ʻO ka anemia Sideroblastic: he aha ia, nā ʻōuli, nā kumu a me nā lāʻau

Anter

• Nā kumu kūpono
• Nā hōʻailona nui
• Pehea e hana ʻia ai ke kuhi
• Pehea e hana ai i ka lāʻau

Kuhi ʻia ka anemia Sideroblastic e ka hoʻohana kūpono ʻole o ka hao no ke synthesi o hemoglobin, ka mea e hōʻiliʻili i ka hao i loko o ka mitochondria o nā erythroblast, e hoʻoulu ana i nā sideroblast, i ʻike ʻia i ka nānā ʻana o ke koko ma lalo o ka microscope.

Hiki ke pili i kēia maʻi i nā kumu hoʻoilina, nā mea i loaʻa a i ʻole ma muli o myelodysplasias, e alakaʻi ana i ka hanana ʻana o nā hōʻailona o ke anemia, e like me ka luhi, pallor, dizziness a nāwaliwali.

Pili ka mālama ʻana i ka paʻakikī o ka maʻi, me ka acidic folic a me ka huaʻai B6 e lawelawe maʻamau ʻia a i nā hihia ʻoi aku ka paʻakikī, pono paha e hana i kahi iwi kuʻupuʻu iwi.

Nā kumu kūpono

Hiki i ka anemia Sideroblastic ke lilo i congenital, ʻo ia ka manawa i hānau ʻia ai ke kanaka me ka maʻi, a i ʻole loaʻa, kahi e kū ai nā sideroblast ma muli o kahi kūlana ʻē aʻe. I ke kumu o ka anemia sideroblastic hikiwawe, pili ia i ka loli moʻomeheu hoʻoilina, i hoʻopili ʻia me ka X chromosome, a ma muli o ka hoʻololi ʻana, paipai ia i nā loli i ka mitochondrial metabolism, e hopena ana i kēia ʻano anemia.

I ke kumu o ka loaʻa ʻana o ka anemia sideroblastic, ʻo ke kumu nui ka myelodysplastic Syndrome, i kūlike i kahi hui o nā maʻi kahi lawa ʻole o ka momona o ka iwi a me ka hopena i ka hana ʻana o nā hunaola kō ʻole. ʻO nā kumu kūpono ʻē aʻe o sideroblastic anemia:

• ʻAhaʻona lama mau;
• Rheumatoid arthritis;
• Hōʻike i nā toxins;
• Ka nele o ka wikamina B6 a i ʻole ke keleawe;
• Hoʻohana o kekahi mau lāʻau, e like me chloramphenicol a me isoniazid;
• Nā maʻi maʻi autoimmune.

Eia hou, hiki i kēia ʻano anemia ke hopena o nā loli pili i ke koko a me ka iwi o ka iwi, e like me myeloma, polycythemia, myelosclerosis a me leukemia.

Nā hōʻailona nui

ʻO nā ʻōuli o ka hapanui o nā hihia o ka heremiaary sideroblastic anemia i hōʻike ʻia i ka wā kamaliʻi, eia nō naʻe, aia kekahi mau hihia momona o ka anemia sideroblastic hereditary nona nā ʻōuli i ʻike wale ʻia i ka wā makua.

Ma ke ʻano laulā, like nā ʻōuli o ka anemia sideroblastic me nā anemia maʻamau, kahi e ʻike ai ke kanaka i ka luhi, hoʻemi i ka hiki ke hana i nā hana kino, dizziness, nāwaliwali, tachycardia a me pallor, a ʻoi aku ka maʻalahi o ke kahe ʻana a me ka maʻi.

E ʻike ai i ka makaʻu o ka loaʻa ʻana o ka anemia, koho i nā ʻōuli āu e ʻike nei ma lalo nei:

1. 1. Ka nele o ka ikaika a me ka luhi nui loa
2. 2. ʻili pale
3. 3. Ka nele o ka makemake a me ka haʻahaʻa hana
4. 4. Ka maʻi poʻo mau
5. 5. Hoʻonāukiuki maʻalahi
6. 6. Koi ʻole hiki ʻole ke wehewehe ʻia e ʻai i kahi mea ʻē e like me ka pōhaku lepo a lepo paha
7. 7. Ka nalowale o ka hoʻomanaʻo a paʻakikī paha i ka noʻonoʻo ʻana

Pehea e hana ʻia ai ke kuhi

ʻO ke kuhi o ka anemia sideroblastic e hana ʻia e ka hematologist a i ʻole ka mea hana maʻamau e ka loiloi ʻana i nā hōʻailona a me nā ʻōuli i hōʻike ʻia e ka hiki a me ka hana ʻana i kahi helu o ke koko e hiki ai ke nānā i nā erythrocytes me nā ʻano like ʻole a ʻike ʻia paha kekahi o lākou e kiko. Hoʻohui ʻia, hana pū ʻia nā helu retikulosit, he mau kōkoko ʻulaʻula makua ʻole ia, i kū maʻa mau i kēia ʻano anemia.

ʻO ke ana o ka hao, ferritin a me transferrin saturation hōʻike ʻia e ke kauka, no ka mea hiki ke hoʻololi ʻia i ka anemia sideroblastic. I kekahi mau hihia, hiki i ke kauka ke koi aku e hana i kahi hoʻokolohua e loiloi i ka iwi iwi, ʻoiai ma ke ʻano he kōkua i ka hōʻoia ʻana i ka anemia sideroblastic, kōkua pū ia e ʻike i ke kumu o ka loli.

Pehea e hana ai i ka lāʻau

Pono e hana i ka hoʻomaʻamaʻa no ka anemia sideroblastic e like me ka hōʻike a ke kauka a me ke kumu o ka anemia, a e hōʻike ʻia paha ka supplementation me ka huaola B6 a me ka folic acid, me ka hoʻoliʻiliʻi o ka inu ʻana i nā mea inu ʻona. Inā loaʻa ka anemia ma muli o ka hoʻohana ʻana o nā lāʻau, hiki ke hōʻike ʻia ke kāpae ʻana o kāna hoʻohana.

I nā hihia koʻikoʻi loa, kahi hopena o ka anemia kahi hopena o nā loli i ka hana ʻana o ka iwi iwi, hōʻike ʻia ke transplantation e ke kauka. Hoʻomaopopo i ka hana ʻia ʻana o ka iwi iwi.