Mea Kākau: Judy Howell
Lā O Ka Hana: 2 Iulai 2021
HōʻAno Hou I Ka Lā: 21 Iune 2024
Anonim
Clinical Reasoning: A case of ataxia, seizure, and choreoathetosis in a 34-year-old woman
Wikiō: Clinical Reasoning: A case of ataxia, seizure, and choreoathetosis in a 34-year-old woman

Anter

He aha ka choreoathetosis?

ʻO Choreoathetosis kahi maʻi neʻe e hoʻokumu i ka twitching a i ʻole writhing. He kūlana koʻikoʻi ia e hiki ke hoʻopili i kou kūlana, ka hele wāwae, a me ka neʻe o kēlā me kēia lā. Hiki i nā hihia ʻoi aku ke koʻikoʻi ke kumu o ke kīnā mau.

Hoʻohui ʻo Choreoathetosis i nā ʻōuli o chorea a me athetosis. ʻO Chorea ke kumu o ka hōʻoki ʻana i nā mākala e like me ka fidgeting, a i ʻole ka neʻe ʻana o ka lima a me ka wāwae. Hoʻopili ka Chorea i ka maka, nā lālā a me ke kumu o ke kino. Hoʻokumu ke Athetosis i nā neʻe lohi ʻana, ʻo ka maʻamau o nā lima a me nā wāwae.

Hiki i ka Choreoathetosis ke hoʻopili i ka poʻe o nā makahiki a i ʻole ke kāne. Loaʻa ka maʻi 15 o ka poʻe 15 a 35 paha.

ʻOiai he mau manawa pōkole kekahi o nā hihia choreoathetosis, hiki i nā ʻāpana ʻoi loa ke waiho no nā makahiki. Hiki ke hanana i ke ʻano a hiki ke hoʻomohala i ka manawa.

Nā ʻōuli o choreoathetosis

ʻO ka neʻe ʻana o ke kino kūlohelohe he maʻamau. Akā ke lilo lākou i mau mau, hiki i nā neʻe ʻole ke kaohi ʻia ke hōʻeha i nā kino kīnā a me ka hōʻoluʻolu ʻole.


Hoʻomaopopo maʻalahi ʻia nā hōʻailona Choreoathetosis, pili pū lākou:

  • ʻūmiʻi mākala
  • twitching ʻaʻano ʻole
  • kūlana paʻa paʻa
  • ʻūpē mākala hiki ʻole ke kaohi ʻia
  • nā neʻe ʻole o ke kino a i ʻole nā ​​ʻāpana o ke kino
  • neʻe kūmau mau

Hiki ke loaʻa i nā ʻāpana Choreoathetosis me ka ʻole. Hiki i kekahi mau mea ke hoʻoulu i kahi ʻāpana, e like me ka caffeine, ʻona a me ke koʻikoʻi. Ma mua o kahi hanana, ʻike paha ʻoe i kou mau mākala e hoʻomaka e hoʻopaʻa, a i ʻole nā ​​hōʻailona kino ʻē aʻe. Hiki ke hoʻouka i nā wahi mai 10 kekona a i hoʻokahi hola.

Nā kumu Choreoathetosis

Hoʻohui pinepine ʻia ʻo Choreoathetosis ma ke ʻano he hōʻailona mai nā ʻano triggering a i ʻole nā ​​maʻi. ʻO nā kumu i hiki ke hoʻopili ʻia:

  • lāʻau lapaʻau
  • hōʻeha a hōʻeha paha
  • lolo lolo
  • ʻōiwi
  • Maʻi ʻo Huntington
  • Tourette maʻi pale
  • Maʻi ʻo Wilson
  • kernicterus, kahi ʻano o ka lolo i hōʻino ʻia i nā keiki hānau hou ʻeleu
  • chorea

Lapaʻau Choreoathetosis

ʻAʻohe lāʻau lapaʻau no choreoathetosis. Nānā nā koho lapaʻau i ka mālama ʻana i nā ʻōuli o kēia ʻano. Pili ka mālama ʻana i ke kumu kumu o kāu hihia o choreoathetosis.


Ma hope o ka nānā pono ʻana i kāu mōʻaukala olakino, hiki i kāu kauka ke koi aku i ka lāʻau e hōʻemi a hoʻopau ai i nā ʻāpana choreoathetosis. Pono kēia mau lāʻau e hoʻomaha i kou mau mākala a hoʻomāmā i ka ʻeha.

ʻO nā koho lāʻau maʻamau no choreoathetosis me:

  • ʻO ka carbamazepine, kahi anticonvulsant e mālama i ka ʻeha o ke aʻa a pale i ka hopu ʻana
  • phenytoin, kahi anticonvulsant e mālama a pale i ka hopu ʻana
  • nā mea hoʻomaha hoʻomaha nāʻiʻo

ʻO ke kaha, ʻoiai he invasive, hiki ke kōkua i ka hōʻemi ʻana i nā hanana choreoathetosis. Paipai paha nā kauka i ka stimulate o ka lolo hohonu, kahi e waiho ai i nā electrodes i ka ʻāpana o ka lolo e kaohi ana i ka neʻe ʻana o nā mākala.

Pili nā uila i kahi hāmeʻa e lawe i nā uila uila a me nā haʻalulu i nā haʻalulu. ʻOiai ua kūleʻa kēia kaʻina hana, halihali ia i ka makaʻu o ka maʻi a koi i kahi pāhiko ʻoki pani ma luna o ka manawa.

Outlook

ʻOiai ʻaʻohe lāʻau lapaʻau no choreoathetosis, hiki i nā koho lapaʻau like ʻole ke hoʻoponopono i nā hōʻailona. E mālama pono i nā kuhikuhi ma kāu lāʻau i kuhikuhi ʻia i ʻole eʻoi aʻe ka maikaʻi o kāu mau ʻōuli.


Hiki i ka hoʻololi ʻana i ka home ke hoʻomaikaʻi i kou ola. Inā pili kāu choreoathetosis i kāu neʻe i kēlā me kēia lā, e pale i kou home e pale i ka hōʻeha a i ʻole nā ​​trauma hou mai nā paheʻe a hāʻule.

Mai koho ponoʻī. Inā hoʻomaka ʻoe e ʻike i nā ʻōuli kūpono ʻole, e kāhea koke aku i kāu kauka.

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