Pukaaniani Aortopulmonary

ʻO ka puka aniani ʻo Aortopulmonary kahi kīnā o ka puʻuwai i ʻike ʻia kahi puka e pili ana i ke aʻa nui e lawe ana i ke koko mai ka puʻuwai i ke kino (aorta) a me ka mea e lawe ana i ke koko mai ka puʻuwai i nā akemāmā (arter pulmonary artery). ʻO ke ʻano he congenital, ʻo ia hoʻi aia ia ma ka wā hānau.

ʻO ka maʻamau, kahe ke koko ma o ka aʻa o ka pulmonary i loko o nā akemāmā, kahi e huki ai ia i ka oxygen. A laila hoʻi hou ke koko i ka puʻuwai a huki ʻia i ka aorta a me ke koena o ke kino.

He puka ko nā pēpē me ka puka aniani aortopulmonary ma waena o ka aorta a me ke aʻa aʻa. Ma muli o kēia lua, kahe ke koko mai ka aorta i loko o ke aʻa o ka pulmonary, a ma muli o ka hopena e kahe nui ke koko i nā akemāmā. ʻO kēia ke kumu o ke kiʻekiʻe o ke koko i loko o nā akemā (kahi ʻano i kapa ʻia he pulmonary hypertension) a me ka puʻuwai puʻuwai. ʻO ka nui o ka kīnā, ʻo ka nui o ke koko i hiki ke komo i ke aʻa o ka pulmonary.

Kū ke ʻano i ka wā ʻaʻole hoʻokaʻawale maʻamau ke aorta a me ka aʻa pulmonary i ka ulu ʻana o ka pēpē i loko o ka ʻōpū.

Kākaʻikahi loa ka puka aniani o Aortopulmonary. Loaʻa ia ma lalo o 1% o nā kīnā o ka naʻau hānau āpau.

Hiki i kēia ʻano ke hana i kāna iho a i ʻole me nā kīnā o ka naʻau e like me:

• ʻO Tetralogy o Fallot
• Pulseary atresia
• Truncus arteriosus
• Hewa septal Atrial
• Patent ductus arteriosus
• ʻAukā aorta ʻoki

Kanekau pākēneka o ka poʻe maʻa mau i nā kīnā ʻole o ka puʻuwai.

Inā liʻiliʻi ka hemahema, ʻaʻole ia e hoʻokumu i kekahi ʻōuli. Eia nō naʻe, nui ka hapa nui o nā kīnā.

Hiki i nā ʻōuli ke hoʻohui pū:

• Hoʻonui lohi
• Hewa puʻuwai
• Huhū
• ʻAi maikaʻi ʻole a me ka loaʻa ʻole o ke kaupaona
• Hanu wikiwiki
• Kuʻi puʻuwai wikiwiki
• Nā maʻi hanu

E lohe pinepine ka mea mālama ola i kahi kani naʻau maʻamau (ʻōhumu) ke hoʻolohe i ka puʻuwai o ke keiki me kahi stethoscope.

E kauoha paha ka mea hāʻawi i nā hoʻokolohua e like me:

• Catheterization Cardiac - he paipu lahilahi i hoʻokomo ʻia i loko o nā kīʻaha koko a me / a i ʻole nā ​​aʻa a puni ka puʻuwai e ʻike i ka puʻuwai a me nā kīʻaha koko a ana pono i ka kaomi i ka puʻuwai a me nā akemāmā.
• Pākuʻi x-ray.
• ʻEchocardiogram.
• MRI o ka puʻuwai.

Koi pinepine ke ʻano i ka ʻoki puʻuwai puʻuwai e hoʻoponopono i ka kīnā. Pono e hana i kahi ʻokiʻoki i ka manawa hiki ke hiki ke hana ma hope o ke kuhi ʻana. I ka hapanui o nā hihia, ʻo kēia ke hānau hou o ke keiki.

Ma ke kaʻina hana, lawe ka mīkini puʻuwai-puʻuwai no ka puʻuwai o ke keiki. Wehe ke kauka i ke aorta a pani i ka hemahema me kahi pā i hana ʻia mai kekahi ʻāpana o ka ʻeke e hoʻopili i ka puʻuwai (ka pericardium) a i ʻole kahi mea i hana ʻia e ke kanaka.

Kūleʻa ke kaha ʻoki ʻana i ka puka aniani aortopulmonary i ka hapanui o nā hihia. Inā mālama koke ʻia ka hemahema, ʻaʻole pono nā keiki i nā hopena mau loa.

Hiki i ka hoʻopaneʻe ʻana i ka lāʻau ke alakaʻi i nā pilikia e like me:

• Hoka puʻuwai Congestive
• Pulmonary hypertension a i ʻole Eisenmenger maʻi maʻi
• Make

Kāhea i kāu mea hāʻawi inā loaʻa kāu keiki i nā ʻōuli o ka pukaaniani aortopulmonary. ʻO ka loaʻa koke o kēia maʻi i kahi maʻi a mālama ʻia, ʻoi aku ka maikaʻi o ka wānana a ke keiki.

ʻAʻohe ala i ʻike ʻia e pale aku ai i ka puka aniani aortopulmonary.

Hewa septal Aortopulmonary; Fenestration Aortopulmonary; Hōʻino puʻuwai Congenital - puka aniani aortopulmonary; Hema kīnā hānau - window window aortopulmonary

• Pukaaniani Aortopulmonary

Fraser CD, Kane LC. Maʻi maʻi ʻōpū. I: Townsend CM, Beauchamp RD, Evers BM, Mattox KL, eds. ʻO Sabiston Textbook of Surgery. 20 ouk. Piladelapia, PA: Elsevier; 2017: chap 58.

ʻO Qureshi AM, Gowda ST, Justino H, Spicer DE, Anderson RH. Nā hana ʻino ʻē aʻe o nā kahawai puka waho ventricular. I: Wernovsky G, Anderson RH, Kumar K, et al, eds. Ka Pediatric Cardiology o Anderson. ʻEhā ed. Piladelapia, PA: Elsevier; 2020: chap 51.

Webb GD, Smallhorn JF, Therrien J, Redington AN. ʻO ka maʻi puʻuwai Congenital i ke kanaka makua a me ka mea maʻi pediatric. I: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. ʻO ka maʻi puʻuwai ʻo Braunwald: He puke aʻo no ka lāʻau Cardiovascular. 11th hua. Piladelapia, PA: Elsevier; 2019: chap 75.