Hema G6PD

Anter

• He aha nā hōʻailona o ka hemahema G6PD?
• He aha ke kumu o ka nele o G6PD?
• He aha nā mea pilikia no ka hemahema G6PD?
• Pehea ka hemahema o ka ʻike G6PD?
• Pehea e mālama ai i ka hemahema G6PD?
• He aha ka manaʻo no kekahi me ka hemahema G6PD?

He aha ka hemahema G6PD?

ʻO ka hemahema G6PD kahi kino kīnā ʻole e hopena i ka lawa ʻole o ka glucose-6-phosphate dehydrogenase (G6PD) i loko o ke koko. He enzyme nui (a protein paha ia) e hoʻoponopono i nā hopena biochemical i loko o ke kino.

ʻO G6PD ke kuleana no ka mālama ʻana i nā hunaola ʻulaʻula i ke olakino i hiki ai iā lākou ke hana pono a ola i kahi ola maʻamau. Me ka lawa ʻole o ia mea, e haki mua ke koko ʻulaʻula. ʻIke ʻia kēia luku mua ʻana o nā hunaola ʻulaʻula hemolisis, a hiki iā ia ke alakaʻi i hemolytic anemia.

E ulu ka anemia hemolytic ke luku ʻia nā hunaola ʻulaʻula ma mua o ka hiki i ke kino ke pani iā ​​lākou, a laila e hoʻemi ana i ka holo ʻana o ka oxygen i nā meaola a me nā aʻa. Hiki i kēia ke kumu i ka luhi, melemele o ka ʻili a me nā maka, a me ka hanu liʻiliʻi.

I ka poʻe me ka hemahema G6PD, hiki ke anemia hemolytic ma hope o ka ʻai ʻana i nā pī fava a i ʻole kekahi mau legume. Hoʻomaka ʻia paha ia e nā maʻi a i ʻole kekahi mau lāʻau, e like me:

• antimalarials, kahi ʻano lāʻau i hoʻohana ʻia e pale a mālama i ka malaria
• sulfonamides, kahi lāʻau i hoʻohana ʻia no ka mālama ʻana i nā maʻi like ʻole
• aspirin, he lāʻau i hoʻohana ʻia no ka hoʻōla ʻana i ke kuni, ka ʻeha, a me ka pehu ʻana
• kekahi mau lāʻau anti-inflammatory nonsteroidal (NSAIDs)

Hoʻonui nui ʻia ka hemahema G6PD ma ʻApelika, kahi e hiki ai ke hoʻopili a 20 pākēneka o ka heluna kānaka. ʻOi aku ka maʻamau o ke kūlana i nā kāne ma mua o ka wahine.

ʻO ka hapa nui o ka poʻe me ka hemahema G6PD ʻike pinepine ʻole i kekahi ʻōuli. Eia nō naʻe, hiki i kekahi ke hoʻomohala i nā ʻōuli ke hōʻike ʻia lākou i ka lāʻau, ka meaʻai, a i ʻole ka maʻi e hoʻonāukiuki i ka luku mua o nā hunaola ʻulaʻula. I ka manawa e mālama ʻia a hoʻoholo ʻia paha ke kumu kumu, nalowale pinepine nā ʻōuli o ka hemahema G6PD i loko o kekahi mau pule.

He aha nā hōʻailona o ka hemahema G6PD?

Hiki i nā ʻōuli o ka hemahema G6PD ke hoʻopili pū me:

• kōmi puʻuwai wikiwiki
• pokole o ka hanu
• mimi ʻeleʻele a melemele-ʻalani paha
• fiva
• luhi
• ʻūpā
• paleness
• jaundice, a melemele paha o ka ʻili a keʻokeʻo o nā maka

He aha ke kumu o ka nele o G6PD?

ʻO ka hemahema G6PD kahi ʻano kūlohelohe i hala ʻia mai hoʻokahi a i ʻole ʻelua mau mākua i kā lāua keiki. ʻO ka gen defective ke kumu o kēia hemahema ma ka X chromosome, ʻo ia kekahi o nā chromosome wahine ʻelua. Hoʻokahi wale nō chromosome X o nā kāne, ʻoiai he ʻelua mau chromosome X i nā wahine. I nā kāne, ua lawa hoʻokahi kope i hoʻololi ʻia o ka moʻo e hana i ka hemahema G6PD.

