Mea Kākau: Robert Simon
Lā O Ka Hana: 21 Iune 2021
HōʻAno Hou I Ka Lā: 20 Iune 2024
Anonim
Understanding Guillain-Barré Syndrome
Wikiō: Understanding Guillain-Barré Syndrome

Anter

He aha ka maʻi ʻo Guillain-Barré?

He maʻi laha ʻole ʻo Guillain-Barré Syndrome akā ʻo ka maʻi autoimmune koʻikoʻi kahi e hoʻouka ai ka ʻōnaehana pale i nā pūnaewele nerve olakino i loko o kāu ʻōnaehana makaʻu ākea (PNS).

ʻO kēia ke alakaʻi i ka nāwaliwali, numbness, a me ka tingling, a hiki i ka hopena ke kumu i ka maʻi lōlō.

ʻAʻole ʻike ʻia ke kumu o kēia ʻano, akā hoʻomaka pinepine ʻia ia e kahi maʻi lele, e like me gastroenteritis (ka huhū o ka ʻōpū a me nā ʻōpū) a i ʻole ka maʻi ʻaʻa.

Kākaʻikahi ʻo Guillain-Barré, e pili ana ma kahi o 1 wale nō ma 100,000 mau ʻAmelika, e like me ka National Institute of Neurological Disorder and Stroke.

ʻAʻohe lāʻau lapaʻau no ka maʻi, akā hiki i ka lapaʻau ke hōʻemi i ke koʻikoʻi o kāu mau hōʻailona a hōʻemi i ka lōʻihi o ka maʻi.

Nui a hewahewa nā ʻano o Guillain-Barré, akā ʻo ka ʻano maʻamau ka polyradiculoneuropathy (CIDP) ākea e hoʻoulu ai i ka maʻi. ʻO ka hopena i ka hōʻino ʻia o myelin.

ʻO nā ʻano ʻē aʻe e pili pū ana me ka maʻi maʻi ʻo Miller Fisher, kahi e hoʻopili ai i nā ʻalalona cranial.


He aha ke kumu o ka maʻi o Guillain-Barré?

ʻAʻole ʻike ʻia ke kumu kikoʻī o Guillain-Barré. Wahi a ka, ma kahi o ʻelua hapakolu o ka poʻe me Guillain-Barré e hoʻomōhala ia ma hope koke iho o ko lākou maʻi ʻana me ka maʻi pākī a i ʻole ka maʻi hanu.

Hōʻike kēia i kahi pane pale ʻole kūpono ʻole i nā maʻi ma mua e hoʻonāukiuki i ka maʻi.

Campylobacter jejuni ua pili ka maʻi maʻi me Guillain-Barré. Campylobacter ʻo ia kekahi o nā kumu maʻi bacteria maʻamau o ka maʻi diarrhea i ʻAmelika Hui Pū ʻIa. ʻO ia nō hoʻi ka mea nui pilikia no Guillain-Barré.

Campylobacter ʻike pinepine ʻia i nā meaʻai undercooked, ʻoi aku ka moa.

Ua pili pū kekahi nā maʻi aʻe me Guillain-Barré:

  • maʻi palū
  • cytomegalovirus (CMV), kahi kānana o ka maʻi herpes
  • ʻO ka maʻi Epstein-Barr (EBV) maʻi, a i ʻole mononucleosis
  • mycoplasma pneumonia, ʻo ia kahi maʻi ākea ʻole i hana ʻia e nā meaola like bacteria
  • ʻO HIV a ʻo AIDS paha

Hiki i kēlā me kēia mea ke kiʻi iā Guillain-Barré, akā ʻoi aku ka nui ma waena o nā ʻelemākule.


I nā hihia maʻamau loa, hiki i nā kānaka ke hoʻomohala i ka lā maʻi a i ʻole mau pule ma hope o ka loaʻa ʻana iā.

