Mea Kākau: Lewis Jackson
Lā O Ka Hana: 7 Mei 2021
HōʻAno Hou I Ka Lā: 1 Iulai 2024
Anonim
Idiopathic Pulmonary Fibrosis - pathophysiology, signs and symptoms, investigation and treatment
Wikiō: Idiopathic Pulmonary Fibrosis - pathophysiology, signs and symptoms, investigation and treatment

Anter

Pulmonary fibrosis kahi kūlana e kumu ai i ka scarring baga a me ka ʻoʻoleʻa. He mea paʻakikī kēia e hanu ai. Hiki iā ia ke pale i kou kino mai ka loaʻa ʻana o ka oxygen a hiki i ka hopena ke alakaʻi i ka ʻole hanu, ʻole ʻole ka puʻuwai, a i ʻole nā ​​pilikia ʻē aʻe.

Manaʻo nā kānaka noiʻi i kēia manawa ka hui pū ʻana o ka hōʻike ʻana i nā ukiuki o ka hū e like me kekahi mau kemika, ka puhipaka, a me nā maʻi, a me nā genetics a me nā hana ʻōnaehana paleʻea, ke kuleana nui i ka pulmonary fibrosis.

Ua manaʻo ʻia ma muli o ke kuni ka hopena. I kēia manawa ua manaʻo ka ʻepekema aia kahi hana hoʻōla ʻole i loko o nā akemāmā e hiki ai i ka scarring. ʻO ke hoʻokumu ʻana i nā scarring māmā nui e lilo i fibrosis pulmonary.

He aha nā hōʻailona o ka pulmonary fibrosis?

Loaʻa paha iā ʻoe ka fibrosis pulmonary no kekahi manawa me ka ʻole o nā hōʻailona. ʻO ka pōkole o ka hanu ka hōʻailona mua e ulu.

Hiki i nā ʻōuli ʻē aʻe ke hoʻopili pū me:

  • maloo, hacking kohā paʻa loa (wā lōʻihi)
  • nāwaliwali
  • luhi
  • hāwili ʻana o nā manamana lima, i kapa ʻia ʻo clubbing
  • Kaumaha emi
  • hōʻoluʻolu umauma

Ma muli o ke ʻano e pili pinepine ai ke ʻano i ka poʻe mākua, hāʻawi pinepine ʻia nā ʻōuli mua i ka makahiki a i ʻole ka nele o ka hoʻoikaika kino.


Maliʻiliʻi paha kāu mau ʻōuli ma ka mua a holomua i ka holo ʻana o ka manawa. Hiki ke hoʻololi i nā ʻōuli mai kekahi kanaka a i kekahi. ʻO kekahi poʻe me ka fibrosis pulmonary e maʻi koke.

He aha ke kumu o ka pulmonary fibrosis?

Hiki ke hoʻokaʻawale ʻia nā kumu o ka pulmonary fibrosis i mau ʻāpana:

  • nā maʻi maʻi autoimmune
  • nā maʻi maʻi
  • hoʻolilo kaiapuni
  • nā lāʻau
  • idiopathic (ʻike ʻole)
  • genetics

Nā maʻi maʻi autoimmune

Hoʻokomo nā maʻi Autoimmune i kou ʻōnaehana pale maʻi e hoʻouka iā ia iho. ʻO nā kūlana autoimmune i hiki ke alakaʻi i ka fibrosis pulmonary pū:

  • rumatika
  • lupus erythematosus, ka mea i ʻike pinepine ʻia ʻo lupus
  • scleroderma
  • polymyositis
  • dermatomyositis
  • vasculitis

Nā maʻi ʻino

ʻO nā ʻano o nā maʻi i hiki ke kumu i ka fibrosis pulmonary:

  • maʻi kīnā
  • nā maʻi ʻino, nā hopena mai ka hepatitis C, adenovirus, herpes virus, a me nā maʻi ʻē aʻe

Hōʻike kaiapuni

Hiki ke hāʻawi i ka hōʻike i nā mea i ke kaiapuni a i ʻole kahi hana i ka fibrosis pulmonary. ʻO kahi laʻana, loaʻa i ka uahi paka ka nui o nā kemika i hiki ke hōʻino i kou mau māmā a alakaʻi i kēia ʻano.


