Pehea e mālama ai i ka phenylketonuria a pehea e pale ai i nā pilikia

Anter

• 1. Hoʻomaʻamaʻa meaʻai
• Pehea e hāʻawi palekana ai i ka waiū umauma
• 2. Hoʻohana o nā mea hoʻopihaʻai pono
• Nā pilikia kūpono o phenylketonuria
• Pehea e hōʻalo ai

ʻO ka mālama a me ka mālama ʻana i ka phenylketonuria i ka pēpē e alakaʻi ʻia e ka pediatrician, akā ʻo ka mālama nui ka hōʻalo ʻana i nā meaʻai i piha i ka phenylalanine, ʻo ia ka meaʻai nui i nā protein, e like me kaʻiʻo, ka iʻa, ka waiū, ka tī a me nā hua manu No laila, e makaʻala nā mākua o nā pēpē me phenylketonuria i ka meaʻai a kā lākou keiki, ma ka home a ma ke kula.

Eia hou, pono e hoʻonohonoho pono ʻia ka hānai ʻana i ka umauma e ka pediatrician, ʻoiai ka phenylalanine i ka waiū o ka waiū, ʻoiai ʻoi aku ka liʻiliʻi ma mua o ka mea i loaʻa i ka hapanui o nā lāʻau lapaʻau. ʻO ke kūpono, ʻo ka nui o ka phenylalanine no kahi pēpē a hiki i 6 mau makahiki o ka makahiki e mālama ʻia ma waena o 20 a 70 mg o phenylalanine no kg o ke kaumaha o ke kino.

He mea nui ka ukali ʻana no ka phenylketonuria e ukali ʻia e like me nā kulekele o ka pediatrician a me ka mea hānai meaʻai e pale ai i nā pilikia e ala aʻe ana, e pili nui ana i ka hoʻomohala ʻana o ka ʻōnaehana nūhou.

1. Hoʻomaʻamaʻa meaʻai

ʻO ka mālama kino ʻana ke ala nui e hōʻalo ai i nā pilikia o ka maʻi, ʻoiai ma o ka meaʻai e hiki ai ke kaohi i nā kiʻekiʻe o ka phenylalanine i loko o ke koko, a pēlā e pale ai i nā pilikia o ka maʻi. He mea nui e alakaʻi ʻia ka papaʻai e ka mea hānai e like me nā hopena o nā hoʻokolohua a ka pēpē e pono e hana mau ʻia e loiloi i nā pae o ka phenylalanine i loko o ke koko.

Hiki ke loaʻa ʻo Phenylalanine i nā meaʻai, nā holoholona a me nā mea kanu. No laila, e kaohi i ka maʻi a pale i nā pilikia he mea nui e hōʻalo i kekahi mau meaʻai, e like me:

• Nā meaʻai holoholona: nā ʻiʻo, ka waiū a me nā mea ʻai, nā hua, iʻa, iʻa iʻa, a me nā huahana iʻa e like me ka sausage, sausage, bacon, ham.
• Nā meaʻai o nā kumu kanu: ka palaoa, ka soy a me nā derivatives, nā pīpī, nā pīni, nā pī, nā lihi, nā nati, nā peanuts, nā walnuts, nā ʻalemona, nā hazelnuts, nā pistachios, nā hua paina;
• ʻO nā meaʻono me aspartame;
• Nā huahana i loaʻa i nā meaʻai pāpā ʻia ma ke ʻano he mea hoʻohuie like me nā pōpō, nā kuki, nā ʻaikalima a me nā berena.

Hiki ke hoʻopau i nā hua a me nā mea kanu e nā phenylketonurics, a me nā kō a me nā momona. Hiki nō hoʻi ke loaʻa ma ka mākeke i nā huahana kūikawā i hana ʻia no kēia mea hoʻolohe, e like me ka laiki, pasta a me nā pahū pahū, a aia kekahi mau papa hana i hiki ke hoʻohana ʻia e hana i nā meaʻai haʻahaʻa i ka phenylalanine.

E nānā i kahi papa inoa o nā meaʻai i waiwai i ka phenylalanine.