Aia ka CDC a me ka Food and Drug Administration (FDA) i nā ʻōnaehana i kahi e nānā ai i ka palekana o nā lāʻau āpau, e ʻike i nā ʻōuli mua o nā hopena ʻaoʻao, a hoʻopaʻa i nā hihia o Guillain-Barré e hoʻomohala ma hope o kahi wī.

ʻO ka CDC e hōʻike ana ka noiʻi e loaʻa paha iā Guillain-Barré mai ka maʻi flu, ma mua o ka lāʻau lapaʻau.

He aha nā hōʻailona o Guillain-Barré Syndrome?

I ka maʻi ʻo Guillain-Barre, hoʻouka kāu ʻōnaehana pale pale i kāu ʻōnaehana makaʻu ākea.

Hoʻopili nā aʻalolo i loko o kāu ʻōnaehana nūhou i kou lolo i ke koena o kou kino a hoʻouna i nā hōʻailona i kou mau mākala.

ʻAʻole hiki i nā mākala ke pane i nā hōʻailona i loaʻa iā lākou mai kou lolo inā e hōʻino ʻia kēia mau aʻalolo.

'O ka hōʻailona mua he manaʻo nui i kou manamana wāwae, mau wāwae, a me nā wāwae. Hoʻolahalaha ke kani i luna i kou mau lima a me kou mau manamana lima.

Hiki ke holo wikiwiki i nā ʻōuli. I kekahi poʻe, hiki i ka maʻi ke lilo i koʻikoʻi i loko o kekahi mau hola.


ʻO nā ʻōuli o Guillain-Barré me:

  • ʻoniʻoni a prickling paha i kou manamana lima a me kou manamana wāwae
  • nāwaliwali o nā mākala i kou mau wāwae e hele i kou kino luna a lilo i mea ʻoi aku ka maikaʻi ma mua o ka manawa
  • paʻakikī e hele wāwae paʻa
  • paʻakikī e hoʻoneʻe i kou mau maka a i ʻole alo, e kamaʻilio, e nau, a e ale paha
  • ʻehaʻeha hope loa
  • lilo o ka mana o ka ʻaʻa
  • wikiwiki o ka puʻuwai
  • paʻakikī i ka hanu ʻana
  • lolo

Pehea i loaʻa ai ka maʻi ʻo Guillain-Barré?

He paʻakikī ʻo Guillain-Barré e hōʻoia mua. ʻO kēia no ka mea like like nā ʻōuli me nā maʻi neurological ʻē aʻe a i ʻole nā ​​kūlana e hoʻopili i ka ʻōnaehana hopohopo, e like me botulism, meningitis, a me nā lāʻau make kaumaha.

Hoʻokumu ʻia ka lāʻau make kaumaha ma muli o nā mea e like me kēpau, mercury, a me arsenic.

E nīnau ana kāu kauka e pili ana i nā hōʻailona kikoʻī a me kāu mōʻaukala olakino. E hoʻomaopopo pono e haʻi aku i kāu kauka e pili ana i nā ʻōuli maʻamau a inā loaʻa iā ʻoe nā maʻi i hala a hala paha i hala a i ʻole nā ​​maʻi.

Hoʻohana ʻia nā hōʻike aʻe e kōkua i ka hōʻoia ʻana i kahi kuhi.

Piula ʻōiwi

Hoʻopili ke kuamoʻo (lumbar puncture) i ka lawe ʻana i kahi wai liʻiliʻi mai kou iwikuamoʻo i kou ʻaoʻao haʻahaʻa. Kapa ʻia kēia wai i ka wai cerebrospinal. Hōʻike ʻia kāu wai cerebrospinal e ʻike i nā pae protein.

Loaʻa ka poʻe me Guillain-Barré i nā kiʻekiʻe o nā protein i loko o kā lākou wai cerebrospinal.

