  • anemia

Hana ʻia nā tumors ma nā lima, nā wāwae, nā pelvis a i ʻole ka umauma. Aia paha he mau hōʻailona kikoʻī i kahi o ka tumo. ʻO kahi laʻana, ʻike paha ʻoe i ka pōkole o ka hanu inā kū ka tumo i kou umauma.


He aha ke kumu o ka sarkoma a Ewing?

ʻAʻole maopopo ke kumu kūpono o ka sarcoma o Ewing. ʻAʻole hoʻoilina ia, akā hiki ke pili i nā loli hoʻoilina ʻole i nā genes kikoʻī i kū i ke ola o ke kanaka. Ke hoʻololi nā chromosome 11 a me 12 i nā mea kūpuna, hoʻoulu ia i kahi ulu o nā hunaola. E alakaʻi paha kēia i ka hoʻomohala ʻana o ka sarcoma o Ewing.

e hoʻoholo i ke ʻano kikoʻī o ke cell kahi i hoʻomaka ai ʻo Ewing sarcoma e hoʻomau nei.

ʻO wai ka mea kūpilikiʻi no ka sarkoma a Ewing?

ʻOiai hiki ke hoʻomohala i ka sarcoma a Ewing i kēlā me kēia makahiki, ʻoi aku ka nui o nā poʻe me ke ʻano i ʻike ʻia i ka ʻōpio. ʻO ka makahiki waena o ka poʻe i hoʻopilikia ʻia.

Ma ʻAmelika Hui Pū ʻIa, ʻoi aku ka hoʻomohala ʻana o ka sarcoma a Ewing i ka poʻe Caucasians ma mua o ko ʻAmelika-ʻAmelika. Ua hōʻike ʻo ka American Cancer Society ʻaʻole pili iki ka maʻi ʻaʻai i nā hui lāhui ʻē aʻe.

E hoʻomohala paha nā kāne i ke ʻano. Ma kahi noiʻi ʻana o 1,426 poʻe i hoʻopilikia ʻia e Ewing, he kāne a he wahine.

Pehea e ʻike ʻia ai ka sarcoma a Ewing?

Inā ʻoe a ʻo kāu keiki e ʻike i nā ʻōuli, e ʻike i kāu kauka. E pili ana i nā hihia, ua pālahalaha ka maʻi, a i ʻole metastasized, e ka manawa o ke kuhi. ʻO ka hiki wawe o ka hōʻailona, ​​ʻoi aku paha ka maikaʻi o ka lāʻau.


E hoʻohana kāu kauka i kahi hui o nā hōʻike diagnostic e hiki mai ana.

Nā hoʻāʻo kiʻi

Pākuʻi paha kēia i hoʻokahi a ʻoi paha o kēia mau mea:

  • X-kukuna e kiʻi i kou mau iwi a hoʻomaopopo i ke alo o kahi tumo
  • MRI scan e kiʻi i nā kiʻi palupalu, nā ʻokena, nā mākala, a me nā hanana ʻē aʻe a hōʻike i nā kikoʻī o kahi tumo a i ʻole nā ​​mea ʻē aʻe ʻē aʻe
  • CT scan i ke kiʻi i nā ʻāpana o nā iwi a me nā aʻa
  • Nā kiʻi EOS e hōʻike i ka launa pū o nā hono a me nā mākala ʻoiai ʻoe e kū nei
  • scan iwi o kou kino holoʻokoʻa e hōʻike ai inā he metastasized kahi tumo
  • ʻO ka scan PET e hōʻike ai inā paha he mau tumors nā wahi i ʻike ʻole ʻia i ʻike ʻia i nā scans ʻē aʻe

ʻO Biopsies

Ke kiʻi ʻia kahi tumo, hiki i kāu kauka ke kauoha i kahi biopsy e nānā i kahi ʻāpana o ka tumo ma lalo o kahi microscope no ka ʻike kikoʻī.

