Mea Kākau: John Stephens
Lā O Ka Hana: 26 Ianuali 2021
HōʻAno Hou I Ka Lā: 9 Iulai 2025
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ʻO nā mea āpau e pili ana iā Antiphospholipid Syndrome (Hughes Syndrome) - Ola Kino
ʻO nā mea āpau e pili ana iā Antiphospholipid Syndrome (Hughes Syndrome) - Ola Kino

Anter

Hōʻike Overview

ʻO Hughes Syndrome, i ʻike ʻia ʻo "sticky Blood Syndrome" a i ʻole antiphospholipid Syndrome (APS), kahi ʻano autoimmune e hoʻopili i ke ala e hoʻopaʻa pū ai kāu mau hunaola koko. Manaʻo ʻia ʻo Hughes Syndrome he laha ʻole.

ʻO nā wahine i loaʻa hou i nā hāʻule ʻole a me nā poʻe i loaʻa i ka maʻi hahau ma mua o ka makahiki 50 i kekahi manawa ʻike ʻia he kumu kumu ʻo Hughes Syndrome. Ua manaʻo ʻia ʻo Hughes Syndrome e hoʻopili i ʻekolu a ʻelima mau manawa i ka nui o nā wahine ma mua o nā kāne.

ʻOiai ʻaʻole maopopo ke kumu o ka maʻi ʻo Hughes, manaʻo ka poʻe noiʻi he hiki i nā meaʻai āpau, ka nohona, a me nā genetics ke hopena i ka hoʻomohala ʻana i kēia ʻano.

Nā ʻōuli o ka maʻi Hughes

He paʻakikī nā ʻōuli o ka maʻi Hughes e ʻike, no ka mea, ʻaʻole nā ​​clots o ke koko kahi mea e hiki ai iā ʻoe ke ʻike maʻalahi me ka ʻole o nā kūlana olakino ʻē aʻe a i ʻole nā ​​pilikia. I kekahi manawa ʻo Hughes Syndrome ke kumu o ka līlia ʻulaʻula a i ʻole ke kahe ʻana o kou ihu a me nā ʻiʻo.

ʻO nā hōʻailona ʻē aʻe e loaʻa iā ʻoe ʻo Hughes Syndrome pū me:

  • hāʻule hou ʻana o ka hānau hānau a hānau hānau hou paha
  • ke koko i kou mau wāwae
  • hoʻouka ischemic kuewa (TIA) (like me ka hahau ʻana, akā me ka ʻole o nā hopena neurologic mau)
  • hahau ʻana, ʻoiai inā ma lalo ʻoe o 50 mau makahiki
  • helu platelet haʻahaʻa haʻahaʻa
  • maʻi hohola

ʻO ka poʻe i loaʻa ka lupus e loaʻa iā Hughes Syndrome.


I nā hihia maʻamau, hiki i ka maʻi ʻo Hughes i hana ʻole ʻia ke piʻi aʻe inā loaʻa iā ʻoe nā hanana ʻōpala i ka wā āpau i ke kino. Kāhea ʻia kēia catastrophic antiphospholipid Syndrome, a hiki iā ia ke kumu i nā hōʻino koʻikoʻi i kāu mau lālā a me ka make pū kekahi.

Nā kumu o ka maʻi Hughes

Ke hana nei nā mea noiʻi e hoʻomaopopo i nā kumu o ka maʻi Hughes. Akā ua hoʻoholo lākou aia kekahi kumu genetical i ka pāʻani.

ʻAʻole i hoʻokuʻu pololei ʻia ʻo Hughes Syndrome mai kahi makua, ke ala e hiki ai i nā kūlana koko ʻē aʻe, e like me hemophilia. Akā ʻo ka loaʻa ʻana o kahi lālā o ka ʻohana me ka maʻi Hughes ʻo ia hoʻi ka hoʻomohala ʻana i ke ʻano.

Hiki paha i kahi ʻāpana ke pili i nā kūlana autoimmune ʻē aʻe e hoʻonāukiuki hoʻi i ka maʻi ʻo Hughes. E wehewehe ia no ke aha e loaʻa pinepine ai i nā poʻe me kēia ʻano i nā ʻano autoimmune ʻē aʻe.

Loaʻa kekahi mau maʻi viral a bacteria paha, e like me E. coli aiʻole ka parvovirus, hiki ke hoʻomaka i ka maʻi ʻo Hughes e hoʻomohala ma hope o ka holoi ʻana o ka maʻi. ʻO ka lāʻau e kaohi ai i ka maʻi epilepsy, a me nā kaola lāʻau oral, e hoʻokani paha i ka hopena i ke ʻano.


Hiki paha i kēia mau mea kūlohelohe ke launa pū me nā ʻano nohona - e like me ka lawa ʻole o ka hoʻoikaika kino a me ka ʻai ʻana i ka papaʻai i kiʻekiʻe i ka kolesterol - a hoʻomaka i ka maʻi ʻo Hughes.

Akā ʻo nā keiki a me nā mākua me ka ʻole o kekahi o kēia mau maʻi, nā mea ola, a i ʻole ka hoʻohana lāʻau ʻana hiki ke loaʻa i ka maʻi ʻo Hughes i kēlā me kēia manawa.

Pono nā noiʻi hou e hoʻokaʻawale i nā kumu o ka maʻi Hughes.

