ʻO ka lauoho ʻohe (Trichorrhexis Invaginata)

Anter

• He aha nā hōʻailona o ka lauoho ʻohe?
• He aha ke kumu o ka lauoho ʻohe?
• Nānā i ka lauoho ʻohe
• Lapaʻau no ka lauoho ʻohe
• He aha ka manaʻo no ka poʻe me ka lauoho ʻohe?

Hoʻopili mākou i nā huahana a mākou e manaʻo nei he pono no kā mākou poʻe heluhelu. Inā kūʻai ʻoe ma o nā loulou i kēia ʻaoʻao, loaʻa iā mākou kahi kōmike liʻiliʻi. Eia kā mākou hana.

He aha ka lauoho ʻohe?

ʻO ka lauoho ʻohe kahi lauoho lauoho i kūpono ʻole i ke ʻano o ka lauoho lauoho e like me nā knots i kahi ʻau ʻohe. Kūleʻa nā lauoho lauoho maʻamau i ke anuanu ma lalo o kahi microscope. ʻIke ʻia i loko o ka lauoho ʻohe he nodule (puʻupuʻu) a i ʻole nā ​​pali kaulike kaulike. ʻIke ʻia ka lauoho ʻohe ʻo trichorrhexis invaginata.

ʻO ka lauoho ʻohe kahi hiʻohiʻona o kahi maʻi i kapa ʻia ʻo Netherton Syndrome. ʻO ka hapa nui o nā hihia o ka lauoho ʻohe e Netherton syndrome. He kūlana hoʻoilina ia e hopena i ka ʻulaʻula, ʻili flaky a puni ke kino a me nā pilikia āpau.

Hiki i ka lauoho ʻohe ke hoʻopili i ka lauoho ma luna o ke poʻo, nā kuʻemaka, a me nā maka maka.

He aha nā hōʻailona o ka lauoho ʻohe?

Hiki i nā ʻōuli o ka lauoho ʻohe ke hoʻopili pū me:

• lauoho haki maʻalahi
• nā lauoho lauoho i loaʻa i kahi helehelena knotty
• he nalowale ʻana o nā maka maka
• he nalowale ʻana o nā kuʻemaka
• ulu lauoho lauwili a lauana pohina kumu
• lauoho maloʻo
• lauoho wiwi ʻole
• lauoho ʻōniʻoniʻo
• lauoho pōkole ma muli o ka haki mau
• nā lauoho ma nā kuʻemaka e like me nā matchsticks

Loaʻa i nā keiki i hānau ʻia me ka maʻi ʻo Netherton he ʻulaʻula, ʻili flaky. ʻAʻole hiki iā lākou ke hoʻomohala i nā hōʻailona o ka lauoho ʻohe a hiki i ka hala ʻana o 2 mau makahiki.

He aha ke kumu o ka lauoho ʻohe?

ʻO kahi moʻomeheu hoʻoilina hoʻoilina i kapa ʻia ʻo SPINK5 ke kumu o ka lauoho ʻohe. Hiki i kahi mutation i kēia gen ke alakaʻi i kahi kaʻina ulu ulu maʻamau.

Kuhi ʻia ka lauoho ʻohe e kahi nāwaliwali o ka cortex (waena) o kāu mau lauoho. Kuhi nā wahi nāwaliwali i kekahi mau kiko ma ka pae. ʻO nā ʻāpana ʻoi aku ka paʻakikī o ka cortex kaomi i loko o kēia mau wahi nāwaliwali, e hoʻokumu ana i nā nodule a i ʻole nā ​​kualono. Hana kēia i kahi hiʻohiʻona puʻupuʻu i ka lauoho lauoho. ʻO ka hopena maʻamau ka lauoho i haki maʻalahi.

Nānā i ka lauoho ʻohe

No ke kuhi ʻana i ka lauoho ʻohe, e ʻako ʻo kāu kauka i kahi lauoho mai kou poʻo e nānā iā ia ma lalo o kahi microscope.

No ke kuhi ʻana i ka maʻi ʻo Netherton, hiki i kāu kauka ke kauoha i kahi moʻo o nā hoʻokolohua DNA a i ʻole kahi biopsy o ka ʻili e hoʻāʻo no ka hoʻololi ʻana o nā ʻāpana. No kahi biopsy o ka ʻili, e hoʻoneʻe kāu kauka i kahi liʻiliʻi o ka ʻili o ka ʻili no ka hoʻāʻo ʻana i ka lab. Hoʻohana pinepine ʻia nā hoʻokolohua DNA e hoʻāʻo i ka ʻaoʻao SPINK5 no nā mea ʻē.

Lapaʻau no ka lauoho ʻohe

ʻOiai ʻo ke ʻano he hopena pololei ia o ka hoʻololi ʻana o ka moʻokūʻauhau, ʻaʻohe ala o kēia manawa i ʻike ʻia e pale ai i ke ʻano. Akā he nui nā ʻano lotion a me nā hamo hiki iā ʻoe ke hoʻohana e mālama i ka lauoho ʻohe. Pākuʻi ʻia kēia mau mea:

• emollients a me keratolytic (ʻo ka mea nui me ka urea, ka wai lactic acid, a me ka waikawa salicylic) e hoʻoulu i kou ʻili.
• antibiotics no nā maʻi i loko o ka ʻili a me nā wahi ʻē aʻe
• antihistamines no ka ʻili o ka ʻili
• nā steroid topical, akā ʻaʻole pono e hoʻohana ʻia kēia mau mea i nā pēpē
• photochemotherapy (PUVA) a me retinoids waha

Kūʻai no nā emollients keratolytic ma ka pūnaewele.

Hiki iā ʻoe ke hoʻoliʻiliʻi i ka haki o ka lauoho me ka hōʻoia ʻana i ka hoʻomau o ka lauoho i kou lauoho. E inu mau i ka wai a pale i ka hoʻohana ʻana i nā huahana lauoho i hoʻokumu ʻia me ka wai ʻona. Hiki iā lākou ke hoʻomaloʻo i kou lauoho, kahi e hōʻino ai i ka haki. Aia kekahi huahana mālama lauoho e pili ana i ka hydrating o ka lauoho maloʻo.

Hōʻalo i ka hoʻohana ʻana o nā kemika i kou lauoho, e like me ka mea hoʻomaha lauoho a perms paha. Mai hoʻohana iā lākou ma ka lauoho poino, pū kekahi. Ke hoʻohana nei i kēia mau huahana i hopena i ka make nui o ka lauoho a me ka alopecia cicatricial (alopecia scarring). Hoʻoweliweli kēia ʻano lauoho i kou lauoho lauoho a hoʻoliʻiliʻi iki ka ulu ʻana o ka lauoho i ka wā e hiki mai ana.

He aha ka manaʻo no ka poʻe me ka lauoho ʻohe?

ʻOiai ʻaʻole hiki ke pale a hōʻola piha ʻia ke ʻano no ka mea ʻo ia ka hopena o kahi mutation, aia kekahi mau ala e mālama ai i kāu mau hōʻailona me ka hydrating ʻana i kou lauoho a me ka hoʻōla ʻana i kou ʻili.

Hōʻalo i nā kemika e hoʻomaloʻo i kou lauoho a me kou poʻo. E hoʻohana i nā huahana mālama lauoho e hydrate i kou lauoho. Hiki i nā hamo a me nā hamo hoʻemi i nā hōʻailona pū kekahi.

Hoʻomaikaʻi pū ke ʻano me ka makahiki, ʻoiai inā haʻalele ʻole ʻia.