Pehea e hāʻawi palekana ai i ka waiū umauma

ʻOiai ʻo ka ʻōlelo aʻoaʻo e kāpae i ka waiū umauma mai ka papaʻai a ka pēpē, e hoʻohana ana i ka waiū pharmacy wale nō me ka ʻole o ka phenylalanine, hiki nō ke hānai i ka pēpē phenylketonuric, akā no kēia mea pono ia:

• E hana i kahi hōʻoia koko ma luna o ka pēpē i kēlā me kēia pule e nānā i nā pae o ka phenylalanine i loko o ke koko;
• E helu i ka nui o ka waiū o ka waiū e hāʻawi i ka pēpē, e like me nā waiwai o ka phenylalanine i ke koko o ka pēpē a e like me ke alakaʻi a ka pediatrician;
• E helu i ka nui o ka waiū hale kūʻai me ka ʻole o ka phenylalanine, e hoʻopau ai i ka hānai ʻana o ka pēpē;
• Me ka pauma, hemo i ka nui kūpono o ka waiū umauma i hiki i ka makuahine ke hāʻawi i ka pēpē;
• E hoʻohana i ka ʻōmole a i ʻole ʻano hana relactation e hānai i ka pēpē.

Pono pono e kāpae i ka amino acid phenylalanine mai ka meaʻai, i ʻole pilikia nā pēpē i ka hoʻomohala kino a me ka noʻonoʻo, e like me ka noʻonoʻo noʻonoʻo. E ʻike i ke ʻano o ka meaʻai ma phenylketonuria.

2. Hoʻohana o nā mea hoʻopihaʻai pono

E like me ka papaʻai ʻana o ke kanaka me ka phenylketonuria i kapu loa ʻia, hiki nō paha ke loaʻa ʻole ka nui o nā wikamina a me nā minelala e pono ai no ka hana pono ʻana o ka meaola a no ka ulu kūpono o ke keiki. No laila, hiki i ka nutristist ke paipai i ka hoʻohana ʻana o nā mea hoʻopihapiha a me nā formulate nutritional e hōʻoia i ka ulu pono ʻana o ka pēpē a hoʻoikaika i kona olakino.

Hōʻike ʻia ke kumukanawai e ka nutristist e like me ka makahiki, ke kaumaha o ke kanaka a me ka hiki o ka digestion o ka pēpē, a pono e mālama ʻia i ke ola holoʻokoʻa.

Nā pilikia kūpono o phenylketonuria

Kū mai nā pilikia o ka phenylketonuria ke hana ʻole ʻia ke kuhi a i ʻole ke ukali ʻia ka mālama ʻana e like me nā kuhikuhi a ka pediatrician, me ka hōʻiliʻili o phenylalanine i loko o ke koko, i hiki i nā wahi kikoʻī o ka lolo a alakaʻi i ka ulu ʻana o nā loli mau, e like me e like me:

• Hoʻolālā i ka hoʻomohala psychomotor;
• Hoʻolālā lolo liʻiliʻi;
• Microcephaly;
• Hyperactivity;
• Nā pilikia pili i ke ʻano;
• Hoʻoemi IQ;
• Hemahema noʻonoʻo nui;
• Huikau;
• Nā haʻalulu.

I ka hala ʻana o ka manawa, inā ʻaʻole mālama pono ʻia ke keiki, loaʻa paha ka paʻakikī i ka noho ʻana a me ka hele wāwae ʻana, nā ʻano maʻi a me ka lohi o ka ʻōlelo a me ka hoʻomohala ʻana o ka ʻike, me ka kaumaha, epilepsy a me ataxia, ka nalowale ʻana o ka kaohi.

Pehea e hōʻalo ai

I mea e hōʻalo ai i nā pilikia, he mea nui ka hana ʻana o ka maʻi i nā lā mua ma hope o ka hānau ʻia ʻana o ke keiki ma o ka hoʻāʻo ʻana o ka kuʻekuʻe wāwae. Inā maikaʻi ka hopena, he mea nui e mālama ʻia ka mālama ʻana e like me ke alakaʻi a ka pediatrician.

Eia hou, i kēia mau hihia he mea nui ka lawe ʻia ʻana o nā hoʻokolokolo maʻamau e nānā i ke olakino olakino o ke keiki a, no laila, e hōʻike i nā loli i ka papaʻai a me nā mea hoʻopihapihaʻai.

Hana mau ʻia nā hoʻokolohua ukali i kēlā me kēia pule a hiki i ka huli ʻana o ka pēpē i ka makahiki 1. ʻO nā keiki ma waena o 2 a me 6 mau makahiki e hana hou i ka hōʻike i kēlā me kēia 15 mau lā, a, mai 7 mau makahiki, hana ʻia ka hōʻike ma hoʻokahi manawa i ka mahina.