Mea Kākau: Eugene Taylor
Lā O Ka Hana: 14 Aukake 2021
HōʻAno Hou I Ka Lā: 18 Iune 2024
Anonim
Haemolytic Uraemic Syndrome
Wikiō: Haemolytic Uraemic Syndrome

Anter

He aha ka Hemolytic Uremic Syndrome?

ʻO kahi hemolytic uremic syndrome (HUS) kahi ʻano paʻakikī kahi e loaʻa ai kahi hopena pale, ʻo ka mea maʻamau ma hope o ka maʻi o ka gastrointestinal tract, e hoʻohaʻahaʻa i nā pae o ke koko ʻulaʻula, nā pae platelet haʻahaʻa, a me nā hōʻeha puʻupaʻa.

ʻO nā maʻi o ka gastrointestinal tract (kou ʻōpū a me kou ʻōpū) ʻo ia ke kumu maʻamau o kēia maʻi. Hana ke ʻōnaehana pale o ke kino i nā toxins i hoʻokuʻu ʻia i ka wā o ka maʻi koʻohune o ka ʻōpū. ʻO kēia ke kumu o ka hōʻino a me ka luku ʻana i nā huna koko ke kaapuni ʻia i loko o nā kīʻaha koko. Hoʻopili kēia i nā hunaola ʻulaʻula (RBC) a me nā platelet, e make ai i ka wā mua. Hoʻopili ʻia ka hakuʻala i loko o nā ʻano ʻelua. ʻOkoʻa, kahi kūkulu ʻana o RBC i hoʻopau ʻia a i ʻole platelet hiki ke pale i ka ʻōnaehana kānana o ka puʻupaʻa a hōʻeha i nā puʻupaʻa a i ʻole ke kūkulu ʻia ʻana o nā huahana neoneo i ke kino, ʻoiai ʻaʻole hiki i ka puʻupaʻa ke hoʻopau pono i nā ʻōpala mai ke koko.


Hiki ke hōʻeha loa ka ʻeha puʻuwai inā haʻalele ʻole ʻia. ʻO nā kōpaʻa maikaʻi ʻole, nā kiʻekiʻe weliweli i ke kahe o ke koko, nā pilikia o ka puʻuwai, a me ka hahau nā hopohopo āpau inā kū i mua ʻo HUS me ka ʻole o ka lapaʻau koke.

ʻO HUS ke kumu maʻamau o ka hōʻino kīwī ʻole i nā keiki.ʻO ka mea maʻamau i nā keiki ma lalo o ka makahiki 5, ʻoiai hiki i nā keiki nui a me nā mākua ke ʻeha pū i kēia maʻi.

ʻO ka mea pōmaikaʻi, ʻo ka hapanui o ka poʻe i loaʻa i ka lāʻau lapaʻau koke hiki ke hoʻōla hou me ka ʻole o ka hōʻino mau o ka hakuʻala.

ʻIke i nā ʻōuli o Hemolytic Uremic Syndrome

ʻOkoʻa nā ʻōuli o HUS. Hiki i nā ʻōuli ke hoʻopili pū me:

  • ʻōpū koko
  • abdominal eha
  • ʻili mae
  • ukiuki
  • luhi
  • fiva
  • ʻehaʻeha ʻole a hoʻokahe koko paha
  • hoʻemi urination
  • ʻōpū ʻōpū
  • koko i ka mimi
  • huikau
  • ka luaʻi
  • helehelena pehu
  • nā lālā pehu
  • ka hopu (ʻike ʻole ʻia)

He aha ke kumu o Hemolytic Uremic Syndrome?