Inā liʻiliʻi ka tumo, hoʻoneʻe paha kāu kauka lāʻau i nā mea āpau ma ke ʻano he ʻāpana o ka biopsy. Kapa ʻia kēia he biopsy kūwaho, a hana ʻia ia ma lalo o ka anesthesia laulā.

Inā ʻoi aku ka nui o ka tumo, ʻoki paha i kāu kauka lāʻau i kahi ʻāpana. Hana ʻia kēia ma ke ʻoki ʻana i kou ʻili e wehe i kahi ʻāpana o ka tumo. A i ʻole e hoʻokomo paha kāu kauka lāʻau i kahi kui kolo nui i loko o kou ʻili e hemo i kahi ʻāpala. Kāhea ʻia kēia mau biopsies incisional a hana pinepine ʻia ma lalo o ka anesthesia ākea.


Hoʻokomo pū paha kāu mea kauka iā ʻoe i ke kui kele i loko o ka iwi e lawe i kahi laʻana o ka wai a me nā keena e ʻike inā ua pālahalaha ka maʻi ʻaʻai i loko o kou iwi iwi.

Ke wehe ʻia kaʻiʻo tumora, aia kekahi mau hoʻokolohua e kōkua i ka ʻike ʻana i kahi sarcoma o Ewing. Hāʻawi pū kekahi nā hōʻoia koko i ka ʻike kōkua no ka lāʻau.

Nā ʻano o ka sarcoma a Ewing

Hoʻokaʻawale ʻia ka sarcoma o Ewing e ka pā ʻana o ka maʻi ʻaʻai mai ka iwi a palupalu paha kahi i hoʻomaka ai. ʻEkolu ʻano:

  • ʻO ka sarcoma a Ewing i hoʻopaʻa ʻia: ʻAʻole i pālahalaha ka maʻi ʻaʻai i nā wahi ʻē aʻe o ke kino.
  • ʻO sarcoma a Metastatic Ewing: Ua pālahalaha ka maʻi ʻaʻai i nā akemāmā a i ʻole nā ​​wahi ʻē aʻe i ke kino.
  • Hana hou ʻo Ewing's sarcoma: ʻAʻole pane ka maʻi ʻaʻai i ka lāʻau a hoʻi mai paha ma hope o ke kūleʻa maikaʻi ʻana o ka lāʻau. Kū pinepine pinepine ia i nā māmā.

Pehea e mālama ai i ka sarcoma a Ewing?

ʻO ka mālama ʻana i ka sarcoma a Ewing ma muli o kahi i hoʻomaka ai ka maʻi tumo, ka nui o ka tumo, a inā paha ua pāhola ka maʻi ʻaʻai.

ʻO ka maʻamau, pili ka mālama ʻana i hoʻokahi a ʻoi paha mau hoʻokokoke ʻana, e like me:

  • chemotherapy
  • lāʻau pāhawewe
  • ʻoki kino
  • hoʻomālama proton therapy
  • ʻo ka chemotherapy kiʻekiʻe i hoʻohui ʻia me ka transplant cell stem

Nā koho lapaʻau no ka sarcoma o Ewing kūloko

ʻO ke ala maʻamau no kahi maʻi ʻaʻai ʻaʻole pālahalaha he hui pū ʻia o:

  • ʻoki kino e hemo i ka puʻupuʻu
  • Pāhawewe i ka wahi hikoko e pepehi i nā koena maʻi ʻaʻai
  • e hoʻomake i ka chemotherapy hiki i nā hunaola maʻi ʻaʻai i hoʻolaha ʻia, a i ʻole micrometastasies

Ua ʻike nā kānaka noiʻi i hoʻokahi noiʻi 2004 ua kūleʻa ka hoʻohuihui hoʻohui e like me kēia. Ua ʻike lākou i ka hopena i hopena i kahi ola ola 5 mau makahiki ma kahi o 89 pākēneka a me kahi helu ola 8-makahiki ma kahi o 82 pākēneka.

