West Syndrome: he aha ia, nā ʻōuli a me nā lāʻau

Anter

• Nā hiʻohiʻona nui
• Nā kumu o ka maʻi komohana
• Pehea e hana ai i ka lāʻau
• Hiki ke mālama ʻia ʻo West syndrome?

ʻO West Syndrome kahi maʻi maʻamau i ʻike ʻia e ka hopu pinepine ʻana o ka maʻi epileptic, ʻoi aku ka maʻamau ma waena o nā keikikāne a hoʻomaka ʻo ia e hōʻike iā ia iho i ka makahiki mua o ke ola o ka pēpē. ʻO ka maʻamau, kū nā pilikia mua ma waena o 3 a me 5 mau mahina o ke ola, ʻoiai hiki ke ʻike ʻia a hiki i ka 12 mau mahina.

Aia he 3 ʻano o kēia maʻi, ʻo ka hōʻailona, ​​idiopathic a me ka cryptogenic, a i loko o ka hōʻailona he kumu ko ka pēpē e like me ka hanu ʻole o ka pēpē no ka manawa lōʻihi; ʻO ka cryptogenic ke kumu ia e kekahi maʻi lolo a i ʻole ke kūpono ʻole, a ʻo ka idiopathic ke hiki ʻole ke ʻike ʻia ke kumu a loaʻa paha i ka pēpē ka hoʻomohala kaʻa maʻamau, e like me ka noho ʻana a me ke kolo ʻana.

Nā hiʻohiʻona nui

ʻO nā hiʻohiʻona e kū nei i kēia maʻi e hoʻolohi ʻia i ka hoʻomohala psychomotor, ka hopu ʻana o ka epileptic i kēlā me kēia lā (i kekahi manawa ʻoi aku ma mua o 100), a me nā hoʻokolohua e like me ka electroencephalogram e hōʻoia i ka kānalua. Ma kahi o 90% o nā keiki me kēia maʻi maʻamau ka hoʻomau ʻana o ka noʻonoʻo, autism a me nā loli waha he laha loa. ʻO Bruxism, ka hanu waha, ka maloccusion niho a me ka gingivitis nā loli maʻamau i kēia mau keiki.

ʻO ka mea pinepine pinepine ka mea lawe i kēia maʻi e hoʻopili ʻia e nā maʻi lolo ʻē aʻe, kahi hiki ke pale i ka mālama ʻana, me ka ulu ʻana o ka maikaʻi, paʻakikī e kaohi. Eia nō naʻe, aia kekahi mau pēpē inā ola hou lākou.

Nā kumu o ka maʻi komohana

ʻO nā kumu o kēia maʻi, i hiki i nā kumu he nui, ʻaʻole i ʻike ʻia no kekahi mau mea, akā ʻo nā pilikia maʻamau ka hānau ʻana, e like me ka nele o ka oxygenation cerebral i ka manawa o ka hānau ʻana a ma hope koke paha o ka hānau ʻana, a me hypoglycemia.

ʻO kekahi mau hanana i makemake e makemake i kēia maʻi ʻo ka lolo ka malformation, prematurity, sepsis, Angelman syndrome, hahau, a i ʻole nā ​​maʻi e like me rubella a cytomegalovirus i ka wā hāpai, i hoʻohui ʻia me ka hoʻohana ʻana i nā lāʻau a i ʻole ka inu ʻana i ka waiʻona i ka wā hāpai. ʻO kekahi kumu ka hoʻololi ʻana i ka ʻāpana ʻO homeobox e pili ana iā Aristaless (ARX) ma ka X chromosome.

Pehea e hana ai i ka lāʻau

Pono e hoʻomaka i ka mālama ʻana no ka West Syndrome i ka wā hiki loa, no ka mea i ka wā o ka hopu ʻana o ka maʻi epileptic hiki i ka lolo ke ʻeha i ka pohō i hiki ʻole ke hoʻololi hou ʻia.

ʻO ka hoʻohana ʻana i nā lāʻau e like me adrenocorticotrophic hormone (ACTH) kahi lāʻau lapaʻau ʻē aʻe, a me ka physiotherapy a me ka hydrotherapy. ʻO nā lāʻau e like me sodium valproate, vigabatrin, pyridoxine a me benzodiazepines hiki ke kuhikuhi ʻia e ke kauka.

Hiki ke mālama ʻia ʻo West syndrome?

I nā hihia maʻalahi, ke pili ʻole ka West Syndrome i nā maʻi ʻē aʻe, ke hana ʻole ia nā ʻōuli, ʻo ia hoʻi, ke ʻike ʻole ʻia ke kumu, e manaʻo ʻia ana he idiopathic West syndrome a ke loaʻa i ke keiki ka lapaʻau ma mua, ke hiki koke nā pilikia mua. ʻike ʻia, hiki ke kaohi ʻia ka maʻi, me ka manawa o ka hoʻōla, me ka ʻole o ka pono hoʻoikaika kino, a he hanana maʻamau paha ke keiki.

Eia nō naʻe, inā loaʻa nā maʻi ʻē aʻe i ka pēpē a inā koʻikoʻi kona olakino, ʻaʻole hiki ke hoʻōla ʻia ka maʻi, ʻoiai hiki i nā lapaʻau ke hōʻoluʻolu hou aʻe. ʻO ke kanaka maikaʻi loa e hōʻike i ke kūlana olakino o ka pēpē ka neuropediatrician nāna, ma hope o ka loiloi ʻana i nā hoʻokolohua āpau, e hiki ke hōʻike i nā lāʻau kūpono loa a me ka pono o ka psychomotor stimulate a me nā physiotherapy session.