Dermatomyositis: he aha ia, nā ʻōuli a me nā lāʻau

Anter

• Nā hōʻailona nui
• Pehea e hana ʻia ai ke kuhi
• Pehea e mālama ai

ʻO Dermatomyositis kahi maʻi maʻi laha ʻole e hoʻopili nui i nā mākala a me ka ʻili, e hoʻoulu ana i ka nāwaliwali o nā mākala a me nā ʻāʻī dermatological. Kū pinepine ia i nā wahine a ʻoi aku ka maʻamau i nā mākua, akā hiki ke ʻike ʻia i nā poʻe ma lalo o ka makahiki 16, i kapa ʻia ʻo dermatomyositis kamaliʻi.

I kekahi manawa, pili ka dermatomyositis me ka maʻi ʻaʻai, kahi hiki ke lilo i hōʻailona o ka hoʻomohala ʻana i kekahi ʻano o nā maʻi ʻaʻai e like me ka lung, ka umauma, ovarian, prostate a me ka maʻi ʻaʻai kolona. Hiki ke pili pū ʻia me nā maʻi ʻē aʻe o ka pale ʻana, e like me scleroderma a me nā maʻi maʻi hoʻopili. Hoʻomaopopo pū i ke ʻano o ka scleroderma.

ʻO nā kumu o kēia maʻi mai ke kumu autoimmune, kahi o nā kino pale pilikino o ke kino e hoʻouka i nā mākala a hana i ka hoʻowahāwahā o ka ʻili, a ʻoiai ke kumu o kēia hopena ʻaʻole i maopopo piha, ua ʻike ʻia e pili ana ia i ka genetical nā hoʻololi, a i ʻole hoʻohuli ʻia e ka hoʻohana ʻana i kekahi mau lāʻau a i ʻole nā ​​maʻi viral. ʻAʻohe lāʻau ʻo Dermatomyositis, a no laila he maʻi maʻi mau ia, akā naʻe, hiki i ka mālama ʻana me nā lāʻau corticosteroids a i ʻole nā ​​lāʻau immunosuppressive ke kōkua i ka mālama ʻana i nā ʻōuli.

Nā hōʻailona nui

Hiki i nā ʻōuli o dermatomyositis ke hoʻopili pū me:

• ʻO ka nāwaliwali o nā mākala, ʻoi aku i nā scapular, pelvic a me nā cerviera ʻāpana, symmetrically a me ka ulu ʻana o ka lohi;
• ʻO nā hiʻohiʻona o nā kiko a ʻulaʻula ʻulaʻula paha i ka ʻili, keu hoʻi i nā ami o nā manamana lima, kuʻekuʻe lima a me nā kuli, i kapa ʻia ka hōʻailona a Gottron a i ʻole nā ​​papule;
• ʻO nā kiko Violet ma nā lihilihi o luna, i kapa ʻia ʻo heliotrope;
• ʻEha hui a pehu;
• Fiva;
• Māluhiluhi;
• Pilikia i ka ale ʻana;
• ʻEha ʻeha;
• ʻO ka luaʻi;
• Kaumaha emi.

ʻO ka maʻamau, paʻakikī paha ka poʻe me kēia maʻi i ka hana maʻamau i kēlā me kēia lā e like me ke kāhili ʻana i ko lākou lauoho, ka hele wāwae ʻana, ka piʻi ʻana i ke alapiʻi a i ʻole ke ala ʻana aʻe mai kahi noho. Hoʻohui ʻia, ʻinoʻino paha nā ʻōuli o ka ʻili me ka ʻike ʻia o ka lā.

I nā hihia ʻoi loa, a i ʻole ke ʻike ʻia ka dermatomyositis i ka hui pū ʻana me nā maʻi autoimmune ʻē aʻe, hiki ke hoʻopili ʻia nā mea ʻē aʻe e like me ka puʻuwai, nā māmā a me nā puʻupaʻa, e hoʻopili ana i kāna hana a hana i nā pilikia koʻikoʻi.

Pehea e hana ʻia ai ke kuhi

Hana ʻia ke kuhi o dermatomyositis ma o ka loiloi ʻana i nā ʻōuli o ka maʻi, ka loiloi kino ʻana a me nā hoʻāʻo e like me ka biopsy muso, electromyography a i ʻole nā ​​hoʻāʻo ʻana o ke koko e ʻike i ke kū ʻana o nā mea e hōʻike ana i ka luku ʻia o nā mākala, e like me ka CPK, DHL a i ʻole AST nā hoʻāʻo, no ka laʻana. laʻana.

Aia paha ka hana ʻana o autoantibodies, e like me myositis-spesifik antibodies (MSA), anti-RNP a i ʻole anti MJ, no ka laʻana. hiki ke loaʻa i nā nui i nā hoʻokolohua koko.

E hōʻoia i ke kuhi, pono nō hoʻi i ke kauka e hoʻokaʻawale i nā ʻōuli o dermatomyositis mai nā maʻi ʻē aʻe i kumu i nā ʻōuli like, e like me polymyositis a i ʻole myositis me nā kino i hoʻohui ʻia, ʻo ia hoʻi nā maʻi ʻino o nā mākala. ʻO nā maʻi ʻē aʻe e pono e noʻonoʻo ʻia ʻo myofascitis, necrotizing myositis, polymyalgia rheumatica a i ʻole nā ​​inflammations i hoʻokumu ʻia e nā lāʻau lapaʻau, e like me clofibrate, simvastatin a i ʻole amphotericin, no ka laʻana.

Pehea e mālama ai

Hana ʻia ka mālama ʻana o dermatomyositis e like me nā ʻōuli i hōʻike ʻia e nā mea maʻi, akā i ka hapanui o nā hihia e hoʻopili ʻia me ka hoʻohana ʻana o:

• Corticosteroids e like me Prednisone, e like me ka mea e hoʻēmi ai i ka mumū i ke kino;
• Nā Immunosuppressants e like me Methotrexate, Azathioprine, Mycophenolate a i ʻole Cyclophosphamide, e hoʻēmi i ka pane o ka ʻōnaehana paleʻea;
• Nā hoʻoponopono ʻē aʻe, e like me Hydroxychloroquine, no ka mea he mea pono ia e hōʻoluʻolu i nā hōʻailona dermatological, e like me ka ʻike i ka mālam, no ka laʻana.

Lawe pinepine ʻia kēia mau mea hoʻōla i nā lāʻau kiʻekiʻe a no nā wā hoʻolōʻihi, a loaʻa ka hopena o ka hoʻemi ʻana i ke kaʻina hana hōʻino a me ka hōʻemi ʻana i nā hōʻailona o ka maʻi. Ke holo ʻole kēia mau lāʻau lapaʻau, kahi koho ʻē aʻe e lawelawe i ka immunoglobulin kanaka.

Hiki nō hoʻi ke hana i nā kauila physiotherapy, me nā hana hoʻoponopono e kōkua ai e hōʻoluʻolu i nā hōʻailona a hōʻalo i nā kuʻikahi a me nā retraction. Hōʻike ʻia ʻo Photoprotection, me nā pale sunscreens, i mea e pale aku ai i ka ʻino o nā ʻili o ka ʻili.

Ke pili ʻia ka dermatomyositis me ka maʻi ʻaʻai, ʻo ka lapaʻau kūpono loa ka mālama ʻana i ka maʻi ʻaʻai, e hoʻomālielie pinepine ana i nā hōʻailona a me nā hōʻailona o ka maʻi.