ʻO nā mea āpau āu e ʻike ai e pili ana iā Porphyria Cutanea Tarda

Anter

• Nā ʻōuli
• Nā kiʻi o porphyria cutanea tarda
• Nā Kumu
• Nā kumu weliweli
• Ka hanana
• Kānāwai
• Lapaʻau
• Outlook

Hōʻike Overview

ʻO Porphyria cutanea tarda (PCT) kahi ʻano porphyria a i ʻole nā ​​maʻi koko e hoʻopili i ka ʻili. ʻO ka PCT kekahi o nā ʻano like ʻole o ka porphyria. Kuhi ʻia ia i kekahi manawa i ka colloqually ma ke ʻano he maʻi vampire. ʻO ia no ka mea ʻike pinepine ka poʻe me kēia ʻano i nā ʻōuli ma hope o ke kū ʻana i ka lā.

Nā ʻōuli

ʻO ka hapa nui o nā ʻōuli o ka porphyria cutanea tarda e ʻike ʻia ma ka ʻili. ʻO nā ʻōuli maʻamau ka:

• pālahalaha i ka ʻili i hōʻike ʻia i ka lā, me nā lima, ka maka, a me nā lima
• photosensitivity, ʻo ia hoʻi he maʻalahi kou ʻili i ka lā
• ʻili lahilahi a palupalu paha
• hoʻonui i ka ulu ʻana o ka lauoho, maʻamau i ka maka
• ʻili a wili ʻana o ka ʻili
• ʻulaʻula, pehu, a i ʻole ʻili ka ʻili
• nā ʻeha e ulu ana ma hope o nā hōʻeha liʻiliʻi i ka ʻili
• hyperpigmentation, ʻo ia hoʻi nā poʻi o ka ʻili i lilo i pouli
• mimi ʻoi aku ka pouli ma mua o ka maʻamau a i ʻole ʻulaʻula ʻulaʻula
• hōʻino ka ate

Ma hope o ka hana ʻia ʻana o nā palapū ma kou ʻili, ʻili paha ka ʻili. He mea maʻamau no ka scarring e hōʻike i ka manawa e ola ai nā palapū.

Hōʻike maʻamau nā pā Hyperpigmentation ma ka maka, nā lima, a me ka ʻāʻī.

Nā kiʻi o porphyria cutanea tarda

Nā Kumu

ʻO Porphyria cutanea tarda paha ke kumu o nā mea like ʻole. Hoʻokaʻawale ʻia nā kumu ma ke ʻano he genetical a loaʻa paha.

ʻO nā kumu kūlohelohe e like me:

• ʻohana moʻolelo o porphyria cutanea tarda
• hoʻoilina hoʻoilina o ke akehua akepola uroporphyrinogen decarboxylase
• moʻolelo o ka ʻohana o ka maʻi ate a i ʻole ke kanesa maʻi ate
• ʻoi aku ka hao ate ma mua o ka maʻamau

ʻO nā kumu i loaʻa pinepine ʻia e hoʻopili ʻia:

• inu lama
• me ka hoʻohana ʻana i ka estrogen therapy
• me ka hoʻohana ʻana i nā mea pale waha
• ka hōʻike ʻana i kekahi mau kaiapuni a i ʻole nā ​​kemika, e like me Agent Orange
• lawe hao nui loa
• puhipaka
• loaʻa he hepatitis C
• loaʻa ka maʻi HIV

I kekahi mau hihia, ʻaʻole hiki ke hoʻoholo i ke kumu o ka porphyria cutanea tarda.

Nā kumu weliweli

Aia ʻoe i kahi makaʻu kiʻekiʻe o ka porphyria cutanea tarda inā ʻoe puhi a hoʻohana paha i ka ʻalekohola. E loaʻa paha kēia ʻano iā ʻoe inā he hepatitis C a i ʻole HIV paha iā ʻoe.

