Optic glioma

ʻO nā gliomas nā tumors e ulu ana ma nā wahi like ʻole o ka lolo. Hiki i nā gliomas optic ke hoʻopili:

• Hoʻokahi a i ʻole ʻelua o nā aʻalolo optic e lawe i ka ʻike ʻike i ka lolo mai kēlā me kēia maka
• ʻO ka chiasm optic, kahi e hele ai nā ʻalolo optic i kekahi i mua o ka hypothalamus o ka lolo.

E ulu pū kekahi glioma optic me kahi glioma hypothalamic.

Kākaʻikahi nā gliomas optic. ʻAʻole ʻike ʻia ke kumu o optic gliomas. ʻO ka hapanui o nā gliomas optic e ulu lohi a noncancerous (benign) a kū i nā keiki, kokoke mau ma mua o ka makahiki 20. ʻO ka hapa nui o nā hihia ʻike ʻia e 5 mau makahiki.

Aia kahi hui ikaika ma waena o optic glioma a me neurofibromatosis ʻano 1 (NF1).

Pili nā ʻōuli i ka ulu ʻana o ka tumo a kaomi ʻana i ke aʻalolo optic a me nā hale kokoke. Pākuʻi ʻia paha nā ʻōuli:

• Neʻe kinipōpō hana ʻaʻano
• Kūwaho o waho o kekahi o nā maka ʻelua paha
• ʻIntingmiʻa
• ʻO ka nalo ʻana o ka hihiʻo i hoʻokahi a i ʻole ʻelua mau maka e hoʻomaka me ka nalo ʻana o ka hihi ākea a i hope e alakaʻi i ka makapō

Hōʻike paha ke keiki i nā ʻōuli o ka maʻi diencephalic, e hoʻopili pū ana me:

• E hiamoe ana i ke ao
• Hoʻoemi i ka hoʻomanaʻo a me ka hana o ka lolo
• Poʻo poʻo poʻo
• Hoʻonui lohi
• Lilo ka momona o ke kino
• ʻO ka luaʻi

Hōʻike kahi lolo a me ka ʻōnaehana ʻōnaehana (neurologic) i ka nalo ʻana o ka hihiʻo i hoʻokahi a i ʻole ʻelua mau maka. Hiki paha i nā hoʻololi i ke aʻalolo optic, e like me ka pehu ʻana a i ʻole ka ʻūlū ʻana o ke aʻalolo, a i ʻole ke keʻokeʻo a me ka hōʻino ʻana i ka disk optic.

Hiki ke hoʻonui i ka tumo i nā ʻāpana hohonu o ka lolo. Aia paha he mau hōʻailona o ka hoʻonui ʻia o ke kaomi i ka lolo (kaomi intracranial). Aia paha he mau hōʻailona o ka neurofibromatosis ʻano 1 (NF1).

E hana ʻia paha kēia mau hoʻāʻo:

• Cerebral angiography
• Wehe ʻia ka nīnaninau o nā maʻi mai ka tumo i ka wā o ke ʻoki a biopsy alakaʻi ʻia e CT scan e hōʻoia i ke ʻano tumo
• Head CT scan a i ʻole MRI o ke poʻo
• Nā hoʻāʻo kahua ʻike maka

Hoʻololi ka lāʻau lapaʻau me ka nui o ka tumo a me ke olakino olakino o ke kanaka. ʻO ka pahuhopu paha e hoʻōla i ka maʻi, hōʻoluʻolu i nā ʻōuli, a i ʻole hoʻomaikaʻi i ka ʻike a me ka hōʻoluʻolu.

ʻO ke ʻoki ʻana e hemo i ka puʻupuʻu e hoʻōla paha i kekahi gliomas optic. Hiki ke hana i ka hoʻoneʻe hapa ʻana e hōʻemi i ka nui o ka tumo i nā manawa he nui. Mālama kēia i ka tumelo mai ka hōʻino ʻana i nā kiko o ka lolo āpau a puni ia. Ke hoʻohana ʻia nei ʻo Chemotherapy i kekahi mau keiki. He mea maikaʻi paha ka Chemotherapy ke hoʻonui ʻia ka tumo i loko o ka hypothalamus a i ʻole inā ua hoʻomāhuahua ʻia ka hihi e ka ulu ʻana o ka tumo.

Hiki ke koi ʻia ka radiation radiation i kekahi mau hihia ke ulu nei ka tumo ʻoiai ʻo chemotherapy, a ʻaʻole hiki ke ʻoki. I kekahi mau hihia, lohi paha ka radiation radiation no ka mea lohi ka ulu ʻana o ka tumo. ʻAʻole loaʻa nā keiki me ka NF1 i ka radiation ma muli o nā hopena ʻaoʻao.

Kau ʻia nā Corticosteroids e hōʻemi i ka pehu a me ka mumū i ka wā o ka radiation radiation, a i ʻole inā hoʻi nā hōʻailona.

ʻO nā hui e hāʻawi i ke kākoʻo a me nā ʻike hou aʻe:

• Pūʻulu Oncology Children - www.childrensoncologygroup.org
• Pūnaewele Neurofibromatosis - www.nfnetwork.org

He ʻokoʻa loa ka nānā aku i kēlā me kēia kanaka. Hoʻomaikaʻi ka hoʻomaʻamaʻa mua i ka manawa o kahi hopena maikaʻi. ʻO ka ukali mālama pono ʻana me kahi hui mālama ʻike me kēia ʻano tumo mea nui.

Ke nalowale ka hihi mai ka ulu ʻana o kahi tumic optic, ʻaʻole paha ia e hoʻi.

ʻO ka maʻamau, lohi loa ka ulu ʻana o ka tumo, a paʻa mau ke ʻano no nā wā lōʻihi. Eia nō naʻe, hiki ke hoʻomau i ka ulu ʻana o ka tumo, no laila pono ke kiaʻi pono ʻia.

Kāhea i kāu mea mālama ola no ka nalowale ʻana o ka hihiʻo, ka ʻehaʻeha ʻole o ka maka, a i ʻole nā ​​hōʻailona ʻē aʻe o kēia ʻano.

Kūkā ʻia paha ka ʻōlelo aʻoaʻo genetic no ka poʻe me NF1. Hiki i nā hoʻokolohua maka maka maʻamau ke ʻae i ka hōʻoia mua ʻana o kēia mau tumors ma mua o ke kumu o nā ʻōuli.

Glioma - optic; Optic nerve glioma; Astrositio pilocytic ʻōpio; Ka maʻi ʻaʻai lolo - optic glioma

• Neurofibromatosis I - foramen optic hoʻonui ʻia

ʻO Eberhart CG. Adnexa maka a me ka maka. I: Goldblum JR, Lamps LW, McKenney JK, Myers JL, eds. ʻO Rosai lāua ʻo Ackerman's Surgical Pathology. 11th hua. Piladelapia, PA: Elsevier; 2018: chap 45.

ʻO Goodden J, Mallucci C. Ala optic ala hypothalamic gliomas. I: Winn HR, hoʻoponopono. ʻO Youmans a me Winn Neurological Surgery. ʻEpekema 7 Piladelapia, PA: Elsevier; 2017: chap 207.

Olitsky SE, Marsh JD. Nā kūpono ʻole o ke aʻalolo optic. I: Kliegman RM, St Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. ʻO Puka Textbook of Pediatrics ʻo Nelson. 21st ed. Piladelapia, PA: Elsevier; 2020: chap 649.