ʻO nā mea ʻē aʻe i hiki ke hōʻino i kāu mau māmā me:

  • nā olonā asbestos
  • lepo lepo
  • lepo silika
  • kekahi mau ʻenekini
  • pāhawewe

Nā Lapaʻau

Hiki i kekahi mau lāʻau ke hāpai i kou makaʻu i ka hoʻomōhala ʻana i ka fibrosis pulmonary. Inā ʻoe e lawe i kekahi o kēia mau lāʻau i kēlā me kēia manawa, koi paha ʻoe i ka nānā pono ʻana e kāu kauka.

  • nā lāʻau chemotherapy, e like me cyclophosphamide
  • antibiotics, e like me nitrofurantoin (Macrobid) a me sulfasalazine (Azulfidine)
  • nā lāʻau cardiac, e like me amiodarone (Nexterone)
  • nā lāʻau biologic e like me adalimumab (Humira) a i ʻole etanercept (Enbrel)

ʻIlikopa

I nā manawa he nui, ke kumu kūpono o fibrosis pulmonary i ʻike ʻole ʻia. Keia ka hihia, kapa ʻia ke ʻano he idiopathic pulmonary fibrosis (IPF).

Wahi a ka American Lung Association, ʻo ka hapa nui o ka poʻe me fibrosis pulmonary he IPF.

Nā Genetics

Wahi a ka Pulmonary Fibrosis Foundation, ma kahi o 3 a 20 pākēneka o ka poʻe me IPF i kekahi lālā ʻohana me ka fibrosis pulmonary. I kēia mau hihia, ʻike ʻia ʻo ia ʻo fibrosis pulmonary ʻohana a i ʻole famonia interstitial pneumonia.


Ua hoʻopili nā kānaka noiʻi i kekahi mau ʻiʻo i kēia kūlana, a me ka noiʻi ʻana e pili ana i nā hana a nā genetics e hoʻomau nei.

ʻO wai ka makaʻu i ka fibrosis pulmonary?

E ʻike ʻia paha ʻoe me ka pulrosary fibrosis inā ʻoe:

  • he kāne
  • Aia ma waena o nā makahiki 40 a 70
  • he moʻolelo no ka puhipaka
  • he moʻolelo ʻohana ko kēia ʻano
  • pili i kahi maʻi autoimmune e pili ana i ke ʻano
  • ua lawe i kekahi mau lāʻau e pili ana i ka maʻi
  • ua mālama ʻia i nā maʻi maʻi ʻaʻai, ʻo ka radiation radiation
  • hana i kahi hana e pili ana me ka hoʻonui i ka makaʻu, e like me ka mining, mahiʻai, a kūkulu ʻana paha

Pehea e ʻike ʻia ai ka fibrosis pulmonary?

Pulmonary fibrosis kekahi o nā ʻano ʻoi aku o 200 o nā maʻi ākea e kū nei. Ma muli o ka nui o nā ʻano maʻi like ʻole o ka maʻi, he pilikia paha kāu kauka e ʻike ai ʻo ka fibrosis pulmonary ke kumu o kāu mau ʻōuli.

I kahi ana e ka Pulmonary Fibrosis Foundation, 55 pākēneka o nā mea pane i hōʻike hewa ʻia i kekahi manawa. ʻO nā misdiagnoses maʻamau ka hānō, ka ponia, a me ka bronchitis.

Ke hoʻohana nei i nā alakaʻi i kēia manawa, ua manaʻo ʻia hiki i ka 2 ma 3 mau maʻi me ka pulmonary fibrosis ke ʻike pono ʻia me ka ʻole o kahi biopsy.

Ma ka hoʻohui ʻana i kāu ʻike haukapila a me nā hopena o kahi ʻano CT scan o ka umauma, e ʻike pono kāu kauka iā ʻoe.

I nā hihia ke maopopo ʻole ke kuhi, pono paha kahi laʻana kiko, a biopsy paha.

Nui a hewahewa nā ʻano hana no ka hana ʻana i kahi biopsy o ka maʻi āpau, no laila e paipai ai kāu kauka i ke kaʻina hana maikaʻi loa nāu.

Hiki paha i kāu kauka ke hoʻohana i nā ʻano hana like ʻole e ʻike i ka fibrosis pulmonary a i ʻole e kāpae i nā kūlana ʻē aʻe. Pākuʻi ʻia kēia mau mea:

  • pulse oximetry, kahi hōʻike noninvasive o kāu pae oxygen oxygen
  • nā ho'āʻo koko e nānā i nā maʻi autoimmune, nā maʻi, a me ka anemia
  • kahi hoʻokolohua kinoea koko arterial e hōʻoia pololei i nā pae o ka oxygen i kou koko
  • kahi sputum sample e nānā ai i nā hōʻailona o ka maʻi
  • kahi hoʻāʻo hana pulmonary e ana i kou hiki māmā
  • kahi echocardiogram a i ʻole ka hoʻāʻo koʻikoʻi puʻuwai e ʻike inā pilikia ka puʻuwai i kāu mau ʻōuli

Pehea e mālama ʻia ai ka fibrosis pulmonary?