HUS kahi kahi hopena immune e hōʻino ai i nā hunaola koko. ʻO kēia ka hopena i nā pae o ke koko ʻulaʻula haʻahaʻa, nā pae platelet haʻahaʻa, a me nā hōʻeha puʻupaʻa


HUS i nā Keiki

ʻO ke kumu kumu pinepine o HUS i nā keiki ka maʻi maʻi EscherichiaʻO Coli (E. coli). Nui nā ʻano like ʻole o E. coli, a ʻaʻole pilikia ka hapa nui. I ka 'oiaʻiʻo, E. coli ʻike mau ʻia ka bacteria i loko o nā ʻōpū o nā kānaka olakino a me nā holoholona. Eia nō naʻe, kekahi mau ʻano kikoʻī o E. coli, hala ma waena o nā meaʻai haumia, nā kuleana no nā maʻi i hiki ke alakaʻi iā HUS. Nā kino o nā wai i haumia me nā feces e halihali pū kekahi E. coli.

Nā bacteria ʻē aʻe e like me ʻO Shigelladisenteriae a ʻO Salmonella typhi hiki iā HUS.

HUS i nā mākua

HUS i nā mākua hiki ke hoʻonāukiuki ʻia e ka maʻi maʻi me E. coli.. Nui a hewahewa nā kumu o ka HUS ma nā mākua i emi ʻole ka nui, e like me:

  • hāpai keiki
  • Maʻi maʻi HIV / AIDS
  • quinine (hoʻohana ʻia no ka cramp Muscle)
  • chemotherapy a me ka lāʻau pale maʻi
  • lāʻau hoʻomalu hānau
  • nā lāʻau pale anti-platelet
  • maʻi ʻaʻai
  • lupus ʻōnaehana a me glomerulonephritis

Nānā i ka Hemolytic Uremic Syndrome

Hiki ke kauoha ʻia kekahi mau hoʻokolohua maʻalahi loa e hoʻoholo inā ua hōʻino ʻia nā huna koko a i ʻole a hōʻino ʻia ka hana o ka hakuʻala.


CBC

Kuhi kahi helu piha i ke koko (CBC) i ka nui a me ka maikaʻi o nā RBC a me nā platelet i kahi hāpana koko.

Nā ho'āʻo koko ʻē aʻe

I mea e hoʻāʻo ai no ka nalo ʻana o ka hana hakuʻala, hiki i kāu kauka ke kauoha i kahi hōʻike BUN (kahi e nānā ai no nā huahana urea kiʻekiʻe) a me ka hoʻāʻo creatinine (e ʻimi ana i nā huahana kiʻekiʻe nā mākala i hoʻokiʻekiʻe ʻia). Hiki i nā hopena maʻamau ke hōʻike i nā pilikia ʻōpū.

Hōʻike Mīkini

Makemake kāu kauka e hoʻāʻo no ke koko a i ʻole protein i loko o kāu mimi.

Laʻana Sampol

ʻO ke koʻohune a i ʻole ke koko i loko o kāu pahu ka mea hiki ke kōkua i kāu kauka e hoʻokaʻawale i ke kumu kumu o kāu mau ʻōuli.

Pehea e mālama ʻia ai ka Hemolytic Uremic Syndrome?

Hiki i nā hana maʻamau no HUS ke:

Hoʻololi hou

ʻO ke kī nui no HUS ka hoʻololi wai. Hoʻololi kēia hana i nā electrolytes e pono ai ke kino e hana. ʻO nā electrolytes nā minelala e like me ka calcium, potassium, a me ka magnesium. Hoʻonui pū ka hoʻololi o ka wai i ke kahe o ke koko ma o nā puʻupaʻa .. E hāʻawi kāu kauka iā ʻoe i nā wai i loko o ke kino, akā e paipai paha iā ʻoe e hoʻonui i kāu lawe wai i ka inu ʻana i nā wai a i ʻole nā ​​electrolyte solution.

Hoʻohuli Koko

Pono paha kahi transfusion koko ʻulaʻula inā he pae haʻahaʻa kou o nā RBC. Hana ʻia nā transfusion i ka haukapila. Hiki i nā transfusions ke hoʻokuʻu i nā hōʻailona e pili ana i nā helu RBC haʻahaʻa, e like me ka hanu ʻana a me ka luhi nui loa.