Kānāwai o Hughes syndrome

ʻIke ʻia ka maʻi ʻo Hughes ma o nā hōʻike koko. Nānā kēia mau hoʻāʻo koko i nā mea ʻino i hana ʻia e kāu mau pale pilikino inā ʻike lākou i ke ʻano maʻamau a i ʻole nā ​​pahuhopu olakino ʻē aʻe.

ʻO kahi hōʻike koko maʻamau e ʻike ai i ka maʻi ʻo Hughes i kapa ʻia he immunoassay antibody. Pono paha ʻoe e hana i kekahi o kēia mau mea e kāpae i nā kūlana ʻē aʻe.

Hiki ke kuhi hewa ʻia ʻo Hughes Syndrome e like me nā sclerosis he nui no ka mea aia nā ʻano like ʻelua i like me nā ʻōuli. Pono e hoʻāʻo pono e hoʻoholo i kāu ʻike pololei, akā hiki ke hala i kahi manawa.


Ka mālama ʻana i ka maʻi ʻo Hughes

Hiki ke mālama ʻia ʻo Hughes Syndrome me nā mea lahilahi o ke koko (ka lāʻau e hōʻemi ai i kou makaʻi i ke koko koko).

ʻO kekahi poʻe me ka maʻi Hughes ʻaʻole lākou e hōʻike i nā ʻōuli o ke kīʻaha koko a ʻaʻole e koi i nā lāʻau lapaʻau ma ʻō aku o ka aspirin e pale ai i ka pilikia o ka ulu ʻana o ka maʻi.

Hiki ke kuhikuhi ʻia nā lāʻau anticoagulant, e like me warfarin (Coumadin), keu hoʻi inā he moʻolelo kou o ka thrombosis hohonu.

Inā ʻoe e hoʻāʻo e hāpai i kahi hāpai hāpai a hiki i ka manawa a loaʻa iā Hughes syndrome, hiki ke kuhikuhi ʻia ʻoe i kahi aspirin haʻahaʻa haʻahaʻa a i ʻole i kēlā me kēia lā o ka heparin lahilahi o ke koko.

ʻO nā wahine me ka maʻi Hughes he 80 pākēneka ka nui o ka hāpai ʻana i kahi pēpē a hiki i ka wā e ʻike ʻia a hoʻomaka lākou i kahi lāʻau maʻalahi.

ʻO kaʻai a me ka hoʻoikaika kino no ka maʻi ʻo Hughes

Inā kuhi ʻia ʻoe me ka maʻi Hughes, hiki i kahi papaʻai olakino ke hōʻemi i kou makaʻi ʻana i nā pilikia kūpono, e like me ka hahau ʻana.

ʻO ka ʻai ʻana i kahi papaʻai momona i nā huaʻai a me nā mea kanu a me ka momona o nā momona trans a me nā kō e hāʻawi iā ʻoe i kahi ʻōnaehana cardiovascular olakino olakino, e hoʻemi ana i ke kahe o ke koko.

Inā ʻoe e mālama nei i ka maʻi ʻo Hughes me warfarin (Coumadin), aʻoaʻo ka Mayo Clinic iā ʻoe e kūlike me ka nui o ka lāʻau K e ʻai ai.

ʻOiai ka hopena o ka nui o nā huaora K i kāu mālama ʻana, e loli mau ana i kāu lawe ʻana i ka wikamina K hiki ke hoʻololi i kāu lāʻau pono. ʻO Broccoli, Brussels sprouts, garbanzo beans, a me ka avocado kekahi o nā meaʻai i kiʻekiʻe i ka huaʻai K.

ʻO ka loaʻa ʻana o ka hoʻoikaika kino mau hiki ke lilo i ʻāpana o ka mālama ʻana i kāu kūlana. Hōʻalo i ka puhī ʻana a mālama i kahi kaupaona olakino no kou ʻano o ke kino e mālama i kou puʻuwai a me nā uaua ikaika a pale aku i ka hōʻino.

ʻO ka nānā aku

No ka hapanui o ka poʻe me ka maʻi Hughes, hiki ke mālama ʻia nā hōʻailona a me nā ʻōuli me nā mea lahilahi o ke koko a me nā lāʻau anticoagulant.

Aia kekahi mau hihia kahi i kūpono ʻole ai kēia mau ʻano hana, a pono e hoʻohana ʻia nā ʻano hana ʻē aʻe e kāohi ʻole ai i kou koko.

Inā haʻalele ʻole ʻia, hiki i ka maʻi ʻo Hughes ke hōʻino i kāu ʻōnaehana puʻuwai a hoʻonui i kou makaʻi no nā kūlana olakino ʻē aʻe, e like me ka hāʻule ʻana o ka maʻi a me ka hahau ʻana. ʻO ka mālama ʻana i ka maʻi ʻo Hughes ke ola a pau, no ka mea ʻaʻohe lāʻau lapaʻau no kēia ʻano.

Inā loaʻa iā ʻoe kekahi o kēia mau mea, e kamaʻilio me kāu kauka e pili ana i ka hoʻāʻo ʻana no ka maʻi Hughes:

  • ʻoi aku ka nui o nā kahe koko i hōʻoia i nā pilikia
  • hoʻokahi a ʻoi paha nā hāʻule ma hope o ka hebedoma 10 o ka hāpai keiki
  • ʻekolu a ʻoi paha ʻo nā miscarriages mua i ka trimester mua o ka hāpai keiki

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