Uila uila

ʻO kahi electromyography kahi hōʻike hana nerve. Heluhelu ia i ka hana uila mai nā mākala e kōkua i kāu kauka e aʻo inā pili kou nawaliwali i ka nāwaliwali o ke aʻa a i ʻole nā ​​ʻino.

Nā hoʻāʻo conduction nerve

Hiki ke hoʻohana ʻia nā haʻawina conduction nerve e hōʻoia i ka maikaʻi o ka pane ʻana o nā ʻalolo a me nā mākala i nā puʻupuʻu uila liʻiliʻi.

Pehea e mālama ʻia ai ka maʻi ʻo Guillain-Barré?

ʻO Guillain-Barré kahi hana hoʻoweliweli autoimmune e kaohi ana iā ia iho, ʻo ia hoʻi e hoʻonā iā ia iho. Eia nō naʻe, ʻo kēlā me kēia ʻano e lawe i ka haukapila no ka nānā pono ʻana. Hiki ke hōʻino koke nā ʻōuli a hiki ke make inā mālama ʻole ʻia.

I nā hihia koʻikoʻi, hiki i ka poʻe me Guillain-Barré ke hoʻomohala i ka lolo āpau. Hiki iā Guillain-Barré ke hoʻoweliweli i ke ola inā pili ka paralysis i ka diaphragm a i ʻole nāʻiʻo o ka umauma, e pale ana i ka hanu kūpono.

ʻO ka pahuhopu o ka mālama ʻana e hoʻemi i ka nui o ka hōʻeha pale a kākoʻo i nā hana o kou kino, e like me ka hana o ka māmā, ʻoiai e loaʻa hou ana kāu ʻōnaehana.

Hiki i nā mālama ke hoʻopili:

Plasmapheresis (pānaʻi plasma)

Hoʻopuka ka ʻōnaehana pale pale i nā protein i kapa ʻia he antibodies e hoʻouka maʻamau i nā mea haole weliweli, e like me nā bacteria a me nā mea ʻino. Kū ʻo Guillain-Barré ke hana kuhi hewa kāu ʻōnaehana pale i nā ʻalopa e hoʻouka i nā ʻalolo olakino o kāu ʻōnaehana.

Hoʻolako ʻia ʻo Plasmapheresis e hemo i nā mea ʻino e hoʻouka ana i nā aʻalolo o kou koko.

I kēia kaʻina hana, lawe ʻia ke koko mai kou kino e kahi mīkini. Lawe kēia mīkini i nā mea ʻino mai kou koko a hoʻi mai i ke koko i kou kino.

Immunoglobulin i loko o ke kino

Hiki i nā lāʻau kiʻekiʻe o immunoglobulin ke kōkua i ka pale ʻana i nā mea ʻino i hiki iā Guillain-Barré. Loaʻa i ka Immunoglobulin nā antibodies olakino olakino olakino mai nā mea hāʻawi.

ʻO ka Plasmapheresis a me ka immunoglobulin intravenous e like ka hopena. Aia iā ʻoe a me kāu kauka ke hoʻoholo i ka lāʻau ʻoi loa.

Nā lapaʻau ʻē aʻe

Hāʻawi ʻia ʻoe i ka lāʻau e hōʻoluʻolu i ka ʻeha a pale i nā kahe koko ke ʻole ʻoe e neʻe.

E loaʻa paha iā ʻoe ka lāʻau hoʻoikaika kino a me ka ʻoihana hana. I ka wā koʻikoʻi o ka maʻi, e hoʻoneʻe ka poʻe mālama i kou mau lima a me kou mau wāwae e maʻalahi.

Ke hoʻomaka hou ʻoe e ola, e hana pū nā mea hoʻoponopono me ʻoe i ka hoʻoikaika ʻana i nā mākala a me nā ʻano o nā hana o kēlā me kēia lā nohona (ADLs). Hiki i kēia ke komo i nā hana mālama pilikino, e like me ka lole ʻana.

He aha nā pilikia kūpono o Guillain-Barré Syndrome?