Kūlike kēia mau ʻōuli me ka anemia, kahi ʻano i hiki ʻole i kou kino ke hoʻohua i nā hunaola ʻulaʻula e lawa i nā kino o ke kino me ka lawa o ka oxygen e lawe i ka metabolism maʻamau. ʻO kēia ka hopena o ka lilo o RBC's.

Nā Hana ʻē aʻe

Lawe aku kāu kauka iā ʻoe mai nā lāʻau i hiki ke lilo i kumu kumu o HUS.

Pono paha ka transfusion platelet inā he helu platelet haʻahaʻa kāu.

ʻO ka pānaʻi Plasma kahi ʻano lapaʻau ʻē aʻe, kahi e kau ai kāu kauka i kāu plasma koko me ka plasma mai kahi mea hāʻawi. E loaʻa iā ʻoe ka plasma olakino maikaʻi e kākoʻo i ka holo ʻana o ke olakino, nā ʻulaʻula hou a me nā pā.

He aha nā pilikia kūpono no ka Hemolytic Uremic Syndrome?

I nā hihia koʻikoʻi inā ʻaʻole i hoʻokō kāu mau puʻupaʻa, hiki ke hoʻohana ʻia ka dialysis kidney e kānana i nā ʻōpala mai kou kino. He lāʻau kūlohelohe kēia a hiki i nā puʻupaʻa ke hana maʻamau. Inā ʻaʻole lākou e loaʻa hou i ka hana maʻamau, pono ʻoe i kahi transplant kidney.

Nā Hoʻohuli Lōʻihi

ʻO ka pilikia nui o HUS ka hōʻole ʻana o ka hakuʻala. Eia nō naʻe, hiki iā HUS ke kumu:

  • kahe koko kiʻekiʻe
  • pancreatitis
  • ke kūlana noʻonoʻo i hoʻololi ʻia
  • ka hopu ʻana
  • cardiomyopathy
  • hahau
  • koma

ʻO ka mea pōmaikaʻi, hiki i ka hapanui o ka poʻe ke hoʻōla hou iā HUS.

He aha ka manaʻo no Hemolytic Uremic Syndrome?

He kūlana ʻoi loa paha ʻo HUS. Eia nō naʻe, e hana ʻoe i kahi ola hou inā ʻike ʻia ʻoe i nā wā mua o ke ʻano a hoʻomaka koke i ka lāʻau. Kāhea i kāu kauka i nā manawa āpau e hoʻomohala i nā hōʻailona āu e hopohopo nei.

Pehea e hiki ai iā ʻoe ke pale aku i ka Hemolytic Uremic Syndrome?

ʻO ke kumu maʻamau o ka HUS nā maʻi e E. coli. ʻOiai ʻaʻole hiki iā ʻoe ke hōʻalo i kēia mau koʻohune āpau, hiki iā ʻoe ke hōʻemi i kāu makaʻu o ka maʻi i:

  • holoi lima mau
  • holoi holoi i nā pono
  • mālama i ka hoʻomaʻemaʻe o nā papa hoʻomākaukau meaʻai
  • ka mālama ʻana i ka ʻai maka mai ka mea ʻai mākaukau
  • hoʻowahāwahā i ka ʻiʻo i loko o ka pahu hau ma kahi o ka pā
  • haʻalele ʻole i ka ʻiʻo i ke ana wela o ka lumi (hiki i kēia ke ulu i ka bacteria).
  • ke kuke ʻana i ka ʻiʻo i 160 kekelē Fahrenheit e pepehi i nā maʻi koʻohune
  • holoi pono ʻana i nā huaʻai a me nā lauʻai
  • ʻauʻau ʻole i ka wai haumia
  • e hōʻalo nei i ka lawe ʻana i ka wai momona a waiū ʻole paha

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