Ke hōʻike ʻia nei i kekahi mau kemika, e like me Agent Orange, hiki ke hoʻonui i kou makaʻu. Ua hōʻike paha ʻoe i kēia kemika inā he kūpuna ʻoe i lawelawe i kahi i loaʻa iā Agent Orange.

Ka hanana

Hiki i ka Porphyria cutanea tarda ke hoʻopili i nā kāne a me nā wahine. Hōʻike maʻamau ia ma hope o ka makahiki 30, no laila ʻaʻole maʻamau i waena o nā keiki a i ʻole nā ​​ʻōpio.

Hoʻopili ʻo Porphyria cutanea tarda i ka poʻe a puni ka honua a ʻaʻole i kaupalena ʻia i kekahi wahi a ʻāina paha. Ua manaʻo ʻia aia he 1 mai loko o 10,000 a 25,000 mau kānaka i kēia ʻano.

Kānāwai

E hana paha kāu kauka i kahi hoʻokolohua kino, e nānā i nā hōʻailona, ​​a hoʻopaʻa i kāu mōʻaukala olakino. Eia hou, hiki iā lākou ke hoʻohana i nā hōʻike aʻe e hōʻike ai i ka porphyria cutanea tarda:

• hoʻāʻo koko
• hoʻāʻo mimi
• nā hoʻāʻo o ka noho
• ʻili lāʻau

E nānā ke kauka i kāu mau pae o porphyrin a me nā ʻenema ate. Koi ʻia paha ka hoʻāʻo genetic no ka poʻe me ka mōʻaukala ʻohana o kēia ʻano.

Lapaʻau

Mālama ka lāʻau no ka porphyria cutanea tarda i ka mālama ʻana a me ka hōʻoki ʻana i nā ʻōuli. Hiki ke kōkua i nā loli nohona, e like me ka palena ʻana i ka inu waiʻona a me ka puhipaka ʻole.

ʻO nā koho lapaʻau maʻamau e:

• phlebotomy, ʻo ia ka lawe ʻana i ke koko e hōʻemi i ka hao
• chloroquine (Aralen)
• hydroxychloroquine (Plaquenil)
• lāʻau lapaʻau ʻeha
• hao chelators
• ka mālama ʻana i nā maʻi e loaʻa ai ka porphyria cutanea tarda, e like me HCV a i ʻole HIV

ʻO Phlebotomy kekahi o nā lāʻau maʻamau no ka porphyria cutanea tarda. Hoʻohana pinepine ʻia nā pā Antimalarial.

Hoʻololi nā ʻano nohona maʻamau e mālama iā porphyria cutanea tarda:

• pale ʻana i ka ʻalekohola
• puhipaka ʻole
• pale ʻana i ka lā
• ka hoʻohana ʻana i ka pale lā
• pale i nā hōʻeha i ka ʻili
• ʻaʻole lawe estrogen

E komo paha ʻoe i ka pale lā, nā pūlima lōʻihi, a me ka pāpale e hōʻalo ai i ka lā.

Hiki i ka Porphyria cutanea tarda ke hoʻonui i ka makaʻu o ka maʻi ʻaʻai ate a i ʻole cirrhosis, ka ʻili o ke ake. ʻO kēia ke kumu he mea nui ʻaʻole e inu i ka waiʻona inā loaʻa iā ʻoe kēia ʻano.

Outlook

Hoʻololi pinepine ʻo Porphyria cutanea tarda i nā mākua i ʻoi aku ma mua o ka 30. He maʻi koko ia e pili nui i ka ʻili. ʻOi aku ka maʻalahi o kou ʻili i ka lā, no laila pono ʻoe e hana i ke akahele e pale aku i ka lā. Kūleʻa nā pālū mai kēia ʻano.

Hiki i kāu kauka ke koi aku i nā ʻano lāʻau like ʻole no ka porphyria cutanea tarda. ʻO Phlebotomy a me nā papa antimalarial nā koho lapaʻau maʻamau.

Inā ʻoe e ʻimi nei i ke kākoʻo, e nānā i kēia papa inoa curate o nā blog maʻi ʻili maikaʻi loa o ka makahiki.