Hoʻopili ʻo Guillain-Barré i kou aʻa. Hiki i ka nāwaliwali a me ka maʻi lōlō ke hoʻopili i nā ʻāpana he nui o kou kino.

Komo pū ka pilikia i ka hanu paʻakikī ke laha ka lōlō a nāwaliwali paha i nā mākala e kaohi ana i ka hanu. Pono paha ʻoe i kahi mīkini i kapa ʻia he respirator e kōkua iā ʻoe e hanu inā kū kēia.

Hiki i nā pilikia ke hoʻopili pū:

  • nāwaliwali lōʻihi, numbness, a i ʻole nā ​​ʻano ʻē aʻe ʻē aʻe ma hope o ka hoʻōla ʻana
  • nā pilikia puʻuwai a i ʻole ke koko
  • ʻeha
  • lohi ka ʻōpū a me ka hana o ka ʻai
  • nā maʻi koko a me nā bedores ma muli o ka paralysis

He aha ka manaʻo lōʻihi?

ʻO ka wā hoʻōla no Guillain-Barré hiki ke lōʻihi, akā hoʻōla ka hapa nui o ka poʻe.

Ma ka laulaha, eʻoi aku ka maikaʻi o nā ʻōuli no ʻelua a ʻehā mau pule ma mua o ka paʻa. Hiki i ka hoʻōla ke lawe ma nā wahi āpau mai kekahi mau pule a i kekahi mau makahiki, akā ʻo ka hapanui e ola i 6 a 12 mau mahina.

Ma kahi o 80 pākēneka o ka poʻe i hoʻopilikia ʻia e Guillain-Barré hiki ke hele kūʻokoʻa i ʻeono mau mahina, a he 60 pākēneka e hoʻihoʻi i ko lākou ikaika maʻa mau i hoʻokahi makahiki.

No kekahi, ʻoi aku ka lōʻihi o ke ola ʻana. Ma kahi o 30 pākēneka ʻike mau i kekahi nāwaliwali ma hope o ʻekolu mau makahiki.

Ma kahi o 3 pākēneka o ka poʻe i hoʻopilikia ʻia e Guillain-Barré e ʻike i ka hoʻi hou ʻana o kā lākou mau hōʻailona, ​​e like me ka nāwaliwali a me ke kaniʻū, ʻoiai he mau makahiki ma hope o ka hanana kumu.

I nā hihia kakaikahi, hiki ke hoʻoweliweli i ke ʻano, keu hoʻi inā ʻaʻole ʻoe e lapaʻau. Nā kumu i alakaʻi i kahi hopena maikaʻi ʻole e hoʻopili ʻia:

  • makahiki kiʻekiʻe
  • maʻi nui a i ʻole holomua holomua
  • lohi o ka lāʻau ʻana, a laila hiki i kēia ke hopena i nā mea ʻino hou aʻe
  • hoʻohana hoʻolōʻihi ʻia o kahi hanu, ka mea hiki ke predispose iā ʻoe i ka niumonia

Hiki ke hoʻemi ʻia ke koko a me nā bedores i loaʻa i ka immobilized. Hiki i nā mea lahilahi a me nā lāʻau kaohi ke hoʻoliʻiliʻi i ka hoʻopili ʻana.

ʻO ka hoʻonohonoho pinepine ʻana i kou kino e hoʻomaha i ke kaomi o ke kino hoʻolōʻihi e hiki ai i ka haʻihaʻi o nā kiko, a i ʻole nā ​​bedores.

Ma waho aʻe o kāu mau hōʻailona kino, ʻike paha ʻoe i nā pilikia o ka naʻau. Hiki iā ia ke lilo i mea paʻakikī e hoʻoponopono i ka neʻe palena ʻia a me ka hilinaʻi nui ʻana i nā poʻe ʻē aʻe. E ʻike paha ʻoe he mea kōkua ke kamaʻilio pū me kahi kauka.

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