Syringomyelia

ʻO Syringomyelia kahi hōʻuluʻulu like o ka cerebrospinal fluid (CSF) e like me ka cyst e like me ka hopena o ka iwi āpau. I ka hala ʻana o ka manawa, hoʻopōʻino ia i ka iwi kuamoʻo.

Kāhea ʻia ka cyst piha piha i ka wai i kahi syrinx. Hiki ke hoʻokumu ʻia ka wai wai ʻōiwi e:

• Nā kīnā hānau (ʻo ia hoʻi ʻo Chiari malformation, kahi o ka lolo e pahu i lalo i ka iwi kuamoo ma ke kumu o ka iwi poʻo)
• ʻ .pala kuamoʻo spinal
• Nā Tumors o ka iwi kuamoʻo

Hoʻomaka ka hoʻomaka ʻana o ka cyst piha i ka wai i ka ʻāʻī o ka ʻāʻī. Hoʻonui mālie ia, kau i ke kaomi ma ka iwi kuamoʻo a hoʻolōʻihi i ka hōʻino.

ʻO ka hoʻomaka ʻana o syringomyelia ma waena o 25 a 40 mau makahiki. ʻOi aku ka hopena o nā kāne ma mua o nā wahine.

Inā pili ke ʻano i nā kīnā o ka hānau ʻana, ʻaʻohe paha hōʻailona a hiki i ka 30 a 40 mau makahiki. Hōʻike mālie nā ʻōuli o syringomyelia a ulu i nā makahiki he nui. I ke kumu o ka hōʻeha, hoʻomaka paha nā hōʻailona e like paha me 2 a 3 mau mahina o ka makahiki. Inā loaʻa nā ʻōuli, pili pū paha lākou:

• ʻEha poʻo
• Scoliosis (i nā keiki)
• ʻO ka nalowale o ka nui o nā mākala (ʻōpala, atrophy), pinepine i nā lima a me nā lima
• Loaʻa ka reflexes i nā lālā luna
• Hoʻonui i nā reflexes i nā lālā haʻahaʻa
• Spasms a paʻa paha i ka wāwae a i ʻole ka lima a me nā mākala lima
• Ka nalowale ʻana o ka mākala, ka nalowale o ka hiki ke hoʻohana i nā lima a i ʻole nā ​​wāwae
• Numbness e hoʻoliʻiliʻi i ka ʻeha a i ʻole ka mahana; hoʻohaʻahaʻa i ka hiki ke ʻike ke hoʻopā ʻia ka ʻili; aia i ka ʻāʻī, nā poʻohiwi, nā lima luna, a me ke kumu i kahi ʻano cape; a hele a mānoanoa i ka wā
• E hōʻeha i nā lima, ka ʻāʻī, a i ke kua waena a i ʻole nā ​​wāwae
• Nāwaliwali (hoʻemi i ka ikaika o ka mākala) i nā lima a i ʻole nā ​​wāwae
• Kuni ʻeha a ʻeha paha o ka lima
• Ke hele wāwae paʻakikī a me ka wāwae wāwae i nā keiki
• Nā neʻe ʻole e kaohi ʻia o nā maka (nystagmus)
• ʻO ke kūlana e hoʻopili i nā aʻa i ka maka a me ka maka (Horner Syndrome)

E hana ka mea mālama ola i kahi hoʻokolohua kino a nīnau e pili ana i nā ʻōuli, e kia ana i ka ʻōnaehana hopohopo. ʻO nā hoʻāʻo e hana ʻia ana paha:

• MRI o ke poʻo a me ka iwi kuamoʻo
• Spinal CT scan me ka myelogram (hiki ke hana ʻia ke hiki ʻole kahi MRI)

ʻAʻohe lāʻau lapaʻau maikaʻi e ʻike ʻia no syringomyelia. ʻO nā pahuhopu o ka mālama ʻana e hōʻoki i ka hōʻino o ke kuamoʻo mai ka ʻino a hoʻomaikaʻi i ka hana.

Pono paha ke kaha ʻana e hōʻoluʻolu i ke kaomi o ka iwi kuamoʻo. Pono paha ke olakino a me ka ʻoihana hana e hoʻomaikaʻi i ka hana muscle.

Hiki ke koi ʻia ʻo Ventriculoperitoneal shunting a i ʻole syringosubarachnoid shunting. ʻO ke kaʻina hana kēia e hoʻokomo ʻia ai kahi catheter (lahilahi, ʻōmole maʻalahi) i mea e hoʻokahe ai i ke kūkulu wai.

Me ka ʻole o ka lapaʻau ʻana, e hele mālie loa paha ka maʻi. I ka hala ʻana o ka manawa, he kumu ia no ke kīnā koʻikoʻi.

Kū ka hana ʻoki kino i ke kūlana mai ka ʻino loa ʻana. E hoʻomaikaʻi ka ʻōnaehana nervous ma kahi o 30% o ka poʻe i loaʻa i ka ʻoki kino.

Me ka mālama ʻole ʻia, hiki i ke ʻano ke alakaʻi i:

• Lilo o ka ʻōnaehana ʻōnaehana
• Kīnā paʻa paʻa

ʻO nā pilikia kūpono o ke kaha ʻana:

• Maʻi kīnā
• Nā pilikia ʻē aʻe o ke kaha ʻana

Kāhea i kāu mea hāʻawi inā loaʻa iā ʻoe nā ʻōuli o syringomyelia.

ʻAʻohe ala i ʻike ʻia e pale aku ai i kēia ʻano, ʻē aʻe ma mua o ka hōʻalo ʻana i nā hōʻeha i ka iwi kuamoʻo. ʻO ka mālama ʻana i kēia manawa e hoʻolohi i ka maʻi mai ka ʻino ʻana.

ʻO Syrinx

• ʻŌnaehana ʻōnaehana waena

Batzdorf U. Syringomyelia. I: Shen FH, Samartzis D, Fessler RG, nā hua. Puka puke o ka iwi kuamoʻo. Piladelapia, PA: Elsevier Saunders; 2015: chap 29.

Benglis DM, Jea A, Vanni S, Shah AH, Green BA. Syringomyelia. I: Garfin SR, Eismont FJ, Bell GR, Fischgrund JS, Bono CM, eds. ʻO Rothman-Simeone lāua ʻo Herkowitz's The Spine. ʻEpekema 7 Piladelapia, PA: Elsevier; 2018: chap 94.

Roguski M, Samdani AF, Hwang SW. ʻO syringomyelia makua. I: Winn HR, hoʻoponopono. ʻO Youmans a me Winn Neurological Surgery. ʻEpekema 7 Piladelapia, PA: Elsevier; 2017: chap 301.