ʻO ka maʻi pale mua: he aha ia, nā ʻōuli a me nā lāʻau
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Anter
ʻO ka immunodeficiency mua, a i ʻole PID, kahi hanana i loli ai nā mea o ka ʻōnaehana pale, i hiki ai i ke kanaka ke maʻalahi i nā maʻi like ʻole, ʻoiai ʻaʻole e holo pono ka ʻōnaehana pale. ʻO ka hōʻailona hōʻailona nui o ka PID ka hanana ʻana o nā maʻi bacteri hou, ʻo ka sinusitis, otitis a me ka pulumonia.
ʻO ka immunodeficiency mua he genetical a me ka maʻi hānau a ʻoi aku ka nui ma nā hihia o ka male consanguineous, ʻo ia ka male ma waena o ka poʻe o ka ʻohana like, a ʻaʻole i hana pinepine ʻia ka hōʻailona ma hope o ka hānau ʻana ma muli o ka ʻike ʻole e pili ana i kēia maʻi. Eia nō naʻe, pono ka ʻike mua i mea e hōʻoia ai ke olakino a me ke ola o ke keiki, me ka pale ʻana i nā pilikia koʻikoʻi e hopena i ka make, no ka laʻana.
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Nā hōʻailona nui
ʻIke ʻia nā ʻōuli o ka maʻi pale maʻi mua i nā malama mua o ke ola, akā naʻe, i kekahi mau manawa, ʻike ʻia nā ʻōuli wale nō i ka wā makua, no ka mea pili ia i ka ʻano a me ke koʻikoʻi o ka loli.
Hiki ke ʻike ʻia nā ʻōuli ma nā ʻāpana o ke kino, no ka mea hiki ke kiʻi i kekahi ʻōnaehana a i ʻole ʻōnaehana, eia naʻe ʻike ʻia nā ʻōuli e pili ana i ka ʻōnaehana hanu, i hiki ai ke huikau i ka immunodeficiency mua me nā hanu ʻōpio a me nā maʻi lele.
No laila, no ka maʻi pale maʻi mua e lawe ʻia i ka helu i ka manawa o ke kuhi, he mea nui e makaʻala i kekahi o nā hōʻailona a me nā ʻōuli, e like me:
- 4 a ʻoi aku nā maʻi o ka pepeiao ma lalo o 1 makahiki;
- 2 a ʻoi paha nā maʻi maʻi hanu ma lalo o 1 makahiki;
- Hoʻohana i nā lāʻau antibiotic no 2 mau mahina me ka ʻole o ka hopena;
- ʻOi aku ma mua o ʻelua mau hihia o ka maʻi pneumonia ma lalo o 1 makahiki;
- Hoopanee i ka ulu ana o ke keiki;
- Nā maʻi o ka ʻōpū i hana hou ʻia;
- Ke kū ʻana o nā pilikia vaccine;
- ʻO ka hele pinepine ʻana o abscesses ma ka ʻili.
Eia hou, inā he moʻolelo ko ka ʻohana o ka immunodeficiency mua a i ʻole he kaikamahine ke keiki a kahi kāne consanguineous, ʻoi aku ka nui o ka manawa o ka loaʻa ʻana o ka maʻi pale maʻi mua.
He mea nui e makaʻala nā mākua i nā ʻōuli i hōʻike ʻia e ke keiki a me ka hanana ʻana o nā maʻi kūlohelohe i mea e hana ʻia ai ke kuhi a hoʻomaka koke ʻia ka lapaʻau ʻana i mea e hōʻalo ai i nā pilikia koʻikoʻi, e like me ka hōʻeha ʻana i ka hanu a me ka septicemia, a hiki make loa.
Pehea ka hōʻailona
Hiki ke hana i ke kuhi ma o nā hoʻokolohua koko a me nā hoʻokolohua genetical kikoʻī, ʻoiai aia he ʻoi aku ma mua o 100 mau ʻano o nā immunodeficiencies mua.
He mea nui ka hana ʻia ʻana o ka maʻi immunodeficiencies mua a hiki i ka makahiki mua o ke ola i hiki ai ke ʻōlelo i ka ʻohana no ka mālama ʻana a me ka mālama pono ʻana e mālama pono ai ke keiki a pale i nā pilikia. ʻOiai ke ʻano o ka hoʻokolohua kumu, ʻaʻole i loaʻa ka hōʻike ʻike maʻi pale pono mua ma o ka Unified Health System, aia wale nō i nā keʻena pilikino.
Iapaau ana o ka iniiaiie immunodeficiency
Pono e mālama ʻia ka mālama ʻana i ka maʻi pale maʻi mua e like me ke alakaʻi a ka pediatrician a ʻano ʻē e like me nā ʻōuli i hōʻike ʻia e ke keiki, ke koʻikoʻi a me ke kahua o ka ʻike.
Ke ʻike koke ʻia ka PID a akahai paha nā ʻōuli i hōʻike ʻia, hiki i ka pediatrician ke paipai i ka hoʻōla me nā immunoglobulins, kahi e lawelawe ʻia ai nā mea ʻohola e nalo ana i ke kino, e hoʻomaikaʻi ana i ka hana o ka ʻōnaehana pale. Hoʻohui ʻia, hoʻokele ʻia paha ka lawelawe ʻana i nā lāʻau antibiotic i loko o ke aa e hakakā i nā maʻi kūlohelohe.
Eia nō naʻe, i ka wā e pili ana i ka PID koʻikoʻi, ka mea paha ma muli o ka ʻike hope a i ʻole ke kū ʻana o nā mutation e hōʻemi i ka palekana hou aku, pono paha ka lawe ʻana i ka iwi iwi. E ʻike pehea e hana ʻia ai ka hoʻoneʻe iwi.