Goodpasture Syndrome: he aha ia, nā ʻōuli, nā kumu a me nā lāʻau
Anter
ʻO ka Goodpasture Syndrome kahi maʻi autoimmune laha ʻole, kahi e hoʻouka ai nā kino pale o ke kino i nā puʻupaʻa a me nā akemāmā, ke kumu nui ʻia nā hōʻailona e like me ke kahe ʻana o ke koko, paʻakikī ka hanu ʻana a me ke kahe o ke koko i ka mimi.
Kūpono kēia maʻi ma muli o ke alo o nā mea ʻino e hoʻouka i nā hunaola o nā puʻupaʻa a me nā akemāmā. ʻO kekahi mau mea e hoʻonui i ka makaʻu o ka hoʻomohala ʻana i kēia maʻi ʻo: ka loaʻa ʻana o ka moʻaukala o ka maʻi a me ka puhipaka pū kekahi, i loaʻa i nā maʻi hanu hou a hōʻike ʻia i ka inhalation o nā mea e like me ka methane a propane paha, e laʻa me.
Hoʻokumu ʻia ka mālama ʻana i ka hoʻohana ʻana i nā lāʻau e like me nā immunosuppressants a me nā corticosteroids, akā i nā hihia ʻoi loa, pono paha ka plasmapheresis a i ʻole ka hemodialysis.
Nā hōʻailona nui
ʻO nā ʻōuli nui o Goodpasture Syndrome:
- Luhi nui loa;
- E hoʻomake ana i ke koko;
- Hanu paʻakikī;
- ʻEha ke hanu;
- Hoʻonui i nā pae o ka urea i ke koko;
- Loaʻa ke koko a me / a i ʻole ka huʻa i ka mimi;
- Puhi ke ʻino.
Ke hōʻike ʻia nā ʻōuli, pono ia e ʻimi koke i ka lāʻau no nā hoʻokolohua a me ka hōʻailona o ka lapaʻau kūpono loa, ʻoiai e ʻoi aku paha ka maikaʻi o nā ʻōuli inā ʻaʻole mālama mua ʻia ka maʻi.
Hoʻohui ʻia, loaʻa paha nā maʻi ʻē aʻe i nā ʻōuli e like loa me kēia maʻi, e like me Wegener's granulomatosis, ka mea e paʻakikī ai ka ʻike. ʻIke i nā ʻōuli a pehea e mālama ai i ka granulomatosis a Wegener.
Pehea e hōʻoia ai i ke kuhi
E hōʻoia i ka maʻi o Goodpasture, e nānā ke kauka i kou mōʻaukala olakino a me ka lōʻihi o kāu mau ʻōuli. A laila, kauoha paha ke kauka i kekahi mau hoʻokolohua, e like me nā hoʻāʻo ʻana o ke koko a me ka mimi, e ʻike ai i nā mea ʻino i hana ʻia e ke kino nāna i hoʻokumu i ka maʻi o Goodpasture.
e like me ka biopsy hakuʻala, ʻo ia ka hemo ʻana o kahi ʻāpana liʻiliʻi o ke kola puʻupaʻa, e ʻike ai inā aia he mau hunaola ke kumu o ka maʻi ʻo Goodpasture.
Hoʻohui ʻia, kauoha paha ke kauka i nā hoʻokolohua ʻē aʻe, e like me ka biopsy hakuʻala, ʻo ia ka wehe ʻana i kahi ʻāpana o nā puʻupaʻa e nānā ʻia i loko o ke keʻena hoʻokolohua, i mea e ʻike ai inā aia nā pūnaewele i kumu i ka maʻi o Goodpasture.
Hiki ke kauoha ʻia i nā kaola X a me CT scans e kāu kauka e ʻike i ka hōʻino o ka hū. E ʻike i nā kikoʻī e pili ana i ka hana ʻia ʻana o ka tomography.
Nā kumu kūpono
ʻO ke kumu o Goodpasture's Syndrome ma muli o nā anti-GBM anti-antodies i hoʻouka i ka NC-1 ʻāpana o ka ʻano IV collagen i nā puʻupaʻa a me nā puʻupaʻa.
ʻIke ʻia ka maʻi maʻamau o kēia maʻi ma nā kāne ma mua o nā wahine, ma waena o 20 a 30 mau makahiki, a i ka poʻe me ka ʻili māmā. Hoʻohui ʻia, ka hōʻike ʻana i nā kemika e like me nā pesticides, ka uahi paka, a me nā maʻi i hoʻokumu ʻia e nā mea ʻino nā kumu ʻē aʻe i ʻike ʻia e hoʻonui i ka makaʻu o ka hoʻomohala ʻana i ka maʻi, no ka mea hiki iā lākou ke hoʻouka i nā huna pale o ke kino i nā māmā a me nā puʻupaʻa.
Pehea e hana ai i ka lāʻau
Lawe ʻia ka mālama ʻana iā Goodpasture's Syndrome ma ka haukapila a hoʻokumu ʻia i ka hoʻohana ʻana i nā lāʻau immunosuppressive a me nā corticosteroids, ka mea e pale ai i nā huna pale o ke kino mai ka luku ʻana i nā puʻupaʻa a me nā akemāmā.
I kekahi mau hihia, hōʻike ʻia ka lapaʻau ʻana e plasmapheresis, kahi hana e kānana ai i ke koko a hoʻokaʻawale i nā mea ʻino e hoʻopōʻino ai i ka puʻupaʻa a me ka akemāmā. Inā ua loli nui ʻia nā puʻupaʻa, e koi ʻia ka hemodialysis a i ʻole ke transplantation hakuʻala. Maopopo ke ʻano o ka plasmapheresis a pehea e hana ai.
HoʻOmaopopo Mākou
Hoʻomaʻamaʻa Retroperitoneal