ʻAʻole hiki i kāu kauka ke hoʻohuli i ka scarring paru, akā hiki iā lākou ke kuhikuhi i nā lāʻau e kōkua i ka hoʻomaikaʻi ʻana i kou hanu ʻana a hoʻolōʻihi i ka holomua o ka maʻi.

ʻO nā ʻano ma lalo iho nei kekahi mau laʻana o nā koho o kēia manawa i hoʻohana ʻia no ka mālama ʻana i ka fibrosis pulmonary:

  • oxygen hoʻonui
  • prednisone e kāohi i kāu ʻōnaehana paleʻoniʻoni a hoʻēmi i ka puhū
  • azathioprine (Imuran) a i ʻole mycophenolate (CellCept) e kāohi i kāu ʻōnaehana pale maʻi
  • pirfenidone (Esbriet) a i ʻole nintedanib (Ofev), nā lāʻau antifibrotic e ālai ana i ke kaʻina scarring i loko o nā akemāmā

E ʻōlelo paha kāu kauka i ka hoʻoponopono pulmonary. Pili kēia mālama ʻana i kahi papahana hoʻoikaika kino, aʻo, a me ke kākoʻo e kōkua iā ʻoe e aʻo pehea e hanu maʻalahi ai.

Paipai paha kāu kauka iā ʻoe e hoʻololi i kou nohona. Pili pū paha kēia mau hoʻololi i kēia mau mea:

  • Pono ʻoe e hōʻalo i ka uahi lua a hana i nā ʻanuʻu e haʻalele inā puhipaka ʻoe. Hiki i kēia ke kōkua i ka lohi i ka holomua o ka maʻi a hōʻoluʻolu i kou hanu.
  • ʻAi i ka papaʻai kaulike maikaʻi.
  • E hāhai i kahi hoʻolālā hoʻoikaika i hoʻomohala ʻia me ke alakaʻi a kāu kauka.
  • E hoʻomaha kūpono a pale i ke koʻikoʻi nui.

Hiki ke ʻōlelo ʻia kahi transplant lung no nā mea ma lalo o ka makahiki 65 me nā maʻi nui.

He aha ka nānā no ka poʻe me fibrosis pulmonary?

ʻO ka helu o ka fibrosis pulmonary e hoʻoweliweli ai i nā ake māmā o nā kānaka. ʻAʻole hiki ke hoʻohuli ʻia ka scarring, akā hiki i kāu kauka ke koi aku i nā mālama e hōʻemi ai i ka helu o kāu kūlana.

Hiki i ke ʻano ke hana i nā pilikia he nui, e like me ka hanu ʻole o ka hanu. Hana ʻia kēia ke hana pono ʻole kou mau māmā a ʻaʻole hiki iā lākou ke lawa ka oxygen i kou koko.

Hāpai pū kekahi ʻo pulosary fibrosis i kou makaʻu o ka maʻi ʻaʻai pūpū.

Nā ʻōlelo aʻoaʻo no ka pale ʻana

ʻAʻole hiki ke pale ʻia kekahi mau hihia o ka pulosary fibrosis. Pili nā hihia ʻē aʻe i nā hopena pilikia a puni a me ka lawena e hiki ke kaohi ʻia. E hāhai i kēia mau ʻōlelo aʻoaʻo e hoʻohaʻahaʻa i kou makaʻu i ka loaʻa ʻana o ka maʻi.

  • Pale i ka puhipaka.
  • Hōʻalo i ka uahi lua.
  • E ʻaahu i kahi pale maka a i ʻole nā ​​mea hanu ʻē aʻe inā ʻoe e hana i kahi kaiaulu me nā kemika weliweli.

Inā pilikia ʻoe i ka hanu, hana i kahi manawa me kāu kauka. Hiki ke hoʻomaikaʻi a me ka mālama ʻana i ka wā mua ke hoʻomaikaʻi i ka wā lōʻihi no ka poʻe me nā maʻi maʻi he nui, e like me ka pulmonary fibrosis.

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