Pemphigoid nui loa
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ʻO Bullous pemphigoid kahi maʻi ʻili i ʻike ʻia e nā palapū.
ʻO Bullous pemphigoid kahi maʻi autoimmune i kū i ka wā e hōʻeha a hōʻino ke kino o ke kino i nā kino o ke kino me ke kuhihewa. Kūlike, hoʻouka ka ʻōnaehana pale i nā protein i hoʻopili i ka papa luna o ka ʻili (epidermis) i ka papa o lalo o ka ʻili.
Kū pinepine kēia maʻi i nā poʻe ʻelemākule a laha ʻole i ka poʻe ʻōpio. Hele mai nā ʻōuli a hele hoʻi. Hele pinepine ke ʻano i loko o 5 mau makahiki.
ʻO ka hapa nui o ka poʻe me kēia maʻi he ʻeha ka ʻili a ʻeha paha. I ka hapanui o nā hihia, aia nā pūlehu, i kapa ʻia ʻo bullae.
- Aia nā pālū ma nā lima, nā wāwae, a ma waena paha o ke kino. I nā hihia kakaikahi, hiki i nā palapū ke hana i ka waha.
- Hiki paha i nā pā ke hāmama a hana i nā ʻeha hāmama (ulcer).
E nānā ka mea mālama ola i ka ʻili a nīnau e pili ana i nā ʻōuli.
Nā hoʻāʻo e hiki ke hana ʻia e kōkua i ke kuhi ʻana i kēia ʻano me:
- Nā hoʻāʻo koko
- ʻO ka biopsy o ka ʻili a i ʻole ka wahi e kokoke ana iā ia
Hiki ke kuhikuhi ʻia nā lāʻau anti-inflammatory i kapa ʻia ʻo corticosteroids. Lawe ʻia lākou i ka waha a noi ʻia i ka ʻili. Hiki ke hoʻohana ʻia nā lāʻau ʻoi aku ka ikaika e kāohi i ka ʻōnaehana pale inā ʻaʻole holo pono nā steroid, a i ʻole e ʻae i nā lāʻau steroid haʻahaʻa e hoʻohana.
He mea pono paha nā antibiotic i ka ʻohana tetracycline. Hāʻawi ʻia ʻo Niacin (kahi huaʻai B paʻakikī) i kekahi manawa me ka tetracycline.
Hōʻike paha kāu mea hāʻawi i nā hana mālama pilikino. Pākuʻi ʻia kēia mau mea:
- Ke noi nei i nā kalima anti-itch i ka ʻili
- Ke hoʻohana nei i nā kopa kuni a me ka hoʻopili ʻana i ka ʻili i ka ʻili ma hope o ka ʻauʻau ʻana
- Ka pale ʻana i ka ʻili i hoʻopili ʻia mai ka puka ʻana o ka lā a me ka hōʻeha
Pane maikaʻi ka pemphigoid Bullous i ka lāʻau. Hiki ke hoʻopau pinepine ʻia ka lāʻau ma hope o kekahi mau makahiki. Hoʻi ka maʻi i kekahi manawa ma hope o ka pau ʻana o ka lāʻau.
ʻO ka maʻi ʻili ka pilikia pinepine.
Hiki ke hana i nā pilikia ma muli o ka mālama ʻana, keu hoʻi mai ka lawe ʻana i nā corticosteroids.
Kāhea i kāu mea hāʻawi inā loaʻa iā ʻoe:
- Pāleʻa ʻole i wehewehe ʻia i kou ʻili
- Kahi huehue e hoʻomau me ka mālama ʻana i ka home
Pemphigoid Bullous - hoʻopau loa i nā palahū kūmau
ʻO Habif TP. Nā maʻi Vesicular a me bullous. I: Habif TP, hoʻoponopono. ʻO Dermatology Haumana: Kahi Alakaʻi Kānana i ka Diagnosis a me ka Therapy. ʻElua huaʻōlelo Piladelapia, PA: Elsevier; 2016: chap 16.
ʻO PeñaS, Werth VP. Pemphigoid nui loa. I: Lebwohl MG, Heymann WR, Berth-Jones J, Coulson IH, eds. Ka mālama ʻana i ka maʻi ʻili: nā ʻōnaehana Therapyutic Comprehensive. 5th lā. Piladelapia, PA: Elsevier; 2018: chap 33.