Fibrous dysplasia

ʻO Fibrous dysplasia kahi maʻi iwi e hoʻopau a hoʻololi i ka iwi maʻamau me ka iwi fibrous. Hiki ke hoʻopili ʻia hoʻokahi a ʻoi paha mau iwi.

Hana pinepine ʻo Fibrous dysplasia i ka wā kamaliʻi. Loaʻa ka hapanui o ka poʻe i nā hōʻailona ma ka manawa o 30 mau makahiki. Kū pinepine ka maʻi i nā wahine.

Hoʻopili ʻia ʻo Fibrous dysplasia i kahi pilikia me nā genes (gen mutation) e kaohi i nā hunaola hana iwi. Hiki ke hoʻololi i ka wā e ulu ana kahi pēpē i loko o ka ʻōpū. ʻAʻole hoʻoholo ʻia kēia ʻano mai ka makua a ke keiki.

Pākuʻi ʻia paha nā ʻōuli i kekahi o kēia mau mea:

• ʻEha iwi
• ʻEha iwi (lesions)
• Nā pilikia gland Endocrine (hormone)
• Nā haki a me nā deformities iwi
• ʻO ke kala o ka ʻili maʻamau (pigmentation), e kū nei me ka maʻi ʻo McCune-Albright

E pau paha ka ʻino o nā iwi i ka wā ʻōpio o ke keiki.

E hana ka mea mālama ola i kahi hoʻokolokolo kino. Lawe ʻia nā kukuna X o nā iwi. Paipai ʻia kahi MRI.

ʻAʻohe mea ola no fibrous dysplasia. Mālama ʻia nā haʻi iwi a i ʻole deformities e pono ai. Pono e mālama ʻia nā pilikia Hormone.

Aia ka nānā i ka paʻakikī o ke ʻano a me nā ʻōuli e hana ʻia.

Kaukaʻi ʻia i nā iwi i hoʻopili ʻia, nā pilikia olakino e hopena ai paha:

• Inā pili ka iwi iwi poʻo, hiki i ka hihi a me ka nalo ʻana o ka pepeiao
• Inā pili ka iwi iwi, hiki i ka paʻakikī ke hele a me nā pilikia hui e like me ka maʻi kō

Kāhea i kāu mea hāʻawi inā loaʻa kāu keiki i nā ʻōuli o kēia ʻano, e like me ka haʻi pinepine ʻana o ka iwi a me ka deformity iwi maopopo ʻole.

Hiki paha i nā loea i nā orthopedics, endocrinology, a me nā genetics ke hoʻopili i ka hōʻailona a me ka mālama ʻana o kāu keiki.

ʻAʻohe ala i ʻike ʻia e pale aku ai i fibplus displasia. Hoʻopaʻa ka mālama ʻana i mea e pale ai i nā pilikia, e like me ka haʻi pinepine ʻana o ka iwi, e kōkua i ka hōʻemi ʻana i ke ʻano.

ʻO hyperplasia fibrous hoʻoweliweli; Idiopathic fibrous hyperplasia; ʻO ka maʻi maʻi ʻo McCune-Albright

• Anatomy iwi mua

ʻO Czerniak B. Fibrous dysplasia a me nā leona pili. I: Czerniak B, ed. ʻO Tumf Bone ʻO Dorfman lāua ʻo Czerniak. ʻElua ed. Piladelapia, PA: Elsevier Saunders; 2016: chap 8.

Heck RK, Pāʻani PC. Nā kūpuna iwi Benign a me nā kūlana nonneoplastic e hoʻohālikelike i nā iwi iwi. I: Azar FM, Beaty JH, Canale ST, hua. ʻO Campbell's Operative Orthopedics. 13th ed. Piladelapia, PA: Elsevier; 2017: chap 25.

ʻO Merchant SN, Nadol JB. Hōʻike Otologic o ka maʻi ʻōnaehana. I: Flint PW, Haughey BH, Lund V, et al, eds. Cummings Otolaryngology: Ke poʻo poʻo a me ka ʻāʻī. ʻElua huaʻōlelo Piladelapia, PA: Elsevier Saunders; 2015: chap 149.

ʻO Shiflett JM, Perez AJ, makua AD. Nā maʻi poʻo o ke poʻo i nā keiki: dermoids, langerhans cell histiocytosis, fibrous dysplasia, a me lipomas. I: Winn HR, hoʻoponopono. ʻO Youmans a me Winn Neurological Surgery. ʻEpekema 7 Piladelapia, PA: Elsevier; 2017: chap 219.