I nā wahine naʻe, aia kahi hoʻololi i nā kope ʻelua o ka ʻāpana. Ma muli o ka liʻiliʻi o ka loaʻa ʻana o nā kope wahine ʻelua i hoʻololi ʻia o kēia moʻo, hoʻopili ʻia nā kāne e ka hemahema G6PD ʻoi aku ka nui ma mua o nā wahine.

He aha nā mea pilikia no ka hemahema G6PD?

Hiki paha iā ʻoe ke kiʻekiʻe aʻe i ka loaʻa ʻole o ka G6PD hemahema inā ʻoe:

• he kāne
• he ʻApelika-ʻAmelika
• he mamo lākou ma ka Hikina Waena
• he moʻolelo ʻohana ko kēia ʻano

Ke loaʻa nei i hoʻokahi a ʻoi paha o kēia mau kumuhana pilikia ʻaʻole ia he kumu e loaʻa ai iā ʻoe ka hemahema G6PD. E kamaʻilio me kāu kauka inā hopohopo ʻoe i kou makaʻi no kēia ʻano.

Pehea ka hemahema o ka ʻike G6PD?

Hiki i kāu kauka ke hōʻoia i ka hemahema G6PD ma o ka hana ʻana i kahi hoʻokolohua koko maʻalahi e nānā i nā pae enzyme G6PD.

ʻO nā hoʻokolohua diagnostical ʻē aʻe i hana ʻia e like me ka helu piha o ke koko, ka hemoglobin serum, a me ka helu retikulosit. Hāʻawi kēia mau hōʻike āpau i ka ʻike e pili ana i nā hunaola ʻulaʻula i ke kino. Hiki iā lākou ke kōkua i kāu kauka e hōʻoia i ka hemolytic anemia.

I kou wā i koho ʻia, he mea nui e haʻi i kāu kauka e pili ana i kāu papaʻai a me nā lāʻau āu e lawe nei. Hiki i kēia mau kikoʻī ke kōkua i kāu kauka me ka hōʻailona.

Pehea e mālama ai i ka hemahema G6PD?

ʻO ka mālama ʻana no ka hemahema G6PD o ka hemo ʻana i ka mea hoʻouluulu e hoʻomaka nei i nā ʻōuli.

Inā ua hoʻonā ʻia ke ʻano e ka maʻi, a laila mālama ʻia ka maʻi maʻi ma muli. ʻO nā lāʻau i kēia manawa e luku paha i nā hunaola ʻulaʻula e hoʻopau ʻia hoʻi. I kēia mau hihia, hiki i ka hapanui o ka poʻe ke ola mai kahi ʻāpana i kā lākou iho.

I ka manawa e holomua ai ka hemahema o G6PD i hemolytic anemia, akā naʻe, koi ʻia kahi lapaʻau ʻoi loa. Hoʻopili kēia i kekahi manawa i ka oxygen therapy a me ka hoʻololi koko e hoʻopiha i ka oxygen a me nā pae o ke koko ʻulaʻula.

Pono ʻoe e noho i ka haukapila ʻoiai ke loaʻa ʻana o kēia mau ʻano hana, ʻoiai ke kiaʻi pono loa ʻana i ka hemolytic anemia koʻikoʻi no ka hōʻoia ʻana i ke ola piha me ka ʻole o nā pilikia.

He aha ka manaʻo no kekahi me ka hemahema G6PD?

Nui a hewahewa ka poʻe me ka hemahema G6PD. ʻO ka poʻe e ola pono loa mai kā lākou mau ʻōuli ke loaʻa ka lāʻau no ke kumu o ke ʻano o ka maʻi. Eia nō naʻe, he mea nui e aʻo pehea e hiki ai iā ʻoe ke mālama i ke ʻano a pale i nā hōʻailona mai ka hoʻomohala ʻana.

ʻO ka mālama ʻana i ka hemahema G6PD e pili ana i ka hōʻalo ʻana i nā meaʻai a me nā lāʻau i hiki ke hoʻoulu i ke ʻano. Hiki ke kōkua i ka hōʻemi ʻana i nā pae koʻikoʻi i ke kaohi ʻana i nā ʻōuli. E noi i kāu kauka no kahi papa inoa i paʻi ʻia o nā lāʻau a me nā meaʻai āu e hōʻalo ai.