Aplastic anemia: he aha ia, nā hōʻailona nui a me ka mālama ʻana

Anter
ʻO ka anemia anplastic kahi ʻano o ka iwi iwi a, a no laila, maʻi maʻi koko, ʻike ʻia e ka hoʻemi ʻana o ka nui o nā hunaola ʻulaʻula, nā leukosit a me nā platelet e hoʻopuni nei, e hōʻike ana i ke ʻano o ka pancytopenia. Hiki ke loaʻa kēia kūlana mai ka hānau ʻana a i loaʻa paha i ka manawa, a ma muli paha o ka hoʻohana ʻia ʻana o kekahi mau lāʻau a i ʻole ka hoʻopili pinepine ʻana me nā mea kemika, no ka laʻana.
Ma muli o ka hiki ʻole i ka iwi o ka iwi ke hana i nā keena o ke koko a i nā nui kūpono, hoʻomaka nā hōʻailona a me nā ʻōuli o kēia ʻano anemia, e like me ka pale, ka luhi nui, nā maʻi pinepine a me nā hiʻohiʻona poni ma ka ʻili. me ke kumu ole.

Nā ʻōuli o ka anemia aplastic
Kū aʻe nā ʻōuli a me nā hōʻailona o ka anemia aplastic ma muli o ka emi o ka nui o nā kahe o ke koko e kahe ana, nā mea nui:
- Pallor i ka ʻili a me nā membrane mucous;
- Nā hihia o nā maʻi i hoʻokahi makahiki;
- Nā māka poni ma ka ʻili me ke kumu ʻole;
- Nā hemorrhages nui a i nā ʻoki liʻiliʻi;
- Luhi,
- Ka pōkole o ka hanu;
- Kāleka Kāleka;
- Hemorrhage i loko o ka gums;
- Puʻupuʻu;
- ʻEha poʻo poʻo;
- Pāwī i ka ʻili.
Hoʻohui ʻia, i kekahi mau hihia aia kekahi mau loli paha i nā puʻupaʻa a me nā wahi urinary, ʻoi aku ka pinepine o kēia mau loli i ka hihia o Fanconi anemia, kahi ʻano o ka congenital aplastic anemia. E aʻo hou aʻe e pili ana i ka anemia Fanconi.
Pehea e hana ʻia ai ke kuhi
Hoʻokumu ʻia ke kuhi o ka anemia aplastic ma muli o ke kālailai ʻana i nā hoʻokolohua hoʻokolohua, ʻo ka nui hoʻi o ka helu o ke koko, e hōʻike ana i ka haʻahaʻa ma mua o ka nui o nā hunaola ʻulaʻula, nā leukosit a me nā platelet
No ka hōʻoia ʻana i ke kuhi, noi pinepine ke kauka e hana i ka myelogram, ka mea e manaʻo ai e loiloi pehea ka hana ʻana o ka cell e ka iwi o ka iwi, a ʻo ka biopsy iwi pū kekahi. Hoʻomaopopo i ke ʻano o ka biopsy o ka iwi iwi a pehea e hana ai.
I kekahi mau hihia, keu hoʻi ke loaʻa ʻia ka anemia aplastic he congenital, hiki i ke kauka ke noi i nā hoʻokolohua kiʻi e loiloi i ka urinary tract a me nā puʻupaʻa, a me nā hoʻokolohua hoʻokolohua e loiloi i kēia ʻōnaehana, e like me ka urea a me ka creatinine, no ka laʻana.
Nā kumu nui
ʻO ka loli i ka iwi o ka iwi e hiki ai i ka anemia aplastic hiki ke hānau a loaʻa paha. I ka anemia aplastic congenital, hānau ke keiki me kēia hoʻololi, hoʻomohala i nā hōʻailona i nā makahiki mua o ke ola.
Ma ka ʻaoʻao ʻē aʻe, ulu aʻe ka anemia aplastic ma mua o ka manawa, a pili paha i ka hoʻohana ʻana i nā lāʻau, no ka hopena o nā maʻi autoimmune a i ʻole nā maʻi viral, a ma muli paha o ka hōʻike pinepine ʻia i kekahi mau mea ʻona, nā bismuth nui, nā pesticides. , insecticides, chloramphenicol, nā paʻakai gula a me nā huahana ʻaila.
Hoʻomaʻo no ka anemia aplastic
ʻO ka mālama ʻana no ka anemia aplastic ka mea e hōʻoluʻolu ai i nā ʻōuli a hoʻoulu i ka iwi o ka iwi e hana i nā kahe o ke koko i hiki ke hana i kā lākou hana.
No laila, hiki ke noi ʻia i ke kahe o ke koko, ka mea ma muli o ka lawe ʻia ʻana o nā hunaola ʻulaʻula a me nā platelet, ʻo ka mea nui, hiki ke hoʻokuʻu i nā ʻōuli, ʻoiai e nui ana ka nui o ka oxygen e lawe ʻia e nā hunaola. Eia kekahi, ʻo ka hoʻohana ʻana i nā lāʻau ʻalopiko i ke aa koko e kōkua i ka hoʻoikaika ʻana i ka ʻōnaehana pale, e kōkua ana i ke kaua ʻana i nā maʻi.
ʻO ka hoʻohana ʻana i nā lāʻau e kōkua i ka hoʻoulu ʻana i ka hana o ka iwi iwi a me nā lāʻau immunosuppressive, e like me Methylprednisolone, Cyclosporine a me Prednisone.
I loko nō o kēia mau mālama ʻana, ʻo ka mea pono e hoʻōla i ka anemia aplastic ka hoʻoneʻe iwi iwi, kahi e loaʻa ai i ke kanaka ka iwi iwi e hana pono ana, e paipai ana i ke kūkulu ʻia ʻana o nā hunaola i nā nui kūpono. Hoʻomaopopo i ke kuʻi ʻana o ka iwi iwi a pehea e hana ai.