ʻO ka maʻi veno-occlusive pulmonary

ʻO ka maʻi pulmonary veno-occlusive maʻi (PVOD) kahi maʻi ʻano nui loa. Alakaʻi ia i ke kiʻekiʻe o ke koko i nā aʻa o ke akemā (hypertension pulmonary).

I ka hapanui o nā hihia, ʻike ʻole ʻia ke kumu o ka PVOD. Loaʻa ke kiʻekiʻe o ke koko i loko o nā aʻa pulmonary. Pili pono kēia mau aʻa māmā i ka ʻaoʻao ʻākau o ka puʻuwai.

Pili paha ke ʻano i kahi maʻi viral. Hiki ke hana ʻia ma ke ʻano he pilikia o kekahi mau maʻi e like me ka lupus, a i ʻole ke kuʻi iwi o ka iwi.

ʻO ka maʻi maʻamau i waena o nā keiki a me nā ʻōpio makua. Ke hele a māhuahua ka maʻi, kumu ia:

• Pēpē puʻupuʻu paʻa
• ʻO ke kiʻekiʻe o ke aʻa aʻa
• ʻO ke kūpikipiki a me ka pehu ʻana o ka hanu

ʻO nā kumuhana kūpono no ka PVOD me:

• Mōʻaukala ʻohana o kēia ʻano
• Puhipaka
• Hōʻike i nā mea e like me trichlorethylene a i ʻole chemotherapy chemotherapy
• ʻO sclerosis ʻōnaehana (maʻi ʻili autoimmune)

Pākuʻi ʻia paha nā ʻōuli i kekahi o kēia mau mea:

• Pokole o ka hanu
• Mū maloo
• Ka luhi i ka hoʻoikaika ʻana
• Mauleʻa
• ʻApu ʻana i ke koko
• Hanu paʻakikī i ka wā e moe pālahalaha ana

E nānā ka mea mālama ola iā ʻoe a nīnau e pili ana i kāu mōʻaukala a me nā ʻōuli.

Hōʻike paha ka hōʻike:

• Hoʻonui kaomi i nā ʻāʻī o ka ʻāʻī
• ʻO ka ʻōniu ʻana o nā manamana lima
• ʻO ka waihoʻoluʻu ʻulaʻula o ka ʻili ma muli o ka nele o ka oxygen (cyanosis)
• ʻO ka pehu i nā wāwae

Lohe paha kāu mea hāʻawi i nā kani naʻau maikaʻi ʻole ke hoʻolohe nei i ka umauma a me nā akemāmā me kahi stethoscope.

E hana ʻia paha kēia mau hoʻāʻo:

• Nā ʻenekini koko arterial
• ʻO ka oximetry koko
• Pākuʻi x-ray
• ʻO Chest CT
• ʻO ka catheterization Cardiac
• Nā hoʻāʻo hana lung
• ʻEchocardiogram
• ʻO Biopsy Lung

ʻAʻole ʻike ʻia i kēia manawa ka lapaʻau olakino maikaʻi. Eia nō naʻe, he kōkua paha nā lāʻau aʻe no kekahi poʻe:

• Nā lāʻau e hoʻonui i nā kīʻaha koko (vasodilators)
• Nā lāʻau lapaʻau e kaohi ai i ka pane o ka ʻōnaehana pale (e like me azathioprine a i ʻole steroid)

Pono paha kahi transplant lung.

ʻO ka hopena he ʻilihune loa ia i nā pēpē, me kahi ola i loko o kekahi mau pule wale nō. ʻO ke ola ʻana i nā mākua he mau mahina a i kekahi mau makahiki.

Pākuʻi ʻia paha nā pilikia o ka PVOD:

• ʻO ka hanu paʻakikī e hele a ʻoi aku ka maikaʻi, e like me ka pō (apnea hiamoe)
• Hypertension pulmonary
• Hoka puʻuwai ʻaoʻao ʻākau (cor pulmonale)

Kāhea i kāu mea hāʻawi inā loaʻa iā ʻoe nā ʻōuli o kēia maʻi.

ʻO ka maʻi vaso pulmonary

• ʻŌnaehana hanu

ʻO Chin K, Channick RN. Hypertension pulmonary. I: Broaddus VC, Mason RJ, Ernst JD, et al, eds. ʻO Murray a me Nadel's Textbook of Respiratory Medicine. ʻElua huaʻōleloPiladelapia, PA: Elsevier Saunders; 2016: chap 58.

ʻO Churg A, Wright JL. Hypertension pulmonary. I: Leslie KO, Wick MR, eds. ʻO ke ʻano pulmonary pathology: kahi hoʻokokoke ʻana. ʻEkolu huaʻōlelo. Piladelapia, PA: Elsevier; 2018: chap 12.

Mclaughlin VV, Humbert M. Pulmonary hypertension. I: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. ʻO ka maʻi puʻuwai ʻo Braunwald: He puke aʻo no ka lāʻau Cardiovascular. 11th hua. Piladelapia, PA: Elsevier; 2019: chap 85.