ʻO Eosinophilic fasciitis

ʻO Eosinophilic fasciitis (EF) kahi maʻi maʻi ma lalo o ka ʻili a ma luna o ka ʻiʻo, i kapa ʻia ʻo fascia, lilo i pehu, pehu a mānoanoa. Hiki ke pehu ka ʻili ma nā lima, nā wāwae, ka ʻāʻī, ʻōpū a me nā wāwae. Kākaʻikahi loa ke kūlana.

E like paha ka like o EF me ka scleroderma, akā ʻaʻohe pili. ʻAʻole like me scleroderma, ma EF, ʻaʻole pili nā manamana lima.

ʻAʻole ʻike ʻia ke kumu o EF. Ua loaʻa nā hihia kakaikahi ma hope o ka lawe ʻana i nā kōkua L-tryptophan. I ka poʻe me kēia ʻano, kūkulu nā ʻulaʻula keʻokeʻo, i kapa ʻia ʻo eosinophils, i loko o nā mākala a me nā ʻaʻa. Hoʻopili ʻia ʻo Eosinophils i nā hopena maʻi ʻaʻai. ʻOi aku ka maʻamau o ka maʻi maʻi i nā poʻe mai 30 a 60 mau makahiki.

Pākuʻi ʻia paha nā ʻōuli:

• Ka palupalu a me ka pehu ʻana o ka ʻili ma nā lima, nā wāwae, a i ʻole kekahi manawa i nā ami (pinepine i nā ʻaoʻao ʻelua o ke kino)
• Pākuʻi
• Carpal tunnel maʻi maʻi
• ʻEha ʻeha
• ʻIli mānoanoa e nānā puckered

ʻO nā hoʻāʻo e hana ʻia ana paha:

• CBC me ka ʻokoʻa
• ʻO Gamma globulins (kahi ʻano protein immune system)
• Ka helu sedimentation ʻErythrocyte (ESR)
• MRI
• ʻO Biopsy Muscle
• ʻO ka biopsy ʻili (pono i ka biopsy e hoʻopili i nā aʻa hohonu o ka fascia)

Hoʻohana ʻia ʻo Corticosteroids a me nā lāʻau ʻino e pale ana i ka pale pale e hoʻōla i nā ʻōuli. ʻOi aku ka maikaʻi o kēia mau lāʻau i ka hoʻomaka mua ʻana i ka maʻi. Hiki ke kōkua i nā lāʻau anti-inflammatory Nonsteroidal (NSAIDs) e hōʻemi i nā ʻōuli.

I ka hapanui o nā hihia, hele ke ʻano i loko o 1 a 3 mau makahiki. Eia nō naʻe, lōʻihi a lōʻihi paha ka hoʻi ʻana o nā ʻōuli.

ʻO ka lohi o ka maʻi he maʻi paʻakikī o EF. Hiki i kekahi poʻe ke hoʻomohala i nā maʻi koko koʻikoʻi a i ʻole nā ​​maʻi maʻi pili koko, e like me ka anemia aplastic a i ʻole leukemia. ʻOi aku ka maikaʻi o ka nānā inā kū nā maʻi o ke koko.

Kāhea i kāu mea mālama ola inā loaʻa nā ʻōuli o kēia maʻi.

ʻAʻohe pale e ʻike ʻia.

ʻO Shulman Syndrome

• Nā mākala mua ma mua

Aronson JK. ʻO Tropophan I: Aronson JK, hoʻoponopono. Nā hopena a Meyler o nā lāʻau. 16th ed. Waltham, MA: Elsevier B.V.; 2016: 220-221.

James WD, Elston DM, Hana iā JR, Rosenbach MA, Neuhaus IM. Nā maʻi palahalaha hoʻohui. I: James WD, Elston DM, mālama iā JR, Rosenbach MA, Neuhaus IM, eds. Nā maʻi o Andrews 'o ka ʻili: Dermatology Haumāna. 13th ed. Piladelapia, PA: Elsevier; 2020: chap 8.

Lee LA, Werth VP. Nā maʻi ʻili a me ka rumatika. I: Firestein GS, Budd RC, Gabriel SE, McInnes IB, O'Dell JR, nā hua. ʻO Kelley lāua ʻo Firestein's Bookbook of Rheumatology. 10 o ka lā. Piladelapia, PA: Elsevier; 2017: chap 43.

Pinal-Fernandez I, Selva-O 'Callaghan A, Grau JM. ʻIke a me ka hoʻonohonoho ʻana o fosciitis eosinophilic. ʻO Autoimmun Rev.. 2014; 13 (4-5): 379-382. PMID: 24424187 www.ncbi.nlm.nih.gov/pubmed/24424187.

ʻO ka hui aupuni no nā maʻi kakaikahi. ʻO Eosinophilic fasciitis. rarediseases.org/rare-diseases/eosinophilic-fasciitis/. Hoʻohou 2016. Loaʻa iā Malaki 6, 2017.