Pōʻalima Urticaria

ʻO ka Urticaria pigmentosa kahi maʻi maʻi e hana i nā pā o ka ʻili ʻeleʻele a me ka ʻinoʻino ʻino loa. Hiki i nā Hives ke ulu i ka wā e ʻānai ʻia ai kēia mau ʻili.

Hana ʻia ka urticaria pigmentosa ke nui a hewahewa nā hunaola (mast cells) i ka ʻili. ʻO nā pūnaewele mast nā pūnaewele pale pale e kōkua i ke kino e hakakā i nā maʻi. Hana a hoʻokuʻu i nā pūnaewele paʻa i ka histamine, kahi e kumu ai nā mākū e lilo i pehu a wela.

Nā mea i hiki ke hoʻoulu i ka hoʻokuʻu histamine a me nā ʻōuli o ka ʻili e pili pū me:

• ʻĀnai ʻana i ka ʻili
• Nā maʻi ʻino
• Hoʻoikaika kino
• Ke inu nei i nā wai wela, ʻai i nā meaʻai nīoi
• Puka lā, kū i ke anu
• Nā lāʻau, e like me ka aspirin a i ʻole nā ​​NSAID ʻē aʻe, codeine, morphine, kala x-ray, kekahi mau lāʻau anesthesia, ʻalekohola

ʻO ka urticaria pigmentosa ka mea maʻamau i nā keiki. Hiki iā ia ke hana i nā mākua.

ʻO ka hōʻailona nui he mau ʻāpana brownish i ka ʻili. Loaʻa i kēia mau pākuʻi nā hunaola i kapa ʻia nā mastocytes. Ke hoʻokuʻu ka mastocytes i ka histamine kemika, ulu nā pākuʻi i nā puʻupuʻu like me ka hive. Hiki i nā keiki ʻōpio ke hoʻomohala i kahi pehu i piha i ka wai inā ʻalalā ka puʻupuʻu.

E ʻulaʻula paha ka maka.

I nā hihia koʻikoʻi, hiki mai kēia mau ʻōuli:

• Pohā
• Fainting (ʻike ʻole ʻia)
• ʻEha poʻo
• Wheeze
• Kuʻi puʻuwai wikiwiki

E nānā ka mea mālama ola i ka ʻili. Manaʻo paha ka mea hāʻawi i ka pigmentosa urticarial ke ʻānai ʻia nā ʻili a hoʻāla ʻia nā puʻupuʻu (hives). Kapa ʻia kēia ka inoa ʻo Darier.

ʻO nā hoʻāʻo e nānā no kēia ʻano:

• ʻO ka biopsy ʻili e nānā no kahi kiʻekiʻe o nā hunaola mast
• Uramine histamine
• ʻO nā hoʻokolohua koko no nā helu o ke koko a me nā pae tryptase koko (ʻo ka tryptase kahi enzyme i loaʻa i nā cell mast)

Hiki i nā lāʻau Antihistamine ke kōkua i ka hoʻopakele ʻana i nā ʻōuli e like me ka ʻili a me ka holoi ʻana. E kamaʻilio i kāu mea hāʻawi e pili ana i kahi ʻano antihistamine e hoʻohana ai. Hoʻohana ʻia ʻo Corticosteroids ma ka ʻili a me ka light therapy i kekahi mau hihia.

Kauoha paha kāu mea hāʻawi i nā ʻano lāʻau ʻē aʻe e mālama i nā ʻōuli o nā ʻano ʻeha a ʻano ʻē o ka urticaria pigmentosa.

Hele ʻo Urticaria pigmentosa i ka wā ʻōpio ma kahi o hoʻokahi hapalua o nā keiki i hoʻopilikia ʻia. ʻOi aku ka maikaʻi o nā ʻōuli ma nā poʻe ʻē aʻe ke ulu a makua.

I nā mākua, hiki i ka urticaria pigmentosa ke alakaʻi i ka mastocytosis ʻōnaehana. He kūlana koʻikoʻi kēia e hiki ke hoʻopili i nā iwi, ka lolo, nā aʻalolo, a me ka ʻōnaehana digestive.

ʻO nā pilikia nui ka ʻoluʻolu ʻole mai ka makaʻu a me ka hopohopo e pili ana i nā hiʻohiʻona o nā kiko. Kākaʻikahi nā pilikia ʻē aʻe e like me ka diarrhea a me ka maʻule.

Hiki i nā ʻūpala ke kumu i kahi hopena maʻi maikaʻi ʻole i ka poʻe me ka pigmentosa urticaria. E noi i kāu mea hāʻawi inā pono ʻoe e lawe i kahi pahu epinephrine e hoʻohana ai ke loaʻa ʻoe i ka nalo pi.

Kāhea i kāu mea hāʻawi inā ʻike ʻoe i nā ʻōuli o ka urticaria pigmentosa.

Mastocytosis; Mastocytoma

• ʻO ka pigticosa urticaria i ka ʻāpana lima
• Mastocytosis - diffuse cutaneous
• ʻO Urticaria pigmentosa ma ka umauma
• ʻO ka pigtosa urticaria - keu

ʻO Chapman MS. Urticaria. I: Habif TP, Dinulos JGH, Chapman MS, Zug KA, eds. ʻO ka maʻi ʻili: Diagnosis and Treat. ʻEhā ed. Piladelapia, PA: Elsevier; 2018: chap 3.

ʻO Chen D, ʻo George TI. Mastocytosis. I: Hsi ED, ed. Hematopathology. ʻEkolu huaʻōlelo. Piladelapia, PA: Elsevier; 2018: chap 20.

Paige DG, Wakelin SH. Maʻi maʻi ʻili. I: Kumar P, Clark M, eds. ʻO Kauka Lapaʻau ʻo Kumar lāua ʻo Clarke. 9th ed. Piladelapia, PA: Elsevier; 2017: chap 31.