He aha nā ala Müller

Anter
- Pehea lākou e hoʻomohala ai
- He aha nā pilikia
- 1. ʻO Rokitansky-Kuster-Hauser maʻi
- 2. Unicorn uterus
- 3. Nā pilikia kuʻi hope ālai
- 4. Nā pilikia kuʻi hope ʻole kūpikipiki
- 5. Nā pilikia kuʻihui kūnoa ākea
ʻO nā kahawai ʻo Müller, i ʻike ʻia ma ke ʻano he paramesonephric ducts, aia nā hale i kū i loko o ka embryo a hāpai i nā genitalia kūloko o ka wahine, inā he kaikamahine a noho paha i kona ʻano vestigial, inā he keikikāne.
I nā wahine, hoʻomaka nā kahawai o Müller i nā paipu uterine, ka pūpū a me ka ʻaoʻao luna o ka ʻōpala a i nā kāne, nā hale e hoʻoulu ai i nā mea moekolohe kāne e like me ka epididymis, nā vas deferens a me nā vesicle seminal nā kahe o Wolff, i noho nā wahine i ka vestigial form.

Pehea lākou e hoʻomohala ai
Pili nā auwai a Müller's a me nā dole a Wolff i nā kaohi hormonal:
I loko o ka embryo e hāpai i ka moekolohe kāne, hana ʻia kahi hormone, i kapa ʻia ʻo ka anti-Mullerian hormone, kahi e alakaʻi ai i ka regression o nā muliwai Müller, a laila hana ʻia ka testosterone, i hoʻokuʻu ʻia e nā testicle, kahi e hoʻonāukiuki i ka hoʻokaʻawale ʻana o nā duct. o Wolff.
I ka loaʻa ʻole o ka hana ʻana o kēia mau hormones, i loko o ka embryo wahine, ulu nā duct o Müller, e alakaʻi ana i ka hoʻokaʻawale a me ka hoʻokumu ʻana i nā genital wahine o loko.
He aha nā pilikia
Aia kekahi mau pilikia i hiki ke hana ʻia i ka manawa o ka hoʻokaʻawale ʻana i nā dul Mullerian, hiki i nā anomalies:
1. ʻO Rokitansky-Kuster-Hauser maʻi
Hoʻohālikelike ʻia kēia maʻi e ka loaʻa ʻole o ka pūpū, nā paipu uterine a me ka ʻāpana kiʻekiʻe o ka ʻōpala, eia nō naʻe, hoʻomohala nā ʻano moekolohe ʻelua ma loko ona no ka mea aia mau nā ovaries ma muli o ka hilinaʻi ʻole i nā aʻa Müller e ulu.
Hiki ke hana ʻia nā mea maʻamau ʻole i ka ʻōnaehana urinary a me ka iwi kuamoʻo. ʻAʻole maopopo ia ke kumu o kēia maʻi, a ʻike pinepine ʻia ia i ka wā ʻōpio, ma muli o ka loaʻa ʻole o ka menstruation. E aʻo hou aʻe e pili ana i kēia maʻi, he aha nā hōʻailona a pehea e mālama ai.
2. Unicorn uterus
Manaʻo ʻia e ulu kēia anomaly ma muli o kahi pilikia i ka hoʻomohala ʻia ʻana o kekahi o nā duke a Müller. ʻO ka uterus unicorn e pili ana i ka hapalua o ka nui o ka uterus maʻamau a he hoʻokahi wale nō kōpena uterine, i hiki ke paʻakikī i ka hāpai ʻana.
3. Nā pilikia kuʻi hope ālai
Ke hiki mai nā pilikia fusion lateral, ke ālai ʻia i ka pae o ka cervix a i ʻole ka ʻōpū, a i ka wā makua hiki iā ia ke alakaʻi i nā paʻi menstrual a i ʻole ka endometriosis. I kēia mau hihia, pono paha e hana i kahi hemo septum vaginal obstructive.
4. Nā pilikia kuʻi hope ʻole kūpikipiki
Ke hiki mai nā pilikia kuʻi hope ʻole ʻole, hiki ke hoʻokumu ʻia o kahi utic bicornuate a septate paha, kahi mea e paʻakikī ai ka hāpai ʻana, hāpai i nā hānau hānau mua, hoʻokumu i nā hānau hānau ʻole, a i ʻole kumu kumu hānau ʻole.
5. Nā pilikia kuʻihui kūnoa ākea
Hiki paha i nā pilikia me ka hoʻopili hoʻopili kūpilikiʻi ke kū, kahi e hopena ai ka loaʻa ʻole o kahi ʻōpala, akā ke alo o kahi kōpū, a he mea pono paha e hemo inā ʻaʻole ka cervix.