Mea Kākau: Marcus Baldwin
Lā O Ka Hana: 16 Iune 2021
HōʻAno Hou I Ka Lā: 1 Iulai 2024
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Captain Unikitty Legend Of 9 Tribes Movie
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ʻO ka mea hoʻowalewale IX kahi hoʻāʻo koko e ana i ka hana o ka helu IX. ʻO kēia kekahi o nā protein i ke kino e kōkua ai i ke kōʻē ʻana o ke koko.

Pono kahi laʻana koko.

Pono paha ʻoe e hōʻoki i ka lawe ʻana i kekahi lāʻau i mua o kēia hōʻike. E haʻi aku kāu mea mālama ola iā ʻoe nā mea hea.

Ke hoʻokomo ʻia ke kui kele e huki i ke koko, manaʻo kekahi poʻe i ka ʻeha kaulike. ʻIke wale kekahi i kahi ʻōniʻu a i ʻole kui. Ma hope, loaʻa paha i kahi kūpikipiki a i ʻole ʻeha iki. Hele koke kēia.

Hoʻohana ʻia kēia hoʻokolohua e ʻike i ke kumu o ke kahe ʻana o ka nui o ka toto (hoʻoliʻiliʻi ke kāpili ʻana o ke koko). A i ʻole, kauoha ʻia paha inā ʻike ʻia kekahi lālā o ka ʻohana he hemophilia B. Hana ʻia paha ka hōʻike e ʻike ai i ka maikaʻi o ka mālama ʻana no ka hemophilia B.

ʻO 50% ka waiwai maʻamau i ka 200% o ka kaena keʻena hoʻokolohua a i ʻole ka helu kuhikuhi.

Hiki ke loli iki nā pae waiwai maʻamau i waena o nā hale hana ʻokoʻa. Hoʻohana kekahi mau labs i nā ana like ʻole a i ʻole hoʻokolohua i nā laʻana like ʻole. E kamaʻilio i kāu mea hāʻawi e pili ana i ke ʻano o kāu mau hopena hōʻike.


Hōʻike nā hiʻohiʻona ma luna i nā ana maʻamau no nā hopena no kēia mau hoʻāʻo.

Pili paha ka hana no ka hopena IX i:

  • Hemophilia B (kahi maʻi kahe o ke kahe e pili ana i ka nele o ke kaʻi ʻana o ke koko IX)
  • ʻO ka maʻi kahi e mālama ai nā protein i ka hoʻopili ʻia ʻana o ke koko ma luna o kahi hana (hoʻolaha ʻia i ka coagulation intravascular)
  • Malabsorption momona (ʻaʻole e omo i ka momona mai kāu papaʻai)
  • ʻO ka maʻi ate (e like me cirrhosis)
  • Ka hemahema o ka wikamina K
  • Lawe i ka lahilahi koko

ʻAʻohe pilikia iki i ka lawe ʻia ʻana o kou koko. ʻOkoʻa nā aʻa a me nā aʻa i ka nui mai kekahi kanaka a i kekahi, a mai kekahi ʻaoʻao o ke kino i kekahi ʻē aʻe. ʻOi aku ka paʻakikī o ka loaʻa ʻana o kahi laʻana koko mai kekahi poʻe ma mua o nā poʻe ʻē aʻe.

ʻO nā pilikia ʻē aʻe e pili ana i ke kau ʻana o ke koko he liʻiliʻi, akā hiki ke hoʻopili ʻia:

  • Kahe nui ke koko
  • Pāleʻale a ʻoluʻolu paha
  • Nā punctures he nui e ʻimi i nā uaua
  • Hematoma (hōʻiliʻili koko ma lalo o ka ʻili)
  • Maʻiʻaʻai (i iki kamepiula i kēlā me kēia manawa ka ʻili i haki)

Hana pinepine ʻia kēia hōʻike i ka poʻe i loaʻa i nā pilikia kahe. ʻOi aku ka makaʻu o ke kahe nui ʻana ma mua o ka poʻe me ka pilikia ʻole o ke kahe.


ʻIke Kalikimaka hoʻāʻo; ʻO ke kumu serum IX; Mea Hemophilic B; Pākuʻi thromboplastin Plasma; PTC

Carcao M, Moorehead P, Lillicrap D. Hemophilia A a me B. In: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Nā Kumumanaʻo a me ka Hoʻomeheu. ʻEpekema 7 Piladelapia, PA: Elsevier; 2018: chap 135.

Chernecky CC, Berger BJ. ʻOihana IX (mea Kalikimaka, hemophilic factor B, plasma thromboplastin mea, PTC) - koko. I: Chernecky CC, Berger BJ, hua. Nā Hoʻokolohua Laboratory a me nā kaʻina hana Diagnostic. ʻElua huaʻōlelo St Louis, MO: Elsevier Saunders; 2013: 505-506.

Pai M. Keʻena hoʻokolohua loiloi o nā hemostatic a me nā thrombotic maʻi. I: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Nā Kumumanaʻo a me ka Hoʻomeheu. ʻEpekema 7 Piladelapia, PA: Elsevier; 2018: chap 129.

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