Nā hemahema o ka platelet Congenital

ʻO nā kīnā o ka platelet congenital kahi mau mea e pale ai i nā mea hoʻopili i ke koko, i kapa ʻia nā platelet, mai ka hana e like me ka mea e pono ai. Kōkua nā platelet i ka huehue koko. ʻO ke kumu o ka hānau ʻana mai ka wā hānau.

ʻO nā hemahema o ka platelet Congenital kahi maʻi koko e hōʻemi i ka hana platelet.

ʻO ka hapanui o nā manawa, loaʻa i ka poʻe me kēia mau maʻi he moʻolelo ʻohana o kahi maʻi koko, e like me:

• Hana ʻia ʻo Bernard-Soulier Syndrome ke nele ka platelets i kahi mea i pili i nā paia o nā kīʻaha koko. Nui a maʻalahi ka helu o nā peleti. Hiki i kēia maʻi ke kumu i ke kahe nui.
• ʻO Glanzmann thrombasthenia kahi kūlana i hoʻokumu ʻia e ka nele o kahi protein e pono ai no nā platelet e hui pū pū. ʻO nā pāpale he maʻamau o ka nui a me ka helu. Hiki i kēia maʻi ke kumu i ke kahe nui.
• ʻO ka maʻi ʻōpala e mālama ai (kahi i kapa ʻia ʻo ka maʻi huna platelet) ke hiki ke mālama ʻia a hoʻokuʻu ʻia paha nā mea i kapa ʻia he granules i loko o nā platelet. Kōkua nā Granula i nā platelet e hana kūpono. Mālama kēia maʻi i ka palapū a me ke kahe maʻalahi.

Pākuʻi ʻia paha nā ʻōuli i kekahi o kēia mau mea:

• Kahe nui ʻana o ke kahe i ka wā a ma hope o ke kaha ʻana
• Pepeiao koko
• ʻĀpiki maʻalahi
• Nā wā menstrual kaumaha
• Nā Nosebleeds
• ʻO ke kahe lōʻihi ʻana me nā ʻeha liʻiliʻi

Hiki ke hoʻohana ʻia nā hoʻokolohua aʻe e kuhikuhi ai i kēia ʻano:

• Helu piha koko (CBC)
• Wā thromboplastin manawa (PTT)
• Hōʻike hōʻuluʻulu platelet
• Ka manawa Prothrombin (PT)
• Nānā i ka hana platelet
• Kahe cytometry

Pono paha ʻoe i nā hoʻokolohua ʻē aʻe. Pono paha e hoʻāʻo ʻia kou mau hoahānau.

ʻAʻohe mālama kūikawā no kēia mau maʻi. Eia nō naʻe, e nānā paha kāu mea mālama ola i kāu ʻano.

Pono paha ʻoe:

• I mea e hōʻalo ai i ka lawe ʻana i ka aspirin a me nā lāʻau anti-inflammatory nonsteroidal ʻē aʻe (NSAIDs), e like me ka ibuprofen a me naproxen, no ka mea hiki iā lākou ke hōʻino i nā hōʻailona kahe.
• Hoʻohui platelet, e like me ke kaʻoki ʻana a me nā kaʻina hana niho.

ʻAʻohe mea ola no nā maʻi o ka platelet congenital. ʻO ka hapa nui o ka manawa, hiki i ka mālama ke kaohi i ke kahe ʻana o ke kahe.

Komo pū nā pilikia:

• Kahe nui ke koko
• ʻO ka anemia hemahema hao i nā wahine menstruating

Kāhea i kāu mea hāʻawi inā:

• He kahe kou a he ʻeha paha ʻoe a ʻaʻole ʻike i ke kumu.
• ʻAʻole pane ka Bleeding i ke ʻano maʻamau o ka kaohi.

Hiki i kahi hōʻoia koko ke ʻike i ka ʻāpana no ke kīnā hema. Makemake paha ʻoe e ʻimi i nā ʻōlelo aʻoaʻo kūlohelohe inā he moʻolelo ʻohana kāu no kēia pilikia a ke noʻonoʻo nei i ka loaʻa ʻana o nā keiki.

ʻO ka maʻi hōʻino wai puna; ʻO thrombasthenia o Glanzmann; Bernard-Soulier maʻi pale; Nā hemahema o ka platelet - hānau hānau

• Hoʻomaʻamaʻa koko
• Huʻi koko

ʻO Arnold DM, Zeller MP, Smith JW, Nazy I. Nā maʻi o ka helu platelet: immune thrombositopenia, neonatal alloimmune thrombositopenia, a me posturaansfusion purpura. I: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Nā Kumumanaʻo a me ka Hoʻomeheu. ʻEpekema 7 Piladelapia, PA: Elsevier; 2018: chap 131.

Halelu JE. Hemostasis a me ka coagulation koko. I: Hall JE, hoʻoponopono. ʻO Guyton a me Hall Textbook of Medical Physiology. 13th ed. Piladelapia, PA: Elsevier; 2016: chap 37.

ʻO Nichols WL. ʻO ka maʻi ʻo Von Willebrand a me nā hemorrhagic abnormalities o ka platelet a me ka vascular function. I: Goldman L, Schafer AI, eds. ʻO ka lāʻau lapaʻau Goldman-Cecil. 25th hua. Piladelapia, PA: Elsevier Saunders; 2016: chap 173.