Kaukaʻi ʻia i ka pūnaewele tumora, pono hou aʻe kahi lāʻau hou ma hope o ke kaha ʻana e hoʻololi a hoʻihoʻi hou i ka hana a ka lālā.

Nā koho lapaʻau no ka sarcoma a Ewing metastasized a hoʻi hou

ʻO ka mālama ʻana no ka sarcoma a Ewing i metastasize mai ka pūnaewele kumu e like me ia no ka maʻi kūloko, akā me ka helu o ka kūleʻa i lalo loa. Ua hōʻike nā kānaka noiʻi i hoʻokahi manawa ʻo ke ola o 5 mau makahiki ma hope o ka mālama ʻana no ka sarcoma metastasized ʻo Ewing ma kahi o 70 pākēneka.

ʻAʻohe mālama maʻamau no ka sarcoma hou o Ewing. Hoʻololi nā koho lapaʻau ma muli o kahi i hoʻi ai ka maʻi ʻaʻai a me nā ʻano o ka hana ma mua.

Ke hoʻomau nei nā hoʻokolohua hoʻokolohua he nui a me nā noiʻi noiʻi e hoʻomaikaʻi i ka hoʻomaʻamaʻa no ka sarcoma metastasized a me ka hoʻi hou ʻana o Ewing. Pākuʻi ʻia kēia mau mea:

  • transplants keleawe koʻokoʻo
  • immunotherapy
  • hoʻomālama ʻia me nā meaola monoclonal
  • huikau hoʻohui lāʻau hou

He aha ka manaʻo no ka poʻe me ka sarcoma o Ewing?

Ke hoʻomohala nei nā lapaʻau hou, ke hoʻomaikaʻi nei ka nānā aku no ka poʻe i hoʻopilikia ʻia e ka sarcoma a Ewing. ʻO kāu kauka kāu kumuwaiwai ʻoi loa no ka ʻike e pili ana i kāu kuanaʻike pilikino a me ke ola.

Ua hōʻike ʻo ʻAmelika Hui Pū ʻIa ʻAmelika ʻo ka helu ola 5 mau makahiki no ka poʻe i hoʻonohonoho i nā tumors ma kahi o 70 pākēneka.

No ka poʻe me nā tumiko metastasized, ka ola o 5 mau makahiki he 15 a 30 pakeneka. ʻOi aku paha ka maikaʻi o kāu nānā inā ʻaʻole i pālahalaha ka maʻi ʻaʻai i nā mea ʻē aʻe ma mua o nā akemāmā.

ʻO ka helu ola 5 mau makahiki no ka poʻe me ka sarcoma hou o Ewing.

Hiki paha ke hoʻopili i kāu kuanaʻike pākahi, me:

  • makahiki ke kuhi ʻia
  • ka nui o ka tumo
  • wahi ʻōiwi
  • pehea ka maikaʻi o ka pane ʻana o kou tumo i ka chemotherapy
  • pae o ke kō koko
  • ka mālama mua ʻana no ka maʻi ʻaʻai ʻokoʻa
  • kāne kāne

Hiki iā ʻoe ke manaʻo e nānā ʻia i ka wā a ma hope o ka mālama ʻana. E ho'āʻo hou kāu kauka i kekahi manawa e hoʻoholo inā ua pālahalaha ka maʻi ʻaʻai.

ʻOi aku ka nui o ka makaʻu o ka poʻe i loaʻa ka sarcoma o Ewing i ka hoʻomohala ʻana i kahi ʻano maʻi ʻelua. Ua ʻōlelo ʻo ka ʻAhahui Kanaka ʻAmelika e like me ka nui o ka poʻe ʻōpio me ka sarcoma a Ewing e ola nei i ka wā makua, ʻike ʻia nā hopena lōʻihi o kā lākou mālama ʻana i ka maʻi ʻaʻa. Ke hoʻomau nei ka noiʻi ʻana ma kēia wahi.

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